Inferior vena cava and right atrial thrombosis in children with embryonal tumors

Tumor thrombosis of the central venous system in children with embryonal tumors is a rare complication, requiring a comprehensive treatment approach, with chemotherapy and the intervention of a multidisciplinary team of oncologists and cardiac surgeons. The article describes the medical history of a 9-month-old patient with bilateral nephroblastoma and tumor thrombosis of inferior vena cava and right atrium, as well as provides a brief review of the literature. The patient's parents gave their consent to the use of their child's data, including photographs, for research purposes and in publications.

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Obstruction of the inferior vena cava following bicaval orthotopic heart transplantation: a case series

European Heart Journal - Case Reports ◽

10.1093/ehjcr/ytab046 ◽

2021 ◽

Vol 5 (2) ◽

Author(s):

Anas Abudan ◽

Brent Kidd ◽

Peter Hild ◽

Bhanu Gupta

Keyword(s):

Inferior Vena Cava ◽

Heart Transplantation ◽

Inferior Vena ◽

Rare Complication ◽

Vena Cava ◽

Case Series ◽

Transoesophageal Echocardiography ◽

Right Atrial ◽

Orthotopic Heart Transplantation ◽

Eustachian Valve

Abstract Background Inferior vena cava (IVC) obstruction is a rare complication of orthotopic heart transplantation (OHT) and is unique to bicaval surgical technique. The clinical significance, diagnosis, complications, and management of post-operative IVC anastomotic obstruction have not been adequately described. Case summary Two patients with end-stage heart failure presented for bicaval OHT. Post-operative course was complicated with shock refractory to fluid resuscitation and inotropic/vasopressor support. Obstruction at the IVC-right atrial (RA) anastomosis was diagnosed on transoesophageal echocardiography (TOE), prompting emergent reoperation. In both cases, a large donor Eustachian valve was found to be restricting flow across the IVC-RA anastomosis. Resection of the valve resulted in relief of obstruction across the anastomosis and subsequent improvement in haemodynamics and clinical outcome. Discussion Presumably rare, we present two cases of IVC obstruction post-bicaval OHT. Inferior vena cava obstruction is an under-recognized cause of refractory hypotension and shock in the post-operative setting. Prompt recognition using TOE is crucial for immediate surgical correction and prevention of multi-organ failure. Obstruction can be caused by a thickened Eustachian valve caught in the suture line at the IVC anastomosis, which would require surgical resection.

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Budd-Chiari syndrome due to segmental obstruction of the inferior vena cava successfully managed with endovascular stenting

MedPharmRes ◽

10.32895/ump.mpr.2.3.22 ◽

2018 ◽

Vol 2 (3) ◽

pp. 22-26

Author(s):

Uyen Vo ◽

Duc Quach ◽

Luan Dang ◽

Thao Luu ◽

Luan Nguyen

Keyword(s):

Inferior Vena Cava ◽

Inferior Vena ◽

Laboratory Data ◽

Transaminase Level ◽

Vena Cava ◽

Budd Chiari Syndrome ◽

Endovascular Stenting ◽

Massive Ascites ◽

Chiari Syndrome ◽

History Of

Budd–Chiari syndrome (BCS), a rare and life-threatening disorder due to hepatic venous outflow obstruction, is occasionally associated with hypoproteinemia. We herein report the first case of BCS with segmental obstruction of the intrahepatic portion of inferior vena cava (IVC) and hepatic veins (HVs) successfully treated by endovascular stenting in Vietnam. A 32-year-old female patient presented with a 2-month history of massive ascites and leg swelling. She refused history of oral contraceptives use. Hepatosplenomegaly without tenderness was noted. Laboratory data showed polycythemia, mild hypoalbuminemia and hypoproteinemia, slightly high total bilirubin and normal transaminase level. The serum ascites albumin gradient was 1.9 g/dL and ascitic protein level was 1.1 g/dL. The other data were normal. BCS was suspected because of the discrepancy between mild liver failure and massive ascites; and the presence of hepatosplenomegaly and polycythemia. On abdominal magnetic resonance imaging, the segmental obstruction of three HVs and IVC was 2-3 cm long without thrombus. Cavogram revealed the severe segmental stenosis of intrahepatic portion of IVC with no visualized HV and extensive collateral veins. A Protégé stent was deployed to IVC. Leg swelling and ascites were completely resolved within 3 days after stenting. During 1-year follow-up, edema was not recurred and repeated laboratory results were all normal.

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Ectopic hepatocellular carcinoma in the adrenal gland with inferior vena cava thrombosis and right atrial extension.

Authorea ◽

10.22541/au.158739590.08535243 ◽

2020 ◽

Author(s):

Gaetano Ciancio

Keyword(s):

Hepatocellular Carcinoma ◽

Adrenal Gland ◽

Inferior Vena Cava ◽

Inferior Vena ◽

Vena Cava ◽

Right Atrial ◽

Vena Cava Thrombosis ◽

Inferior Vena Cava Thrombosis

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Isolated Marked Inferior Vena Cava Dilatation: Unusual Presentation or Underrecognized Common Phenomenon?

