scholarly journals Subpulmonary Obstruction Due to Aneurysmal Ventricular Septum in a Patient with Congenitally Corrected Transposition of the Great Arteries and Dextrocardia

2015 ◽  
Vol 10 (1) ◽  
pp. 31-38
Author(s):  
Naveen Sheikh ◽  
Sajal Krishna Banerjee ◽  
Md Zahid Hossain ◽  
Md Tariqul Islam ◽  
Tahmina Karim ◽  
...  

Congenitally corrected Transposition of Great Arteries is usually associated with multiple cardiac defects. Morphologic left-ventricular outflow (pulmonary) tract obstruction due to aneurysm of the membranous ventricular septum in patients with corrected transposition and ventricular septal defect is rare, but was reported in the past. This is even more uncommon in patients with dextrocardia, prompting us to document this case. Absence of the conus with resultant proximity of the aneurysm to the subpulmonary region and higher pressures in the left-sided morphologic right ventricle lead to obstruction of outflow tract in corrected transposition. Echocardiogram with Doppler interrogation and cardiac catheterization with selective cineangiography are the diagnostic tests of choice. Surgical resection of the aneurysm with patch closure of ventricular septal defect, avoiding injury to the conduction system, is recommended.University Heart Journal Vol. 10, No. 1, January 2014; 31-38

2018 ◽  
Vol 11 (4) ◽  
pp. NP190-NP194
Author(s):  
Kuntal Roy Chowdhuri ◽  
Manoj Kumar Daga ◽  
Subhendu Mandal ◽  
Pravir Das ◽  
Amanul Hoque ◽  
...  

The surgical management of d-transposition of great arteries (d-TGAs) with ventricular septal defect (VSD) and left ventricular outflow tract obstruction (LVOTO) is ever evolving and still remains a challenge because of wide anatomic variability, age of presentation, surgical options available, and their variable long-term results in different series. We describe a patient with d-TGA, VSD, and LVOTO who presented to us at 13 years of age and underwent an arterial switch operation along with neoaortic valve replacement with a mechanical prosthesis. The postoperative course was uneventful, and at hospital discharge, the echocardiogram was satisfactory. We present the pros and cons of this hitherto undescribed treatment option.


1993 ◽  
Vol 3 (1) ◽  
pp. 82-84 ◽  
Author(s):  
John J. O'Sullivan ◽  
Desmond J. Farrell ◽  
Archibald S. Hunter

AbstractObstruction to the left ventricular outflow tract is not uncommon in patients with congenitally corrected transposition. A case of congenitally corrected transposition is described with significant subpulmonary obstruction which was due to a subpulmonary tag. The patient required an aortopulmonary shunt. Her clinical course was subsequently significantly influenced by arrhythmias associated with an accessory pathway. She died suddenly from an arrhythmia. Post-mortem examination confirmed a large subpulmonary tag which originated from both sides of the ventricular septum—a previously unreported finding. Careful evaluation of the nature of left ventricular outflow obstruction is important in this condition as it may alter the surgical management.


2011 ◽  
Vol 14 (5) ◽  
pp. 326
Author(s):  
Mehmet U. Ergenoglu ◽  
Halit Yerebakan ◽  
Olcay Ozveren ◽  
Ozge Koner ◽  
Afksendiyos Kalangos ◽  
...  

Congenitally corrected transposition of the great arteries, which is characterized by atrioventricular and ventriculoarterial discordance, is a rare congenital heart disease. Most of the cases are diagnosed in childhood, owing to associated cardiac anomalies, such as ventricular septal defect, pulmonary stenosis or pulmonary atresia, and Ebstein-like malformation of the tricuspid valve. We present a patient with congenitally corrected transposition of the great arteries who underwent surgical replacement of the tricuspid valve with a bioprosthesis and reconstruction of the left ventricular outflow tract with bovine conduit.


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