scholarly journals Acquired Hemophilia A Associated with IgG4-related Lung Disease in a Patient with Autoimmune Pancreatitis

2012 ◽  
Vol 51 (22) ◽  
pp. 3151-3154 ◽  
Author(s):  
Keishi Sugino ◽  
Kyoko Gocho ◽  
Fumiaki Ishida ◽  
Naoshi Kikuchi ◽  
Nao Hirota ◽  
...  
Keyword(s):  
Lung Disease ◽  
Autoimmune Pancreatitis ◽  
Hemophilia A ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia

Acquired Hemophilia a Secondary to Autoimmune Pancreatitis with Elevated IG4

2021 ◽  
Vol 5 (2) ◽  
Author(s):  
Li Y ◽  
◽  
Li J ◽  
He H ◽  
Cai R ◽  
...  
Keyword(s):  
Factor Viii ◽  
Hormone Therapy ◽  
Rare Disease ◽  
Plasma Exchange ◽  
Autoimmune Pancreatitis ◽  
Hemophilia A ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia ◽  
Related Disease ◽  
Igg4 Related Disease

Acquired Hemophilia A (AHA) is a rare disease resulting from autoantibodies against Factor VIII (FVIII) that leads to bleeding. AHA associated with IgG4 related diseases is even rarer. The patient was diagnosed with IgG4 associated autoimmune pancreatitis in January 2019, and the condition improved after two hospitalizations. However, 22 months later, the patient was admitted to hospital due to generalized bleeding points. He was diagnosed with AHA and improved after hormone therapy and plasma exchange. Although IgG4 is associated with IgG4-related disease and AHA, its relevance to the etiology of both diseases is not well understood.

Acquired hemophilia A associated with autoimmune pancreatitis with serum IgG4 elevation

2018 ◽  
Vol 108 (3) ◽  
pp. 335-338 ◽  
Author(s):  
Taisuke Narazaki ◽  
Shojiro Haji ◽  
Yasuhiro Nakashima ◽  
Yasuhiro Tsukamoto ◽  
Mariko Tsuda ◽  
...  
Keyword(s):  
Autoimmune Pancreatitis ◽  
Hemophilia A ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia ◽  
Serum Igg4

scholarly journals Successful Management of Acquired Hemophilia A Associated with Bullous Pemphigoid: A Case Report and Review of the Literature

2017 ◽  
Vol 2017 ◽  
pp. 1-7 ◽  
Author(s):  
Quentin Binet ◽  
Catherine Lambert ◽  
Laurine Sacré ◽  
Stéphane Eeckhoudt ◽  
Cedric Hermans
Keyword(s):  
Bullous Pemphigoid ◽  
Neutralizing Antibodies ◽  
Hemophilia A ◽  
Rare Condition ◽  
Term Treatment ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia ◽  
Short Term Treatment ◽  
Life Threatening ◽  
Dose Levels

Background. Acquired hemophilia A (AHA) is a rare condition, due to the spontaneous formation of neutralizing antibodies against endogenous factor VIII. About half the cases are associated with pregnancy, postpartum, autoimmune diseases, malignancies, or adverse drug reactions. Symptoms include severe and unexpected bleeding that may prove life-threatening.Case Study. We report a case of AHA associated with bullous pemphigoid (BP), a chronic, autoimmune, subepidermal, blistering skin disease. To our knowledge, this is the 25th documented case of such an association. Following treatment for less than 3 months consisting of methylprednisolone at decreasing dose levels along with four courses of rituximab (monoclonal antibody directed against the CD20 protein), AHA was completely cured and BP well-controlled.Conclusions. This report illustrates a rare association of AHA and BP, supporting the possibility of eradicating the inhibitor with a well-conducted short-term treatment.

scholarly journals Persistent surgical wound bleeding: A rare condition related to acquired hemophilia A

2013 ◽  
Vol 46 (4) ◽  
pp. 135-139
Author(s):  
Chia-Wei Chang ◽  
Jiun-Ting Yeh ◽  
Shang-Yu Wang ◽  
Chun-Hsiang Ouyang ◽  
Chien-Hung Liao ◽  
...  
Keyword(s):  
Hemophilia A ◽  
Rare Condition ◽  
Surgical Wound ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia

Two Cases of Acquired Hemophilia A Successfully Treated with Oral Steroid or Danazol

2005 ◽  
Vol 40 (1) ◽  
pp. 58 ◽  
Author(s):  
Sun Young Park ◽  
Jin Seok Kim ◽  
Yuri Kim ◽  
In Hae Park ◽  
June-Won Cheong ◽  
...  
Keyword(s):  
Hemophilia A ◽  
Oral Steroid ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia

scholarly journals The First Case of Postpartum Acquired Hemophilia A in Korea

2011 ◽  
Vol 26 (9) ◽  
pp. 1247 ◽  
Author(s):  
Ji Hyun Lee ◽  
Dong-Hwan Kim ◽  
Kiyoung Yoo ◽  
Yongmook Choi ◽  
Sun-Hee Kim ◽  
...  
Keyword(s):  
Hemophilia A ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia ◽  
First Case

scholarly journals A case of acquired hemophilia A incidentally diagnosed on postoperative bleeding after tooth extraction

2013 ◽  
Vol 59 (12) ◽  
pp. 786-790
Author(s):  
Katsumi MOTEGI ◽  
Yukihiro MOMOTA ◽  
Hideyuki TAKANO ◽  
Kouichi KANI ◽  
Yoshiko YAMAMURA ◽  
...  
Keyword(s):  
Tooth Extraction ◽  
Hemophilia A ◽  
Postoperative Bleeding ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia
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