scholarly journals The Role of Computed Tomography in the Diagnosis of Rare Congenital Heart Disease: Interrupted Aortic Arch

2021 ◽  
Author(s):  
Yusen Feng ◽  
Lijuan Wang ◽  
Hui Liu ◽  
Guifang Sun ◽  
Bin Liu ◽  
...  
Keyword(s):  
Computed Tomography ◽  
Pulmonary Artery ◽  
Aortic Arch ◽  
Type A ◽  
Left Pulmonary Artery ◽  
Imaging Features ◽  
Type B ◽  
Descending Aorta ◽  
Trunk Diameter ◽  
Right Pulmonary Artery

Abstract Background: Interrupted aortic arch (IAA) is a rare congenital anomaly of the aortic arch and an anatomical interruption of the lumen between the ascending and descending aorta. Computed tomography (CT) has become a reliable noninvasive diagnostic method for congenital IAA .The purpose of this study was to To investigate the imaging features of IAA and improve the understanding and diagnosis of the disease. Methods: The imaging features and postoperative pathological data of 25 patients with IAA confirmed by dual-source computed tomography (DSCT) angiography were analyzed in this retrospective study. Results: Among the 25 patients with IAA, 15 were type A, 7 were type B, 0 were type C and D, and 2 were type E. The diameter of the pulmonary artery trunk in type A was larger than that in type B (P < 0.05). However, there were no significantly different between type A and type B abomg the ascending aorta diameter; descending aorta; ascending aorta/ descending aorta ratio; left pulmonary artery main trunk diameter; right pulmonary artery main trunk diameter; left pulmonary artery trunk/ pulmonary artery trunk ratio; right pulmonary artery trunk/pulmonary artery trunk ratio; left pulmonary artery trunk/right pulmonary artery trunk ratio.Conclusion: The imaging findings of IAA have typical and specific signs, and the types of IAA are not comprehensive. One type of patient identification can be added: patients who are dissected between the left common carotid artery and left subclavian artery opening, and the descending aorta is circulated by the chest collaterals. Patients with wide pulmonary artery in the IAA are usually type A patients. Patients with IAA after surgical repair require lifetime follow-up, mainly to monitor left ventricular outflow tract obstruction and recurrent aortic coarctation.

Utility of Pre- and Postoperative Computed Tomography Angiography for the Evaluation of a Complex Vascular Ring

2019 ◽  
Vol 10 (5) ◽  
pp. 654-656
Author(s):  
Philip B. Dydynski ◽  
John S. Austin ◽  
Deborah Kozik ◽  
Bahaaldin Alsoufi
Keyword(s):  
Computed Tomography ◽  
Pulmonary Artery ◽  
Aortic Arch ◽  
Computed Tomography Angiography ◽  
Vascular Ring ◽  
Left Pulmonary Artery ◽  
Aberrant Right Subclavian Artery ◽  
Descending Aorta ◽  
Right Pulmonary Artery ◽  
The Right

We present the case of a neonate born with an unusual complex vascular ring formed by a left-sided aortic arch that had retroesophageal course to join a right-sided descending aorta and a very large right-sided arterial ductus from the right pulmonary artery to the descending aorta. Associated finings included aortic arch hypoplasia, aberrant right subclavian artery, and aberrant origin of the left pulmonary artery from the aorta. We focus on the role of computed tomography angiography in the preoperative and postoperative assessment of this complex anomaly.

Two Rare Vascular Rings With Ductal Origin of the Left Pulmonary Artery: A Previously Unrecognized Syndrome?

2016 ◽  
Vol 9 (3) ◽  
pp. 352-356
Author(s):  
Poonam P. Thankavel ◽  
Kristine J. Guleserian ◽  
Robert H. Anderson
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Clinical Course ◽  
Left Pulmonary Artery ◽  
Descending Aorta ◽  
Vascular Rings ◽  
Arterial Duct

We report two neonates with distal ductal origin of the left pulmonary artery who also had rare vascular rings comprised of a left aortic arch and right arterial duct with a midline/rightward descending aorta. To the best of our knowledge, this association has not previously been described, although other abnormalities of the left pulmonary artery in the setting of vascular rings have been reported. We review the embryology, utility of imaging, and clinical course.

Non-confluent pulmonary arteries in a patient with pulmonary atresia and intact ventricular septum: ? a 5th aortic arch with a systemic-to-pulmonary arterial connection

2000 ◽  
Vol 10 (4) ◽  
pp. 419-422 ◽  
Author(s):  
Astolfo Serra ◽  
Francisco Chamie ◽  
R.M. Freedom
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Pulmonary Arteries ◽  
Pulmonary Atresia ◽  
Left Pulmonary Artery ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Right Pulmonary Artery ◽  
Pulmonary Arterial ◽  
The Right

AbstractMajor abnormalities of pulmonary circulation are uncommon in the patient with pulmonary atresia and intact ventricular septum. Non-confluent pulmonary arteries have only rarely been described in this setting. In this case report, we describe a patient in whom the pulmonary arteries are non-confluent, with the right pulmonary artery supplied through a right-sided arterial duct, and the left pulmonary artery most likely through a fifth aortic arch, thus providing a systemic-to-pulmonary arterial connection. We discuss the various forms of non-confluent pulmonary arteries in the setting of pulmonary atresia and intact ventricular septum.

