scholarly journals Renal primitive neuroectodermal tumour in childhood: Case report and review of literature

2013 ◽  
Vol 4 (6) ◽  
pp. 158 ◽  
Author(s):  
Maeed Asiri ◽  
Ahmed Al-Sayyad
Keyword(s):  
Axial Skeleton ◽  
Pathology Report ◽  
Combined Modality Treatment ◽  
Rare Entity ◽  
Review Of Literature ◽  
Rare Tumour ◽  
Primitive Neuroectodermal Tumour ◽  
Neuroectodermal Tumour ◽  
Local Tumour ◽  
Renal Pnet

Primitive neuroectodermal tumour (PNET) is presumed to be ofneural crest origin, mostly presenting as bone or soft tissue masses.It usually occurs in the trunk or axial skeleton; while renal PNET isconsidered an extremely rare tumour. We report a case of 11-yearoldmale who presented with right flank pain and gross hematuriaafter suffering blunt trauma. During investigations, he was found tohave a large renal mass on computed tomography. He underwenta right radical nephrectomy where the pathology report showedPNET of the kidney. The patient received chemotherapy afterwards.Despite the chemotherapy, he had a local tumour recurrence 3months after and continued to deteriorate and developed distantmetastasis. Primitive neuroectodermal tumour of the kidney is adistinct and rare entity. It is very aggressive, with a poor survivaldespite combined modality treatment.

Primitive neuroectodermal tumour (PNET) of the renal capsule mimicking solid adrenal tumour

2020 ◽  
Vol 13 (10) ◽  
pp. e235484
Author(s):  
Amrin Israrahmed ◽  
Somesh Singh ◽  
Hira Lal ◽  
Manoj Jain
Keyword(s):  
Adrenal Gland ◽  
Large Mass ◽  
Rare Entity ◽  
Renal Capsule ◽  
Review Of Literature ◽  
Adrenal Tumour ◽  
Primitive Neuroectodermal Tumour ◽  
Neuroectodermal Tumour ◽  
Suprarenal Mass ◽  
The Right

Primitive neuroectodermal tumour (PNET) of renal capsule is a rare entity. We report a case of a 17-year-old girl, who presented with symptoms of epigastric and right hypochondrium pain since 1 year. She was afebrile and physical examination revealed a soft, non-tender, firm, bimanually palpable and ballotable mass along right flank. Ultrasound abdomen showed a large heteroechoic mass in right suprarenal region with indistinct planes with upper pole of right kidney. On CT, a large right suprarenal mass was noted with origin likely from right adrenal gland. Surgery was done and intraoperatively, the large mass in right suprarenal region showed involvement of the upper pole of the right kidney. The right adrenal gland was small in size, compressed and displaced by the lesion. Histopathology revealed the mass to be PNET of kidney. We report the relevant imaging findings of the case with review of literature of this entity.

scholarly journals Primary Ewing’s Sarcoma/Primitive Neuroectodermal Tumour of the Cervix: a Rare Tumour

2019 ◽  
Vol 11 (1) ◽  
pp. 162-165
Author(s):  
Vikas Gupta ◽  
K. V. V. N. Raju ◽  
D. Sridhar ◽  
Syed Murtaza Ahmed ◽  
Daphne Fonseca
Keyword(s):  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Rare Tumour ◽  
Primitive Neuroectodermal Tumour ◽  
Neuroectodermal Tumour

scholarly journals A Rare Case of Primitive Neuroectodermal Tumour (Pnet) of Kidney with Review of Literature

2016 ◽  
Vol 4 (3) ◽  
pp. 445-447
Author(s):  
Narendra Kumar ◽  
◽  
Deepak Das ◽  
Vijai Simha ◽  
Vani Bharani ◽  
...  
Keyword(s):  
Rare Case ◽  
Review Of Literature ◽  
Primitive Neuroectodermal Tumour ◽  
Neuroectodermal Tumour

scholarly journals Surgical experience with a huge supratentorial primitive neuroectodermal tumour in a 3 years old boy

1970 ◽  
Vol 9 (3) ◽  
pp. 177-182
Author(s):  
MJ Islam ◽  
SK Saha ◽  
AM Khan ◽  
MI Khalil
Keyword(s):  
Poor Prognosis ◽  
Medical Science ◽  
Pathological Finding ◽  
Malignant Tumour ◽  
Surgical Experience ◽  
Total Removal ◽  
Rare Tumour ◽  
Primitive Neuroectodermal Tumour ◽  
Neuroectodermal Tumour ◽  
Visual Disturbances

The concept of Primitive Neuroectodermal Tumor (PNET) has been evolving for many years, since its nomenclature has been done. A 3 years old boy presented with unable to stand and walk, vertigo, vomiting and visual disturbances. MRI of brain revealed suggestive of malignant tumour with intratumoral hemorrhage involving the frontotemporo- parietal region. A gross total removal of tumor was achieved through craniotomy. The pathological finding was consistent with PNET. This case is an exclusive one as it was huge size. Supratentorial PNETs are rare tumour and carry poor prognosis. Newer modalities of treatment should be tried to improve survival. Key words: Supratentorial Primitive Neuroectodermal Tumour; Radiotherapy; Chemotherapy. DOI: 10.3329/bjms.v9i3.6482Bangladesh Journal of Medical Science Vol.09 No.3 July 2010, pp.177-182

scholarly journals Fetus in Fetu (Pre-surgical dilemma: Review of literature and a case report)

2011 ◽  
Vol 2 (1) ◽  
pp. 68-71
Author(s):  
Om Prakash Sharma ◽  
Senthil Shanmugam
Keyword(s):  
Case Report ◽  
Ct Scan ◽  
Abdominal Distension ◽  
Axial Skeleton ◽  
Rare Entity ◽  
Review Of Literature ◽  
Medical Sciences ◽  
Monochorionic Twins ◽  
Fetus In Fetu ◽  
X Ray

Fetus in fetu is an extremely rare developmental anomaly, due to disorganised embryogenesis in a diamniotic monochorionic pregnancy. Approximately 87 reports have been documented in the literature to date. We describe such an entity in two months old boy, who presented with abdominal distension and features of obstruction. Plain X ray abdomen and CT scan helped in correct pre operative diagnosis. The literature on this rare entity is reviewed, and the diagnosis and pathogenesis of the disease are discussed. Key Words: Fetus in fetu; CT scan; Teratoma; Axial skeleton; Diamniotic monochorionic twins DOI: 10.3126/ajms.v2i1.3208 Asian Journal of Medical Sciences 2 (2011) 68-71

Sign in / Sign up

Export Citation Format

Share Document