Management of PAH in Adults with Congenital Heart Disease: Impact and Dilemmas

2013 ◽  
Vol 11 (4) ◽  
pp. 198-206

Guest editor Richard Krasuski, MD, convened a group of experts by telephone on January 17, 2013, to discuss current trends in diagnosis and treatment of pulmonary hypertension among patients with congenital heart disease. Joining the call were Professor Maurice Beghetti, Head of Pediatric Subspecialties, Division Head of Pediatric Cardiology Unit, Children's University Hospital, Geneva, Switzerland; Curt Daniels, MD, Director, Adolescent and Adult Congenital Heart Disease Program Nationwide Children's Hospital, The Ohio State University, Columbus, Ohio; Wayne J. Franklin, MD, Texas Children's Hospital, Houston; and Michael J. Landzberg, MD, Associate Director, Adult Pulmonary Hypertension Program and Director, Boston Adult Congenital Heart Program, Boston Children's Hospital.

2020 ◽  
Vol 4 (S1) ◽  
Author(s):  
Heba Nashat ◽  
Carla Favoccia ◽  
Andrew Constantine ◽  
Konstantinos Dimopoulos

AbstractPulmonary hypertension is not uncommon in adult patients with congenital heart disease and can significantly affect their exercise capacity, quality of life and prognosis. Timely identification and management of pulmonary hypertension in these patients is important. Patients must be allocated to the correct diagnostic group and treatment decided upon, including offering pulmonary arterial hypertension therapies to those who are most likely to benefit.In this paper, we provide an overview of the diagnostic modalities that are used to investigate and diagnose pulmonary hypertension in modern adult congenital heart disease practice. Emphasis is placed on echocardiography, which is the modality of choice for raising the suspicion of PH, and cardiac catheterisation, which is fundamental in establishing the diagnosis. Other modalities, such as cardiac magnetic resonance imaging and computed tomography can provide complementary information on anatomy and physiology.Combining all this information into a clinical diagnosis and management plan requires clinical expertise and a multidisciplinary approach, especially when managing this rare and complex group of patients.


1995 ◽  
Vol 58 (SupplementIV) ◽  
pp. 1255-1259
Author(s):  
Norifumi Nakanishi ◽  
Takeyoshi Kunieda ◽  
Seiki Nagata ◽  
Toshikatu Yagihara ◽  
Makoto Takamiya

2010 ◽  
Vol 5 (1) ◽  
pp. 44-50 ◽  
Author(s):  
Efrén Martínez-Quintana ◽  
Guillermo Miranda-Calderín ◽  
Arantza Ugarte-Lopetegui ◽  
Fayna Rodríguez-González

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