scholarly journals Association of Anomalous Origin of the Right Coronary Artery from the Pulmonary Artery with Aortopulmonary Window. Two case report

2020 ◽  
Vol 5 (6) ◽  

Anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA) is a rare entity. Brooks described first cases in 1885. Only 25% to 30% % of cases are associated with congenital defects such as aortopulmonary window and tetralogy of Fallot. It is recommended the reimplantation of the right coronary artery in the Aorta, with redistribution of coronary flow avoiding the signs of ischemia or other complications even when the diagnosis is done in asymptomatic patients. This is the report of two infants with who debuted with murmur and signs of heart failure. ARCAPA and Pulmonary Aortic Window were diagnosed and they were surgically corrected through intrapulmonary tunneling with a favorable evolution.

2019 ◽  
Vol 30 (1) ◽  
pp. 47-49
Author(s):  
Ali A. Alakhfash ◽  
Mohamad Tagelden ◽  
Abdulrahman Almesned ◽  
Abdullah Alqwaiee

AbstractAortopulmonary window is a rare congenital heart lesion. It might be associated with other CHDs, as well as with anomalous origin of the coronary arteries. Anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA) is the most commonly described coronary artery anomaly in association with aortopulmonary window. We are describing a premature neonate who was diagnosed to have aortopulmonary window and ARCAPA immediately after birth, and had a successful operation at the age of 4 months. This report highlights the importance of very careful assessment of the coronary arteries in patients with aortopulmonary window.


2018 ◽  
Vol 11 (3) ◽  
pp. 325 ◽  
Author(s):  
ChandanaNirmala Chandrashekar ◽  
PadebettuSubramanya Seetharama Bhat ◽  
Divya Mallikarjun ◽  
SL Girish Gowda

2010 ◽  
Vol 1 (2) ◽  
pp. 254-258 ◽  
Author(s):  
Leo A. Bockeria ◽  
David O. Berishvili ◽  
Sofia M. Krupianko ◽  
Andrew V. Sobolev ◽  
Victoria V. Plachova ◽  
...  

2019 ◽  
Vol 46 (3) ◽  
pp. 225-228
Author(s):  
Bryan P. Stefek ◽  
Jason R. Imundo ◽  
Joseph B. Clark

Anomalous origin of the right coronary artery from the pulmonary artery, a rare congenital cardiac defect, is typically not diagnosed during infancy. On the other hand, Turner syndrome is usually diagnosed early, and it is classically associated with bicuspid aortic valve and aortic coarctation. Individuals with Turner syndrome are also at increased risk for coronary artery anomalies. We present a case of anomalous right coronary artery from the pulmonary artery in a week-old neonate who also had Turner syndrome, patent ductus arteriosus, transverse aortic arch hypoplasia, and impaired ventricular function. Prostaglandin therapy through the ductus increased the patient's myocardial perfusion. Four months after corrective surgery, she was doing well. We discuss the reperfusion phenomenon in our patient's case, as well as other considerations in this combination of congenital defects.


2021 ◽  
Vol 11 (1) ◽  
Author(s):  
Francisco Albuquerque ◽  
Pedro de Araújo Gonçalves ◽  
Hugo Marques ◽  
António Ferreira ◽  
Pedro Freitas ◽  
...  

AbstractAnomalous origin of the right coronary artery from the opposite sinus (right-ACAOS) with interarterial course (IAC) has been associated with increased risk of sudden cardiac death (SCD). Widespread use of coronary computed tomography angiography (CCTA) has led to increased recognition of this condition, even among healthy individuals. Our study sought to examine the prevalence, anatomical characteristics, and outcomes of right-ACAOS with IAC in patients undergoing CCTA for suspected coronary artery disease (CAD). We conducted a retrospective analysis of consecutive patients referred for CCTA at one tertiary hospital from January 2012 to December 2020. Patients exhibiting right-ACAOS with IAC were analyzed for cardiac symptoms and mid-term occurrence of first MACE (cardiac death, SCD, non-fatal myocardial infarction (MI) or revascularization of the anomalous vessel). CCTAs were reviewed for anatomical high-risk features and concomitant CAD. Among 10,928 patients referred for CCTA, 28 patients with right-ACAOS with IAC were identified. Mean age was 55 ± 17 years, 64% were male and 11 (39.3%) presented stable cardiac symptoms. Most patients had at least one high risk anatomical feature. During follow-up, there were no cardiac deaths or aborted SCD episodes and only 1 patient underwent surgical revascularization of the anomalous vessel. Right-ACAOS with IAC is an uncommon finding (prevalence of 0.26%). In a contemporary population of predominantly asymptomatic patients who survived this condition well into adulthood, most patients were managed conservatively with a low event rate. Additional studies are needed to support medical follow-up as the preferred option in this setting.


2019 ◽  
Vol 10 (4) ◽  
pp. 508-512
Author(s):  
Vishal Agrawal ◽  
Nikunj Vaidhya ◽  
Mrinal Patel ◽  
Amit Mishra ◽  
Dinesh Patel

Anomalous origin of the left coronary artery (LCA) from the right pulmonary artery (ALCARPA) is an extremely rare subset of an already rare entity, anomalous origin of the LCA from the pulmonary artery. Whenever it is diagnosed preoperatively, one should be extremely vigilant about the potential intramural course of the descending part of the LCA in the aorta. Preoperative imaging frequently fails to delineate this intramural course. We report our experience with one such case where we had accidentally injured the LCA during dissection from the right pulmonary artery. Although it was successfully managed, it reinforces our aforementioned point concerning the importance of vigilance in seeking to identify intramurality as a component of this anomaly of coronary artery origin.


Sign in / Sign up

Export Citation Format

Share Document