Zinner Syndrome with Ectopic Ureter Remnant

Author(s):  
Ara Ko ◽  
Sung Bin Park ◽  
Hyun Jeong Park ◽  
Eun Sun Lee

: Zinner syndrome is a rare congenital abnormality defined by a clinical triad of unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ipsilateral ejaculatory duct obstruction. Most patients are asymptomatic, but if the cystic dilatation of the seminal vesicle becomes significant, it can result in urinary symptoms such as dysuria and urinary retention. This rare developmental anomaly related to the mesonephric duct can also present with other abnormalities. Here, we report our experience of Zinner syndrome with bladder outlet obstruction and an ectopic ureter remnant.

Author(s):  
Abakar Djidda ◽  
Fatima-Ezzahrae Badi ◽  
Mouna Sabiri ◽  
Samia Elmanjra ◽  
Samira Lezar ◽  
...  

Zinner syndrome is a developmental anomaly of the urogenital tract. This condition is defined by the triad of unilateral renal agenesis, ipsilateral seminal vesicle cyst and ipsilateral ejaculatory duct obstruction. The syndrome is due to malformation of the mesonephric duct during embryogenesis. The condition used to be rare but is now frequently encountered due to the advent of MRI and CT. MRI confirms the diagnosis by revealing the seminal vesicle cyst and its contents, and the ejaculatory duct obstruction, while CT confirms renal agenesis. We report the case of a young patient with Zinner syndrome.


2020 ◽  
Vol 3 ◽  
pp. 1
Author(s):  
Devimeenal Jaganathan ◽  
Gopinathan Kathirvelu ◽  
Suriyaprakash Nagarajan ◽  
Usha Nandhini Ganesan

Zinner’s syndrome is a rare congenital abnormality consisting of unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ipsilateral ejaculatory duct obstruction. The mutual embryological origins of the seminal vesicle and the ureteral bud from the Wolffian duct result in both anomalous seminal vesicle and urinary tracts. Most cases have nonspecific symptoms such as prostatism, urinary urgency, dysuria, painful ejaculation, and perineal discomfort. The usual presentation is between the third and fourth decades of life, with infertility being the most common complaint. Ultrasound and magnetic resonance imaging can easily detect this condition. We present here an extremely rare developmental anomaly involving the Wolffian ducts, which would remain undiagnosed but for radiologic imaging.


2021 ◽  
Vol 2021 ◽  
pp. 1-4
Author(s):  
M. Hevia Palacios ◽  
M. Álvarez-Maestro ◽  
J. Gómez Rivas ◽  
A. Aguilera Bazan ◽  
L. Martínez-Piñeiro

A 66-year-old male patient in follow-up in the urology department for a non-muscle-invasive bladder cancer was detected by ultrasound to have absence of the left kidney and a cystic, multilobed image at the location of the seminal vesicle. Magnetic resonance imaging reveals left renal agenesis and the existence of multiple cysts in the ipsilateral seminal vesicle that reaches a size of 6.9 × 3.7   cm , as well as a ureteral remnant that opens into the seminal vesicle. The patient does not present urinary symptoms, neither pain with ejaculation nor hematuria. A triad of seminal vesicle cyst, ipsilateral renal agenesis, and ipsilateral ejaculatory duct obstruction is known as Zinner syndrome. Congenital anomalies of the seminal vesicles are rare; some of them are associated with malformations of the upper urinary system. Seminal vesicle cysts are associated with ipsilateral renal agenesis and ectopic or dysplastic ureter. Patients may remain asymptomatic and be diagnosed incidentally or may present with symptoms such as increased urinary frequency, dysuria, recurrent infections, pain with ejaculation, and perineal discomfort.


2021 ◽  
Vol 2021 ◽  
pp. 1-4
Author(s):  
Niall P. Kelly ◽  
Adrian Fuentes-Bonachera ◽  
William P. Shields ◽  
Ivor M. Cullen ◽  
Padraig J. Daly

Zinner syndrome was first described in 1914 and represents the triad of unilateral renal agenesis and ipsilateral seminal vesicle cyst and ipsilateral ejaculatory duct obstruction. Seminal vesicle cysts are often asymptomatic but can also present with pain, haematospermia, or other lower urinary tract symptoms. Treatment strategies include observation and surgical excision. We present the laparoscopic management of an enlarged seminal vesicle cyst, consistent with Zinner syndrome, 14 years after the initial diagnosis. A 58-year-old male patient was diagnosed with a left-sided seminal vesicle cyst while undergoing assessment for renal transplant due to progressively worsening renal function in his solitary right kidney. The otherwise asymptomatic cyst enlarged from the time of initial diagnosis in 2004 ( 11.3   cm × 9.7   cm × 13.1   cm ) to nearly double the size in 2018 ( 12.8   cm × 11.9   cm × 14.2   cm ). This cyst size ultimately precluded renal transplant, and the patient was referred for excision. Laparoscopic excision of the cyst was performed, histopathology confirmed seminal vesicle cyst tissue, and there has been no recurrence of the cyst to date. The patient remains active on the renal transplant waitlist. Zinner syndrome is a rare syndrome, with the seminal vesicle cysts being managed by observation or surgical excision. We report the longest documented observation of a seminal vesicle cyst, culminating in a safe and successful laparoscopic excision.


2006 ◽  
Vol 175 (4S) ◽  
pp. 523-523
Author(s):  
Irfan Orhan ◽  
Imed Duksal ◽  
Rahmi Onur ◽  
Tansal A. Balci ◽  
Kursad Poyraz ◽  
...  

2020 ◽  
Vol 8 (3) ◽  
pp. 574-576
Author(s):  
Joseph Shawn Smith ◽  
William Patrick Springhart

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