Primitive neuroectodermal tumour (PNET) of the renal capsule mimicking solid adrenal tumour

2020 ◽  
Vol 13 (10) ◽  
pp. e235484
Author(s):  
Amrin Israrahmed ◽  
Somesh Singh ◽  
Hira Lal ◽  
Manoj Jain

Primitive neuroectodermal tumour (PNET) of renal capsule is a rare entity. We report a case of a 17-year-old girl, who presented with symptoms of epigastric and right hypochondrium pain since 1 year. She was afebrile and physical examination revealed a soft, non-tender, firm, bimanually palpable and ballotable mass along right flank. Ultrasound abdomen showed a large heteroechoic mass in right suprarenal region with indistinct planes with upper pole of right kidney. On CT, a large right suprarenal mass was noted with origin likely from right adrenal gland. Surgery was done and intraoperatively, the large mass in right suprarenal region showed involvement of the upper pole of the right kidney. The right adrenal gland was small in size, compressed and displaced by the lesion. Histopathology revealed the mass to be PNET of kidney. We report the relevant imaging findings of the case with review of literature of this entity.

2013 ◽  
Vol 4 (6) ◽  
pp. 158 ◽  
Author(s):  
Maeed Asiri ◽  
Ahmed Al-Sayyad

Primitive neuroectodermal tumour (PNET) is presumed to be ofneural crest origin, mostly presenting as bone or soft tissue masses.It usually occurs in the trunk or axial skeleton; while renal PNET isconsidered an extremely rare tumour. We report a case of 11-yearoldmale who presented with right flank pain and gross hematuriaafter suffering blunt trauma. During investigations, he was found tohave a large renal mass on computed tomography. He underwenta right radical nephrectomy where the pathology report showedPNET of the kidney. The patient received chemotherapy afterwards.Despite the chemotherapy, he had a local tumour recurrence 3months after and continued to deteriorate and developed distantmetastasis. Primitive neuroectodermal tumour of the kidney is adistinct and rare entity. It is very aggressive, with a poor survivaldespite combined modality treatment.


Author(s):  
Christine U. Lee ◽  
James F. Glockner

1-month-old female infant with a renal or adrenal mass Axial fat-suppressed FSE T2-weighted images (Figure 6.11.1) reveal a large mass originating from the right adrenal gland with heterogeneously increased signal intensity. Extensive small hyperintense metastases essentially replace the visualized hepatic parenchyma. Axial fat-suppressed FSE images from the 6-week follow-up examination (...


2014 ◽  
Vol 4 (1) ◽  
Author(s):  
Aftab S. Shaikh ◽  
Girish D. Bakhshi ◽  
Arshad S. Khan ◽  
Nilofar M. Jamadar ◽  
Aravind Kotresh Nirmala ◽  
...  

Adrenal sarcomatoid carcinomas are extremely rare tumors presenting with extensive locoregional spread at the time of diagnosis. Patients succumb to metastases within a couple of months. As a result, very few cases are reported in the literature until now. We present a case of a 62-year old female with non-functional sarcomatoid carcinoma of the right adrenal gland. There was no radiological evidence of locoregional metastases. Patient underwent right adrenalectomy. Follow up after 3 months showed para-aortic lymphadenopathy and similar left adrenal mass on computed tomography. Patient refused further treatment and succumbed to the disease. A brief case report with review of literature is presented.


2013 ◽  
Vol 16 (1) ◽  
pp. 47-48 ◽  
Author(s):  
I Monowarul ◽  
ATM Amanullah ◽  
AKMK Alam

Angiomyolipoma are commonly found in Kidney but extrarenal sites are also mentioned. It arising in adrenal is very rare entity, usually asymptomatic, diagnosed incidentally on radiological investigation of abdomen for other conditions. We report our experience with a 37-year-old man who presented with sudden feeling of jerking discomfort and generalized weakness. An USS showed adrenal mass, computerised tomography (CT) scan confirmed and outlined the adrenal mass.Adrenalectomy was performed and the histopathological features confirmed the diagnosis of adrenal angiomyolipoma. The patient recovered without any complications following surgery. DOI: http://dx.doi.org/10.3329/jss.v16i1.14449 Journal of Surgical Sciences (2012) Vol. 16 (1) : 47-48


2019 ◽  
Vol 15 (04) ◽  
pp. 206-211
Author(s):  
José Alberto Carranco Dueñas ◽  
Genny Sánchez Hernández ◽  
Rosa Edith Gálvez Martínez

Abstract Salmonella osteomyelitis is a rare entity, typically associated with hemoglobinopathies or other underlying disorders. We report a case of Salmonella osteomyelitis of the right knee in an otherwise healthy 1-year-old boy. He received 8 weeks (2 weeks intravenous and 6 weeks oral) of antibiotic treatment, with full recovery.


Author(s):  
Mamta Gupta ◽  
Rita Jindal ◽  
Supriya Kumari ◽  
Namrata Nargotra

ABSTRACT Introduction Leiomyoma arising from the vagina is a rare entity with varied presentations. Case Report A woman 44 years of age presented with complaints of something coming out vaginally, polymenorrhea, and pain in abdomen. A mass arising from the right posterolateral wall of vagina was seen. Ultrasound reported it to be cervical fibroid. The mass was enucleated through vaginal route. Histopathology confirmed it to be a leiomyoma. Review of literature revealed that it has a varied presentation. Diagnosis is often missed. Conclusion The condition should always be kept in mind whenever coming across any mass in vagina. How to cite this article Gupta M, Saini V, Jindal R, Kumari S, Nargotra N. Vaginal Leiomyoma: Case Report and Literature Review. J South Asian Feder Menopause Soc 2017;5(1):62-65.


2007 ◽  
Vol 32 (4) ◽  
pp. 460-461 ◽  
Author(s):  
S. JAYAKUMAR ◽  
S. JATAVALABULLA ◽  
I. M. MILLER

We present a case of a 28 year-old woman who presented with a peripheral primitive neuroectodermal tumour of the right hand involving the fifth metacarpal and little finger. She underwent excision biopsy, then ray amputation of her right little finger. Initial radiological staging did not reveal metastasis but, after recurrence locally at two years and in spite of adjuvant chemotherapy and radiotherapy, the patient died of progressive metastatic disease 4 years later. The current concepts and difficulties in diagnosing these tumours are discussed.


2018 ◽  
Vol 1 (1) ◽  
pp. 125-128
Author(s):  
Guermazi F ◽  
Meddeb K ◽  
Mokrani A ◽  
Charfi L ◽  
Abouda HS ◽  
...  

Small cell carcinoma of the ovary hypercalcemic type (SCCOHT) is an exceedingly rare aggressive malignancy. It typically affects young women. Herein we aimed to report a case of a 28-year-old woman treated for SCCOHT in Salah Azaiez Institute. The tumor was revealed by a delay of menses. The imaging found a large mass of the right ovary. The patient underwent a bilateral salpingo-oophorectomy, a total hysterectomy and a pelvic and a para-aortic lymphadenectomy. She subsequently received 6 cycles of adjuvant chemotherapy. Three years later, she presented a metastatic bone relapse.


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