A CASE OF MRI-NEGATIVE HERPES VIRUS ENCEPHALITIS PRESENTED BY RAMSAY HUNT SYNDROME

2020 ◽  
Vol 73 (11) ◽  
pp. 2555-2556
Author(s):  
Pavel A. Dyachenko ◽  
Anatoly G. Dyachenko

Ramsay Hunt syndrome (RHS) occurs due to reactivation of latent Varicella Zoster Virus (VZV) infection in the geniculate ganglion of the facial nerve. Major clinical symptoms include ipsilateral facial paralysis, otic pain, and herpetic vesicles (rashes) along the nerve with accompanying ear pain. Rarely clinical findings include retrograde transaxonal spread of the virus from the ganglion into the brain parenchyma with developing the encephalitis or multiple cranial nerve involvement. We describe here a patient with both RHS along with complicating brains

2019 ◽  
Vol 112 (1) ◽  
pp. 19-23
Author(s):  
Yusuke Hishimura ◽  
Hiroshi Shinohara ◽  
Hironari Shimizu ◽  
Saeko Yoshida ◽  
Mika Nakano

2019 ◽  
Vol 2019 ◽  
pp. 1-5
Author(s):  
Vijay Letchuman ◽  
Charles D. Donohoe

We present a case of a 62-year-old Caucasian male with laryngeal cancer and Ramsay Hunt Syndrome otherwise known as herpes zoster oticus due to reactivation of the varicella zoster virus. Classic findings include the triad of ipsilateral facial paralysis, otic pain, and herpetic lesions in the sensory supply of the facial nerve. The common pathogenesis is associated with anterograde axonal reactivation of the varicella zoster virus in the geniculate ganglion. Unique features of our case include retrograde transaxonal spread of the varicella-zoster virus from the geniculate ganglion into the brainstem and cerebellum including involvement of the abducens nucleus, facial nucleus, middle cerebral peduncle, and inferior cerebellar peduncle. This presented as left facial paralysis, left sixth nerve palsy, horizontal diplopia to the left lateral gaze, profound truncal ataxia, and left-sided dysmetria. Clinical awareness that Ramsay Hunt syndrome may also involve the brainstem and cerebellum is critical in evaluating the clinical neurologic findings and expanding the diagnostic workup to include brain magnetic resonance imaging and cerebrospinal fluid analysis, including varicella zoster polymerase chain reaction. Encephalitis requires longer duration administration of high-dose intravenous acyclovir in conjunction with steroids. Delays in treatment are often associated with unsatisfactory outcomes with extensive residual deficits.


2014 ◽  
Vol 2014 ◽  
pp. 1-3 ◽  
Author(s):  
Serhan Derin ◽  
Hatice Derin ◽  
Murat Sahan ◽  
Hüseyin Çaksen

Ramsay Hunt syndrome (RHS) is characterized by facial paralysis, inner ear dysfunction, periauricular pain, and herpetiform vesicles. The reported incidence in children is 2.7/100,000. The pathogenesis involves the reactivation of latent varicella zoster virus (VZV) in the geniculate ganglion of the facial nerve. The recovery rate is better in children than in adults. This paper discusses a 12-year-old girl with a rare case of peripheral facial paralysis caused by RHS and reviews the literature.


2014 ◽  
Vol 2014 ◽  
pp. 1-5
Author(s):  
Yoshio Nagayama ◽  
Naoki Matsushiro ◽  
Akihide Nampei ◽  
Hideo Hashimoto ◽  
Kenrin Shi

A 39-year-old female patient with rheumatoid arthritis developed Ramsay Hunt syndrome after infliximab treatment. This condition is caused by the reactivation of varicella zoster virus infection in the geniculate ganglion of facial nerve in the host’s immunosuppression. She was treated immediately with valaciclovir and hydrocortisone, and the complete recovery was achieved at 6 months after the onset. This is the first report of Ramsay Hunt syndrome as an adverse effect of infliximab in rheumatoid arthritis.


2012 ◽  
Vol 18 (2) ◽  
pp. 231-233
Author(s):  
KA Al Mahmud ◽  
Kamal Uddin ◽  
Maleka Afroz

Ramsay Hunt Syndrome classically presents with VII nerve palsy. Other cranial nerve involvement is rare. We describe a case here who presented with VII, IX and X cranial nerve palsies and review the literature. DOI: http://dx.doi.org/10.3329/bjo.v18i2.12029 Bangladesh J Otorhinolaryngol 2012; 18(2): 231-233


2021 ◽  
Author(s):  
Ney Adson Leal II ◽  
Nágila Pereira Mendes ◽  
Caroline Moraes Tapajós Bolzani ◽  
Hilton Mariano da Silva Junior

Context: Ramsay Hunt Syndrome (RHS), also named Optic Herpes Zoster is caused by the reactivation of Varicella-Zoster Virus that occurs in the geniculate ganglion. The classic syndrome is composed of vesicular lesions in the ear, ipsilateral otalgia and peripheral facial palsy. The onset of the syndrome with persistent hemicrania is absolutely atypical as a manifestation of RHS. Case report: A 69 year old woman with subacute onset of left exclusive hemicrania in moderate strong intensity without autonomic signs. Eight days after the onset of headache, she presented left peripheral facial paralysis and after 4 days, she noticed the appearance of vesicles in the left ear and pain in swallowing. She has developed nausea with several episodes of vomiting, important imbalance that made impossible gait. On physical examination she presented vesicles in the left ear and oropharynx, left peripheral facial paralysis House Brackmann grade IV, left hypoacusis, nystagmus and vestibular gait. The brain CT and cerebrospinal fluid analysis were normal. The patient has progressive improvement with Acyclovir. Conclusions: Otalgia or even intermediate neuralgia are more frequent painful manifestations of RHS. This case report highlights the need to consider the diagnosis of SRH in patients with persistent hemicrania, even if without initial classic signs of the syndrome.


Author(s):  
Margarida Gaudencio ◽  
Maria Inês Bertão ◽  
André Carvalho ◽  
Gabriela Pena ◽  
Isabel Bessa ◽  
...  

Ramsay Hunt syndrome is a rare complication of herpes zoster that results from reactivation of varicella-zoster virus in the geniculate ganglion of the VII cranial nerve. Immunosuppression can lead to reactivation of latent varicella-zoster virus, resulting in herpes zoster. Here, we present a case of Ramsay Hunt syndrome in a patient with ulcerative colitis under treatment with infliximab.


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