scholarly journals TETRALOGI FALLOT DAN ATRESIA PULMONAL

2013 ◽  
Vol 4 (3) ◽  
Author(s):  
Alice I. Supit ◽  
Erling D. Kaunang

Abstract: Congenital heart disease is a structural defect due to the malformation of the heart, aorta, and or great blood vessels. It is the most frequent congenital malformation in newborn babies. Tetralogy of Fallot is one of the congenital heart diseases (CHD) with central cyanosis, and covers 5-10% of all CHD. We reported a boy of one year old with Tetralogy of Fallot and pulmonal atresia (ToF-PA), associated with bronchopneumonia. The diagnosis was based on anamnesis, physical examination, and other supporting examinations. The chest X-ray showed a normal sized heart (CTR 57%) with coer-en-sabot shape, and right and left parahilar infiltration, which resulted in bronchopneumonia and ToF. The electrocardiography showed a right deviation of axis and a hypertrophy of the right ventricle; the echocardiography showed a right ventricle hypertrophy, an over-riding aorta, a large malalignment of the ventricular septal defect, no visualization of pulmonar artery, and no visualization of patent ductus arteriosus (PDA). Conclusion: Based on all the tests performed, the diagnosis of this patient was Tetralogy of Fallot and pulmonal atresia (ToF-PA), associated with bronchopneumonia. The prognosis related to bronchopneumonia in this case was good due to the use of antibiotics. Keywords: tetralogy of Fallot, pulmona atresia, bronchopneumonia.  Abstrak: Penyakit jantung bawaan (PJB) ialah kelainan struktural akibat malformasi jantung, aorta dan atau pembuluh darah besar, dan merupakan kelainan kongenital tersering pada bayi baru lahir. Tetralogi Fallot merupakan salah satu PJB dengan sianosis sentral, dan mencakup 5-10% dari seluruh PJB. Kami melaporkan kasus seorang anak laki-laki berusia satu tahun dengan Tetralogi Fallot dan atresia pulmonal (ToF-PA) disertai bronkopneumonia. Diagnosis ditegakkan melalui anamnesis, pemeriksaan fisik, dan pemeriksaan penunjang. Hasil ekspertisi foto toraks AP memperlihatkan ukuran jantung normal (CTR 57%) berbentuk coer-en-sabot, dan pada paru-paru terlihat infiltrat parahilar kanan dan kiri serta corakan vaskular paru berkurang yang menunjukkan suspek bronkopneumonia dan ToF. Elektrokardiografi memperlihatkan deviasi aksis ke kanan dan hipertrofi ventrikel kanan, dan pada ekokardiografi tampak right ventricle hypertrophy, overriding aorta, VSD malalignment besar, tidak tampak visualisasi arteri pulmonal, dan tidak tampak patent ductus arteriosus (PDA) dengan hasil Tetralogi Fallot dan atresia pulmonal. Simpulan: Berdasarkan hasil pemeriksaan yang dilakukan, diagnosis pasien ini ialah Tetralogi Fallot dan atresia pulmonal (ToF-PA) disertai bronkopneumonia. Prognosis bronkopenumonia pada kasus ini baik yang dapat diatasi dengan antibiotika.Kata kunci: tetralogi Fallot, atresia pulmonal, bronkopneumonia.  

Author(s):  
Iuliu Scurtu ◽  
Cosmin Pestean ◽  
Radu Lacatus ◽  
Meda Lascu ◽  
Mircea Mircean ◽  
...  