Abnormal origin of the left pulmonary artery from the descending aorta and heterotaxy syndrome: an undescribed phenotypic association

2021 ◽  
pp. 1-4
Author(s):  
Anne Moreau de Bellaing ◽  
Damien Bonnet ◽  
Lucile Houyel
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Left Pulmonary Artery ◽  
Anomalous Origin ◽  
Cardiac Anatomy ◽  
Heterotaxy Syndrome ◽  
Direct Tension ◽  
Pulmonary Atelectasis ◽  
Descending Aorta ◽  
Arterial Duct

Abstract Extensive screening in a newborn with prenatal suspicion of VACTERL syndrome identified an anomalous origin of the left pulmonary artery from the descending aorta with an arterial duct and left aortic arch, and normal intra-cardiac anatomy. Other anatomical anomalies suggested heterotaxy syndrome. At one-month-old, re-implantation of the 3.5 mm left pulmonary artery was performed by direct tension-low anastomosis. Post-operative course was complicated by severe left pulmonary atelectasis, and the patient died 20 days later.

Echocardiographic delineation of anomalous origin of the right subclavian artery from the right pulmonary artery

1997 ◽  
Vol 7 (3) ◽  
pp. 328-330 ◽  
Author(s):  
Yuk Law ◽  
Jeff Smallhorn ◽  
Ian Adatia
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Subclavian Artery ◽  
Anomalous Origin ◽  
Subclavian Steal Syndrome ◽  
Type B ◽  
Cross Sectional ◽  
Right Pulmonary Artery ◽  
The Right ◽  
Steal Syndrome

AbstractWe describe a case of anomalous origin of the right subclavian artery from the right pulmonary artery detected by cross-sectional echocardiography in an infant with type B interruption of the aortic arch. Preoperative recognition and surgical reimplantation of the right subclavian artery are important to prevent subsequent subclavian steal syndrome.

scholarly journals Partial Anomalous Left Pulmonary Artery: A Case Report and Literature Review

2020 ◽  
Vol 17 (3) ◽  
Author(s):  
Chia Hung Chen ◽  
Pei San Tsai ◽  
Dao Chen Lin ◽  
Yu Peng Liu ◽  
Kun Shan Cheng
Keyword(s):  
Computed Tomography ◽  
Case Report ◽  
Literature Review ◽  
Pulmonary Artery ◽  
Left Pulmonary Artery ◽  
Kabuki Syndrome ◽  
Anomalous Artery ◽  
Right Pulmonary Artery ◽  
Cardiovascular Defects ◽  
The Right

: Hereby, the case of an 8-month-old girl diagnosed with partial anomalous left pulmonary artery (PLPA) is presented. Echocardiography and computed tomography (CT) examination demonstrated that the anomalous artery originated from the right pulmonary artery supplying the left upper lobe. PLPA is sometimes associated with tracheobronchial anomaly and congenital cardiovascular defects. A relationship between PLPA and Kabuki syndrome has also been suggested. Echocardiography and CT angiography can be used as accurate tools for identifying an anomalous left pulmonary artery and adjacent abnormal anatomic structures.

scholarly journals Differences in clinical and computed tomography imaging features between two types of mixed epithelial and stromal tumor of the kidney: Suggestions for patient management

2021 ◽  
Author(s):  
Juan Chen ◽  
Hui Liu ◽  
Meng-Si Li ◽  
Wen-Guang Liu ◽  
Ismail Bilal Masokano ◽  
...  
Keyword(s):  
Computed Tomography ◽  
Treatment Plan ◽  
Clinical Information ◽  
Type A ◽  
Stromal Tumor ◽  
Fisher Exact Test ◽  
Imaging Features ◽  
Type B ◽  
Renal Sinus ◽  
Maximal Diameter

Abstract Background To analyze the differences in clinical features and computed tomography characteristics in the two types of mixed epithelial and stromal tumor of the kidney (MESTK) and to establish a treatment plan for the MESTK types.Methods 17 patients underwent multidetector computed tomography (MDCT) before surgery and had a pathological diagnosis of MESTK were enrolled. Their clinical information (R.E.N.A.L.Nephrometry Score (R.E.N.A.L.－NS), radical nephrectomy (RN), partial nephrectomy (PN), etc.) were collected. The radiological features included renal sinus fat invagination (SFI), maximal diameter (MD), capsule and septa of the tumor, etc. were also analyzed. They were divided into two types according to the MDsolid/MDtumor ratio (type A with > 63%; type B with ≤ 63%). An independent-sample t-test and Fisher exact test were used to assess the differences between the two groups. Results MESTKs demonstrated a variable multi-septate cystic and solid components with a delayed enhancement. There were 9 patients for type A and 8 subjects for type B. Compared with type A, the lesions in type B have larger MD (79.13±39.06 vs. 41.22±24.19, p = 0.028), higher R.E.N.A.L.－NS (10.03±0.50 vs. 8.95±1.26, P＜0.001), higher RN (75.00% vs.22.22%, p =0.015), larger SFI (87.5% vs.33.3%, p=0.05), more septa (100% vs. 0%, p <0.001) and more capsule (100% vs. 11.1%, p < 0.001).Conclusion Type B MESTK has more hazardous features compared with type A, suggesting that RN is more suitable for type B and PN for type A.

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