Synovial chondrosarcoma complicating synovial chondromatosis. Report of a case and review of the literature.

Primary synovial chondromatosis (SC) is a rare proliferative disorder that causes pain, swelling, and restriction of movement to the joints it affects. The disease frequently runs a protracted course, often requiring multiple surgical procedures to obtain some control. Few reports exist detailing the natural history of SC, although malignant transformation to synovial chondrosarcoma (CHS) is recognized to be a rare event. The aim of our study was to review a large orthopaedic oncology database in order to evaluate the incidence of CHS arising from SC. We identified 78 patients who have presented to our centre with primary synovial chondromatosis (SC). Of those patients, 5 went on to develop malignant change. This represents a 6.4% incidence of developing synovial chondrosarcoma (CHS) within preexisting primary synovial chondromatosis. The patients had a mean age of 28 years at first diagnosis with synovial chondromatosis with the median time from original diagnosis to malignant transformation being 20 years (range 2.7–39 yrs).

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Intra- and extracapsular synovial chondromatosis of the temporomandibular joint: Rare case and review of the literature

SAGE Open Medical Case Reports ◽

10.1177/2050313x18775307 ◽

2018 ◽

Vol 6 ◽

pp. 2050313X1877530 ◽

Cited By ~ 1

Author(s):

Henrik Holtmann ◽

Thomas Böttinger ◽

Norbert R Kübler ◽

Daman D Singh ◽

Christoph K Sproll ◽

...

Keyword(s):

Temporomandibular Joint ◽

Rare Case ◽

Unusual Case ◽

Synovial Chondromatosis ◽

Benign Disease ◽

Malignant Diseases ◽

Review Of The Literature ◽

Loose Bodies ◽

Radiographic Findings ◽

The Right

Synovial chondromatosis is a benign disease which most commonly appears in large joints and only rarely affects the temporomandibular joint. The diagnosis is quite difficult due to the fact that a large swelling in the preauricular area and the radiographic findings may be misdiagnosed as other benign or malignant diseases. We report an unusual case of intra- and extracapsular chondromatosis of 25 osteochondral loose bodies in the right temporomandibular joint.

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Synovial chondrosarcoma arising in synovial chondromatosis of the right hip

Skeletal Radiology ◽

10.1007/s002560050249 ◽

1997 ◽

Vol 26 (6) ◽

pp. 366-369 ◽

Cited By ~ 55

Author(s):

G. Hermann ◽

Michael J. Klein ◽

Ibrahim Fikry Abdelwahab ◽

S. Kenan

Keyword(s):

Synovial Chondromatosis ◽

The Right ◽

Synovial Chondrosarcoma

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Tumours and pseudotumorous lesions of the temporomandibular joint: a diagnostic challenge

The Journal of Laryngology & Otology ◽

10.1017/s0022215100138617 ◽

1997 ◽

Vol 111 (8) ◽

pp. 776-781 ◽

Cited By ~ 19

Author(s):

Fabienne Allias-Montmayeur ◽

Régine Durroux ◽

Laurent Dodart ◽

Roger Combelles

Keyword(s):

Temporomandibular Joint ◽

Synovial Chondromatosis ◽

Calcium Pyrophosphate ◽

Calcium Pyrophosphate Dihydrate ◽

Pathological Features ◽

Disease Entity ◽

Review Of The Literature ◽

Diagnostic Challenge ◽

Crystal Deposition ◽

Pyrophosphate Dihydrate

AbstractTumours and pseudotumorous lesions originating from the synovial membrane of the temporomandibular joint are rare. We report a series of six cases of such disorders. There were two cases of synovial chondromatosis, two of calcium pyrophosphate dihydrate crystal deposition disease, one nodular synovitis and one synovial sarcoma. Three patients were female and three were male. Their ages ranged from 36 to 70 years. All had atypical clinical and radiographical presentation. The prevalence, clinical and radiographical findings and pathological features of each disease entity are discussed and a review of the literature is made concerning all tumours and pseudotumours arising from the temporomandibular joint.

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