Introduction: PDA represents one of the most frequently diagnosed type of congenital heart disease. Ductus arteriosus is a normal structure in foetal life, which permits shunting of oxygenated blood from the pulmonary artery into the aorta. Failure of sealing after birth is an abnormal condition and is called patent ductus arteriosus. In normal PDA, due to fact that systemic pressure is fivefold higher than pulmonary circulation, blood is shunted from the aorta into the pulmonary artery. In reverse PDA, pulmonary artery pressure does not drop after birth, and blood will be shunted form right to left. Aims: We want to evaluate clinical, haematological, ECG and echocardiographic changes in case of reverse PDA. Materials and Methods: Two-year old female Bichon Frise was referred to our clinic with signs of effort intolerance and dyspnoea for more than a year. ECG was performed in the right lateral recumbency using a digital device and echocardiography was done with Esaote MyLab40 Vet with a phased array transducer matched with the size of the dog (7.5 MHz). Results: We identified a dog with a good body score, quite alert and without any sign of illness. Haematological investigation underlined polycythaemia and very high PCV. The ECG revealed a normal sinus rhythm with a deep S wave, changes consistent with right ventricle enlargement.  Right atrial dilation and right ventricle hypertrophy were found on cardiac ultrasonography. The right ventricle free wall was hypertrophied and interventricular septum was flattened, changes consistent with increased pressure on the right side of the heart. The left heart was small. Positive diagnosis was done, performing “bubble study” and identification of contrast bubble within the abdominal aorta.   Conclusion: Reverse PDA is a rarely diagnosed congenital heart disease. Polycythaemia in young dogs could raise the suspicion of reverse PDA.  For positive diagnosis, echocardiography and bubble study are required. ECG is not a sensitive tool for diagnosis.


2018 ◽  
Vol 26 (7) ◽  
pp. 756-759 ◽  
Author(s):  
Hua Chun ◽  
Yan Yue ◽  
Yibin Wang ◽  
Zhaxi Dawa ◽  
Pu Zhen ◽  
...  

Background Previous small sample studies suggested that elevated altitudes might be associated with the incidence of cardiovascular diseases. However, it remains uncertain whether high altitudes (over 3000 m above sea level) are related to congenital heart disease. We therefore explored the prevalence of congenital heart disease in a large cohort of students in the world's largest prefecture-level city with the highest altitude. Methods This cross-sectional study included 84,302 student participants (boys 52.12%, girls 47.88%, with an average age of 10.62 ± 3.33 years). Data were extracted from the screening results among different altitude area schools in Nagqu from June 2016 to August 2017. Students were first screened by performing a physical examination consisting of cardiac auscultations and clinical manifestation screenings. An echocardiography was performed to confirm and identify the subtype of congenital heart disease. Results The prevalence of congenital heart disease among students in Nagqu, Tibet, was 5.21‰ (439 cases). The most common congenital heart disease type was patent ductus arteriosus, representing 66.3% of congenital heart diseases diagnosed in this study, followed by atrial septal defect and ventricular septal defect, representing 20.3% and 9.1% of congenital heart diseases, respectively. Students living in higher altitudes were significantly more prone to have congenital heart disease than students in locations with lower altitudes. The prevalence of congenital heart disease in girls was found to be higher than that of boys. Conclusions The correlation between congenital heart disease and increased altitude is noteworthy. This study's results are the first big data epidemiological investigation to confirm that high altitude is a significant environmental risk factor for congenital heart disease, especially patent ductus arteriosus. Furthermore, the results provide additional support to make a diagnostic and treatment plan to prevent congenital heart disease in high altitude areas.


PEDIATRICS ◽  
1960 ◽  
Vol 25 (3) ◽  
pp. 531-S-560
Author(s):  
Benjamin M. Gasul ◽  
Rene A. Arcilla ◽  
Egbert H. Fell ◽  
Joshua Lynfield ◽  
J. Pedro Bicoff ◽  
...  

