scholarly journals Association of fetal unilateral multicystic kidney disease with other urinary tract anomalies

2009 ◽  
Vol 66 (9) ◽  
pp. 733-737
Author(s):  
Sonja Pop-Trajkovic ◽  
Aleksandar Ljubic ◽  
Vladimir Antic ◽  
Milan Trenkic
Keyword(s):  
Diagnostic Procedures ◽  
Multicystic Dysplastic Kidney ◽  
Urogenital System ◽  
Urinary System ◽  
Contralateral Kidney ◽  
Multicystic Kidney ◽  
Gynecology And Obstetrics ◽  
Dysplastic Kidney ◽  
Operative Findings ◽  
The University

Background/Aim. Multicystic dysplastic kidney represents a disorder in the fetus development presented prenatally of postnatally, this deserving special attention due to a risk of additional anomalies in children with this disorder. The aim of this study was to determine the incidence and type of common anomalies of the urinary system in the prenatal diagnosis of unilateral multicystic dysplastic kidney, and point out the necessity of postnatal diagnostic procedures in order to evaluate the state of the urinary system. Methods. This retrospective-prospective study encompassed 38 cases of prenatally diagnosed unilateral fetal multicystic dysplastic kidney, presented to the Council for Fetal Anomalies from the Institute for Gynecology and Obstetrics of the Clinical Centre of Serbia and the University Children's Clinic within a three-year period. Associated anomalies were revealed by autopsy findings when pregnancy was terminated, ie resumed with clinical and operative findings of born children. Results. In every case of terminated pregnancy and death after birth the autopsy revealed additional renal or exstrarenal anomaly which were not prenatally detected. Postnatal evaluation of survived children with unilateral multicistic disease revealed that 31,4% of them have an anomaly of the contralateral kidney, 26,3% anomaly of the ipsilateral side, 13,2% anomaly of the lower portions of the urinary system and the same percent an additional extrarenal anomaly. The surgery was performed in 73,6% of children, more than half of the interventions were related to extrarenal anomaly. In 17% of children the kidney function was deteriorated after surgery. Conclusion. Children suffering from unilateral multicystic dysplastic kidney have a greater chance of exhibiting an anomaly of the contralateral kidney and the urinary system in general. Therefore, they require thorough examination, both prenatally and postnatally. We propose obligatory serial professional prenatal ultrasound examinations, followed by postnatal ultrasound, isotope scan, and we especially emphasize the need for performing urinary cystouretherography, bearing in mind the high incidence of the vesicoureteral reflux of the contralateral kidney. In addition to nephrectomy, cytoscopy and colposcopy also need to be performed for the purpose of discovering possible hidden anomalies of the urogenital system.

scholarly journals Fetal multicystic kidney disease: Outcome and follow up

2010 ◽  
Vol 63 (3-4) ◽  
pp. 262-266 ◽  
Author(s):  
Sonja Pop-Trajkovic ◽  
Aleksandar Ljubic ◽  
Vesna Kopitovic ◽  
Vladimir Antic ◽  
Jelena Milosevic ◽  
...  
Keyword(s):  
Kidney Disease ◽  
Diagnostic Procedures ◽  
Multicystic Dysplastic Kidney ◽  
Mortality And Morbidity ◽  
Contralateral Kidney ◽  
Multicystic Kidney ◽  
Dysplastic Kidney ◽  
Operative Findings ◽  
Multicystic Kidney Disease

Introduction Congenital fetal anomalies are the great problem and one of the main causes of increased perinatal mortality and morbidity. The aim of this study is to determine the outcome of prenataly detected multicystic dysplastic kidney and to point to the necessity of postnatal diagnostic procedures. Material and methods The retrospective-prospective study encompasses 38 cases of the prenatally diagnosed unilateral fetal multicystic dysplastic kidney. The associated anomalies were revealed either by autopsy findings when the pregnancy was terminated, or when the pregnancy continued, by clinical and operative findings the newborns. Results The autopsy finding revealed bilateral multicystic displastic kidney or unilateral mylticystic displastic kidney and the agenesis of the contralateral kidney. The postnatal evaluation of the newborns with unilateral multicistic disease revealed that 84.3% of them had some concomitant anomaly of the urinary tract, most of them had an anomaly of the contralateral kidney (31.4%). The surgery was performed in 73.6% of children, in 17% of children the kidney function deteriorated after the surgery. Conclusion The findings of bilateral multicystic kidney disease and unilateral multicystic kidney disease and anamnion are the indication to terminate the pregnancy. The finding of an isolated unilateral multicystic dysplastic kidney require thorough examination, both prenatally and postnatally. We propose obligatory serial prenatal ultrasound examinations, followed by postnatal ultrasound, isotope scan, and urinary cystourethography.

scholarly journals Posterior Urethral Valve and Prenataly Resolved Multicystic Dysplastic Kidney

PRILOZI ◽  
2021 ◽  
Vol 42 (1) ◽  
pp. 77-81
Author(s):  
Natasha Aluloska ◽  
Snezana Palchevska ◽  
Risto Simeonov ◽  
Zoran Gucev ◽  
Velibor Tasic
Keyword(s):  
Urinary Tract ◽  
Rare Event ◽  
Posterior Urethral Valve ◽  
Multicystic Dysplastic Kidney ◽  
Ultrasound Scan ◽  
Multicystic Kidney ◽  
Dysplastic Kidney ◽  
Urethral Valve ◽  
Normal Thickness ◽  
Work Up