Case Reports in Cardiology ◽

10.1155/2018/8396523 ◽

2018 ◽

Vol 2018 ◽

pp. 1-3 ◽

Cited By ~ 1

Author(s):

Sneha R. Gadi ◽

Benjamin K. Ruth ◽

Alan Johnson ◽

Sula Mazimba ◽

Younghoon Kwon

Keyword(s):

Inferior Vena Cava ◽

Inferior Vena ◽

Vena Cava ◽

Unusual Presentation ◽

Atrial Pressure ◽

Right Atrial ◽

Right Atrial Pressure ◽

Common Phenomenon ◽

Right Heart

Inferior vena cava (IVC) diameter and respirophasic variation are commonly used echocardiographic indices to estimate right atrial pressure. While dilatation of the IVC and reduced collapsibility have traditionally been associated with elevated right heart filling pressures, the significance of isolated IVC dilatation in the absence of raised filling pressures remains poorly understood. We present a case of an asymptomatic 28-year-old male incidentally found to have IVC dilatation, reduced inspiratory collapse, and normal right heart pressures.

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Advanced Hepatocellular Carcinoma with Subtotal Occlusion of the Inferior Vena Cava and a Right Atrial Mass

Case Reports in Vascular Medicine ◽

10.1155/2013/489373 ◽

2013 ◽

Vol 2013 ◽

pp. 1-6 ◽

Cited By ~ 2

Author(s):

Christian Steinberg ◽

Suzanne Boudreau ◽

Felix Leveille ◽

Marc Lamothe ◽

Patrick Chagnon ◽

...

Keyword(s):

Hepatocellular Carcinoma ◽

Inferior Vena Cava ◽

Right Atrium ◽

Inferior Vena ◽

Vena Cava ◽

Great Majority ◽

Right Atrial ◽

Advanced Hepatocellular Carcinoma ◽

Regional Lymph Nodes ◽

The Right

Hepatocellular carcinoma usually metastasizes to regional lymph nodes, lung, and bones but can rarely invade the inferior vena cava with intravascular extension to the right atrium. We present the case of a 75-year-old man who was admitted for generalized oedema and was found to have advanced HCC with invasion of the inferior vena cava and endovascular extension to the right atrium. In contrast to the great majority of hepatocellular carcinoma, which usually develops on the basis of liver cirrhosis due to identifiable risk factors, none of those factors were present in our patient.

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Does Inferior Vena Cava Size Predict Right Atrial Pressures in Patients Receiving Mechanical Ventilation?

Journal of the American Society of Echocardiography ◽

10.1016/s0894-7317(14)80327-1 ◽

1992 ◽

Vol 5 (6) ◽

pp. 613-619 ◽

Cited By ~ 130

Author(s):

John Jue ◽

William Chung ◽

Nelson B. Schiller

Keyword(s):

Mechanical Ventilation ◽

Inferior Vena Cava ◽

Inferior Vena ◽

Vena Cava ◽

Right Atrial

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Pre natal evaluation of heterotaxy syndrome by fetal echocardiography and correlating with autopsy

Ultrasound ◽

10.1177/1742271x19836259 ◽

2019 ◽

Vol 27 (2) ◽

pp. 111-121

Author(s):

Madhavilatha Routhu ◽

Imran Ali Mohammad

Keyword(s):

Inferior Vena Cava ◽

Inferior Vena ◽

Vena Cava ◽

Right Atrial ◽

Heterotaxy Syndrome ◽

Fetal Autopsy ◽

Cardiac Anomalies ◽

Left Isomerism ◽

Right Isomerism ◽

Visceral Heterotaxy

Introduction Heterotaxy syndrome/ isomerism is characterized by an abnormal symmetry of the viscera that are normally dissimilar due to abnormal lateralization of thoracic and abdominal viscera and is frequently associated with complex cardiac anomalies. Isomerism may be of right or left. Materials and methods This article describes the morphological characteristics of heterotaxy and suggests an approach in evaluating the spectrum of abnormalities associated with this syndrome. This study is based on 12 cases diagnosed on antenatal ultrasound as heterotaxy syndrome. Results of the examinations were re-evaluated and compared by fetal autopsy. Result Based on the following echocardiographic criteria, a diagnosis of left isomerism was made if there was viscerocardiac heterotaxy associated with an interruption of inferior vena cava or with bilateral finger-like atrial appendages or if it was associated with heart block. If there was evidence of viscerocardiac heterotaxy with complex cardiac anomalies then it was diagnosed as right atrial isomerism or visceral heterotaxy syndrome. We diagnosed 6/12 as left isomerism and rest of the cases as right isomerism/visceral heterotaxy syndrome. In Autopsy we evaluated visceral situs and morphology of the lungs and the main bronchi, the state of the liver, spleen, bowel, and the precise anatomy of the heart and confirmed 4/12 as left isomerism 4/12 as right isomerism and two cases as visceral heterotaxy syndrome (VHS). Rest of the two cases were included in the study despite missing autopsy data, as the combination of abnormal situs with interrupted inferior vena cava, and cardiac malformation allowed a diagnosis of left isomerism with high probability. Conclusion In this study, we aimed to find common features of heterotaxy syndrome on prenatal ultrasound as well as on fetal autopsy. This syndrome should be accurately diagnosed in the prenatal period in order to allow appropriate counseling of parents.

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