Five patients with congenital coronary arteriovenous fistula communicating with the right ventricle are presented. Case 5, a 3-week-old infant, represents the youngest patient to be diagnosed and studied, in the literature. The clinical features, hemodynamics and angiocardiographic findings are analyzed. Two major types of fistula affecting the coronary arterial system are recognized. In coronary arteriovenous fistula the functional disturbance consists of a left-to-right shunt, and a diastolic overloading of the left heart chambers and of the right heart chambers into which the fistula opens. In coronary arterio-systemic fistula the altered hemodynamics are essentially those of an internal fistula confined to the systemic circulation. A postulate regarding the nature of the blood flow through the various types of fistulae is given, and this is correlated with the phonocardiographic and hemodynamic findings. The diagnosis should be strongly suspected on the basis of a loud, superficial and continuous cardiac murmur localized in an area atypical for a patent ductus arteriosus. If the continuous murmur is maximal at the pulmonary area, it is extremely difficult to differentiate this anomaly from a patent ductus arteriosus and/or aortic-pulmonary septal defect. Phonocardiographic demonstration of a louder diastolic than systolic component is very suggestive of a coronary arteriovenous fistula communicating with the right ventricle. The roentgenologic and electrocardiographic findings are not specific. Cardiac catheterization is not diagnostic, although when correlated with the clinical picture it may strongly suggest the diagnosis. Angiocardiography, particularly retrograde aortography, is diagnostic. The information obtained from the various methods used is discussed. Dilatation of the ascending aorta demonstrated by angiocardiography was a constant finding in our series. Its pathogenesis is discussed, and its importance as a differential sign in the angiocardiogram against the diagnosis of ventricular septal defect is stressed. The differential diagnosis by retrograde aortography between coronary arteriovenous fistula into the right ventricle and ruptured aortic sinus of Valsalva into the same chamber is discussed and illustrated. While this anomaly is compatible with longevity, the potential complications to which the patient with it may be subjected and the relative innocuousness of corrective surgery without the need for hypothermia or cardiopulmonary bypass, demonstrated in previous reports and in our series, make us believe that surgery should be considered in practically all cases of fistula of the coronary arterial system.


PEDIATRICS ◽  
1949 ◽  
Vol 3 (5) ◽  
pp. 597-602
Author(s):  
RICHARD C. BROWN ◽  
JOHN D. BURNETT

The occurrence of a congenital vascular tract between the left posterior aortic sinus of Valsalva and the right ventricle in a 13 month old boy is reported. A group of cardiovascular anomalies which clinically resemble a patent ductus arteriosus is discussed, and the help which cardiac catheterization may give in confirming the diagnosis is indicated.


2016 ◽  
Vol 53 (5) ◽  
pp. 291
Author(s):  
Mulyadi M Djer ◽  
Nikmah Salamia Idris ◽  
Angelina Angelina

Patent ductus arteriosus (PDA) is a common congenital heart disease, accounting for 5-10% of all congenital heart diseases. The incidence of PDA is even higher in preterm neonates, ranging from 20-60%.1-4 Closure of PDA is indicated in all cases, except for duct-dependent congenital heart diseases or PDA with Eisenmenger syndrome.1,5,6 In small asymptomatic PDAs, closure is indicated to prevent the risk of complications, such as endarteritis, endocarditis, aneurysm of ductus arteriosus, or congestive heart failure.1,2,7In recent years, interventional cardiology has become a gold standard therapy for the majority of PDA cases beyond neonatal age. Since its introduction in 1967, many devices and methods have been developed to allow transcatheter closure of virtually all PDAs, regardless of size or configuration. Nevertheless, the tubular shape (type C) PDA, which has the highest residual shunt rate, still poses a great challenge for the interventionist.8-10 The second generation of Amplatzer® device occluders (ADO II), released in 2007, has been suggested to be effective in closing tubular PDAs.10 The purpose of this study was to report the initial clinical experience using ADO II to close a tubular type PDA in Indonesia.


PEDIATRICS ◽  
1948 ◽  
Vol 2 (3) ◽  
pp. 325-334
Author(s):  
STANLEY GIBSON

Since it would appear that the diagnosis of patent ductus arteriosus can be made accurately in such a high percentage of cases and that the surgical treatment of this lesion is highly successful with a low mortality and morbidity rate, we believe surgery is advisable in all cases with this lesion excepting the 35-year-old or older group who have no progressive cardiac hypertrophy and no incapacitation by virtue of their fistula. The optimum age for operation is three years. The vast majority of the patients have a ductus that can be divided and the advantages of division over ligation have been pointed out. Patent ductus arteriosus complicated by subacute bacterial endocarditis should have surgery following intensive penicillin therapy.


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