Abstract Multicystic dysplastic kidney is a rare congenital anomaly of the kidney and urinary tract. The association with the posterior urethral valve is also very rare. Here we present a patient with both entities and prenatal resolution of the cysts. A 10-week old baby was referred for nephrourological work up due to prenatal diagnosis of the left multicystic kidney. He had serial US scans during the pregnancy. Immediately before delivery the cysts were not seen (prenatal resolution). There were no extrarenal anomalies. The first postnatal ultrasound scan revealed normal sized right kidney without dilatation of the pelvicalyceal system. The bladder had normal thickness of the wall. Technetium-99m dimercaptosuccinic acid scan showed no activity on the left side, and the right kidney appeared normal. At two months of age, a poor urinary steam was observed and additional urologic work up was indicated on clinical suspicion of PUV. Voiding urethrocystography revealed posterior urethral valve and the baby underwent cytoscopic valve resection. Conclusion: We present a rare association of two congenital anomalies of the kidney and urinary tract with prenatal involution of the multicystic dysplastic kidney that is extremely rare event as seen in our case. Presence of posterior urethral valve must be suspected in a male baby with a poor urinary stream even when his ultrasound scan of urinary system appears normal.

Abnormal contralateral kidney in unilateral multicystic dysplastic kidney disease

1995 ◽  
Vol 25 (4) ◽  
pp. 275-277 ◽  
Author(s):  
K. Kaneko ◽  
Y. Suzuki ◽  
Y. Fukuda ◽  
K. Yabuta ◽  
T. Miyano
Keyword(s):  
Kidney Disease ◽  
Multicystic Dysplastic Kidney ◽  
Contralateral Kidney ◽  
Dysplastic Kidney ◽  
Multicystic Dysplastic Kidney Disease

Distal ureteral atresia – an embryological dilemma

2022 ◽  
pp. 205141582110481
Author(s):  
Subramanya Kattepura ◽  
Attibele Mahadevaiah Shubha ◽  
Kanishka Das
Keyword(s):  
Preoperative Diagnosis ◽  
Renal Dysplasia ◽  
Urogenital Sinus ◽  
Multicystic Dysplastic Kidney ◽  
Level Of Evidence ◽  
Case Presentation ◽  
Contralateral Kidney ◽  
Urinary Tract Anomaly ◽  
Dysplastic Kidney ◽  
Associated Malformations

Introduction: Distal ureteral atresia is a rare urinary tract anomaly generally associated with ipsilateral renal dysplasia and abnormalities such as multicystic dysplastic kidney, hydronephrosis and megaureter in the contralateral kidney. Despite burgeoning investigation modalities, definitive preoperative diagnosis of this condition is rarely feasible, also the embryological disarray of events that result in the development of this anomaly and the associated malformations is not clearly understood. Case presentation: We hereby report two cases of distal ureteral atresia and discuss the diversity in their presentations, diagnosis, atypical associations and management and review the possible embryological mal-development. Conclusion: Distal ureteral atresia with urogenital sinus as in Case 1 has not been documented so far and a plausible embryological explanation is deduced regarding its occurrence. The course of the affected kidney following timely and adequate relief of obstruction in Case 2 is depicted, highlighting the eventual management. Level of evidence: Not applicable

WHAT IS THE FATE OF THE REFLUXING CONTRALATERAL KIDNEY IN CHILDREN WITH MULTICYSTIC DYSPLASTIC KIDNEY?

2004 ◽  
Vol 172 (4 Part 2) ◽  
pp. 1630-1634 ◽  
Author(s):  
DAVID C. MILLER ◽  
JON A. RUMOHR ◽  
RODNEY L. DUNN ◽  
DAVID A. BLOOM ◽  
JOHN M. PARK
Keyword(s):  
Multicystic Dysplastic Kidney ◽  
Contralateral Kidney ◽  
Dysplastic Kidney

scholarly journals Association of neural tube defects with congenital abnormalities of the urogenital system in a Chinese cohort

2021 ◽  
Vol 21 (1) ◽  
Author(s):  
Zhi-Hua Hong ◽  
Dong-Hui Jin ◽  
Xiao-Jian Yuan ◽  
Yang Zhao ◽  
Hou-Wei Lin ◽  
...  
Keyword(s):  
Neural Tube ◽  
Neural Tube Defects ◽  
Congenital Abnormality ◽  
Congenital Abnormalities ◽  
Urogenital System ◽  
Urinary System ◽  
Intravenous Pyelography ◽  
Abdominal Organs ◽  
Chinese Cohort ◽  
Urogenital Malformation

Abstract Background This study aimed to retrospectively analyze the correlation between congenital abnormality of the urogenital system and various factors in children with neural tube defects (NTDs). Methods A total of 190 children with congenital NTDs, who were admitted to a hospital from May 2013 to May 2018, were included into the present study. All admitted children with congenital NTDs were carried out routine abdominal B-ultrasound examinations to determine the malformations of the abdominal organs, including the urinary system. Children with a B-ultrasound result of suspected and unsure malformation underwent intravenous pyelography (IVP) and voiding cysto-urethrography (VCU), and this was further confirmed by the CT results. Results The incidence of urogenital malformation was 12.1% (23/190) in children with congenital NTDs. For the 23 children with urogenital malformations, most of these children had no definite urinary system symptoms, while some of these children had multiple incidences of urinary system infections. Conclusions Congenital NTDs are often combined with urogenital malformations, if not specifically searched these may be overlooked. The early detection of these malformations is beneficial to reduce the risk of operation and improve the prognosis.

Cytogenomic aberrations in isolated multicystic dysplastic kidney in children

2021 ◽  
Author(s):  
Tian-Jian Chen ◽  
Renfang Song ◽  
Adam Janssen ◽  
Ihor V. Yosypiv
Keyword(s):  
Multicystic Dysplastic Kidney ◽  
Dysplastic Kidney
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