scholarly journals Cholesteatoma secondary to extensive face cutaneous hemangioma

2021 ◽  
Vol 50 ◽  
pp. e202150129
Author(s):  
Larissa Parrela Rodrigues ◽  
Laura Isoni Auad ◽  
Bárbara Andrade Lima ◽  
Vanessa Ribeiro Orlando ◽  
Mirian Cabral Moreira de Castro
Keyword(s):  
Neurosurgery ◽  
2002 ◽  
Vol 51 (5) ◽  
pp. 1275-1279 ◽  
Author(s):  
Michael J. Alexander ◽  
Peter M. Grossi ◽  
Robert F. Spetzler ◽  
Cameron G. McDougall

Abstract OBJECTIVE AND IMPORTANCE Spinal cord involvement in Klippel-Trenaunay-Weber (KTW) syndrome is rare. Cases of intradural spinal cord arteriovenous malformations (AVMs) have been associated with this syndrome. Likewise, cases of epidural hemangioma and angiomyolipoma have been reported to occur at the same segmental level as cutaneous hemangioma in KTW syndrome. This report details a rare case of an extradural thoracic AVM in a patient with KTW syndrome. CLINICAL PRESENTATION A 30-year-old man presented with a 10-month history of progressive myelopathy, bilateral lower-extremity weakness, and numbness, with the right side affected more than the left. His symptoms had progressed to the point that he was unable to walk. The patient had the characteristic manifestations of KTW syndrome, including numerous cutaneous angiomas and cavernomas, limb hypertrophy and syndactyly, and limb venous malformations. A magnetic resonance imaging scan and subsequent angiogram demonstrated a large extradural AVM causing cord compression at the T3–T4 levels. INTERVENTION The patient underwent two separate endovascular procedures, including embolization of upper thoracic and thyrocervical trunk feeders. Subsequently, he underwent T1–T4 laminectomy and microsurgical excision of the AVM. Clinically, the patient improved such that he could walk without assistance. CONCLUSION KTW syndrome represents a spectrum of clinical presentations. Although involvement of the spinal cord is uncommon, the manifestations of this syndrome may include both intradural and extradural AVMs in addition to various tumors.


1993 ◽  
Vol 12 (11) ◽  
pp. 683-687 ◽  
Author(s):  
M C Treadwell ◽  
W Sepulveda ◽  
L L LeBlanc ◽  
R Romero

2016 ◽  
Vol 2016 ◽  
pp. 1-4 ◽  
Author(s):  
Siu Ying Angel Nip ◽  
Kam Lun Hon ◽  
Wing Kwan Alex Leung ◽  
Alexander K. C. Leung ◽  
Paul C. L. Choi

Hemangioma is the most common vascular tumor of infancy; presentation is often as cutaneous infantile hemangioma (IH). Cutaneous hemangioma is a clinical diagnosis. Most IHs follow a benign course, with complete involution without treatment in the majority of cases. Visceral hemangioma often involves the liver and manifests as a life-threatening disorder. Hepatic hemangiomas may be associated with high output cardiac failure, coagulopathy, and hepatomegaly which generally develop between 1 and 16 weeks of age. Mortality has been reportedly high without treatment. We report a rare case of a male infant with neonatal hemangiomatosis with diffuse peritoneal involvement, which mimicked a malignant-looking tumor on imaging, and discuss therapeutic options and efficacy. Propranolol is efficacious for IH but generally not useful for other forms of vascular hemangiomas, tumors, and malformations. In our case of neonatal peritoneal hemangiomatosis, propranolol appears to have halted the growth and possibly expedite the involution of the hemangiomatosis without other treatments.


1978 ◽  
Vol 33 (10) ◽  
pp. 668-671
Author(s):  
RUBEN SHTURMAN-ELLSTEIN ◽  
MARIA ALBA GRECO ◽  
CARMEN MYRIE ◽  
ELIZABETH K. GOLDMAN

2006 ◽  
Vol 37 (1) ◽  
pp. 59-60 ◽  
Author(s):  
Nathalie France Mauroo ◽  
Natalie Louise Rourke ◽  
Wai Kong Chan

2017 ◽  
Vol 13 (3) ◽  
pp. 1861-1865
Author(s):  
Fagang Wang ◽  
Rongjian Xu ◽  
Qian Xu ◽  
Yongqian Cao ◽  
Li Lin ◽  
...  

2007 ◽  
Vol 22 (3) ◽  
pp. 337-340 ◽  
Author(s):  
I. Pascual-Castroviejo ◽  
J.C. Lopez-Gutierrez
Keyword(s):  

1978 ◽  
Vol 67 (2) ◽  
pp. 239-243 ◽  
Author(s):  
RUBEN SHTURMAN-LLSTEIN ◽  
MARIA ALBA GRECO ◽  
CARMEN MYRIE ◽  
ELIZABETH K. GOLDMAN

2009 ◽  
Vol 10 (5) ◽  
pp. 430-435 ◽  
Author(s):  
Walter D. Johnson ◽  
Michelle M. Petrie

Cobb syndrome is a rare clinical entity that includes the combination of a vascular skin nevus and an angioma in the spinal canal present at identical dermatomal level(s) (cutaneomeningospinal angiomatosis). To date, 38 cases have been reported, only 18 of which are in adults (> 18 years of age). The majority of these cases have been described in the era predating current neuroimaging techniques, and most authors have assumed that each case involves similar vascular pathology. This report highlights 2 patients presenting with similar thoracic cutaneous vascular nevi yet with markedly differing spinal vascular pathology. A 29-year-old man presented with cutaneous hemangioma and a progressive paraparesis and paresthesia of the lower extremities. A 20 × 20–cm port-wine stain over his right upper midback (T6–10) correlated precisely with MR imaging that demonstrated an enhancing epidural mass between T-6 and T-10 causing compression of the cord and cord edema. A 34-year-old man also presented with progressive myelopathy and a 15 × 20–cm port-wine stain within the same dermatomal region as a Type III spinal arteriovenous malformation. Workup for each patient included pre- and postoperative contrast-enhanced MR imaging with vascular sequencing and spinal angiography. The first patient was treated with bilateral laminectomy at the T6–10 levels, with significant postoperative improvement in motor strength. The second patient underwent coil embolization of an intranidal aneurysm, with follow-up embolization 8 years later. Cobb syndrome is an unusual entity in the adult population and should be considered when there is a constellation of cutaneous manifestation and underlying neurological deficit. The vascular skin nevus associated with Cobb syndrome is accompanied by a wide variety of vascular pathologies.


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