Hybrid Congenital Lung Malformation with Difficulty in Diagnosis and Treatment: Congenital Cystic Adenoid Malformation and Pulmonary Sequestration Co-existence

We report the case of a neonate affected by prenatally diagnosed congenital diaphragmatic hernia (CDH), treated by thoracoscopy. During the procedure, we detected an associated extralobar pulmonary sequestration (EPS), which was preoperatively undiagnosed, and we removed it. EPS has been shown to be associated with CDH in up to 15 to 40% of cases. A possible explanation hypothesized is that pulmonary sequestration, which develops at 4 to 5 weeks of gestation, can disturb the fusion of the diaphragm and closure of the pleuroperitoneal canal. The thoracoscopic approach permitted us to identify the thoracic EPS that probably would have been otherwise missed.

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The spectrum of congenital malformations of the lung at a rural

Journal of Pediatric and Adolescent Surgery ◽

10.46831/jpas.v1i2.57 ◽

2021 ◽

Vol 1 (2) ◽

Author(s):

Dr. Pooja Bhole ◽

Dr. Vivek Gharpure

Keyword(s):

Congenital Malformations ◽

Pulmonary Sequestration ◽

Rural Hospital ◽

Rural Setting ◽

Open Lung ◽

Congenital Lung Malformation ◽

Number Of Patients ◽

Lobar Emphysema ◽

Lung Resections

ABSTRACT Background: Congenital malformations of lung, such as congenital lobar emphysema, cystic adenomatoid malformation, bronchial cyst, pulmonary sequestration are of rare occurrence. However, our hospital being in a rural area attracts a large number of patients with complex malformations. Method: This retrospective analysis is done to evaluate diagnostic accuracy, safety and efficacy and outcomes of open lung resections at a rural hospital. Results: 16 children with congenital lung malformation underwent open resection in a rural hospital, with no mortality and minimal morbidity, no complications and more than 24 months follow-up. Conclusion: Open lung resections are found to be safe, effective in a rural setting also.

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Distribution, diagnosis, and treatment of pulmonary sequestration: Report of 208 cases

Journal of Pediatric Surgery ◽

10.1016/j.jpedsurg.2018.08.054 ◽

2019 ◽

Vol 54 (7) ◽

pp. 1286-1292 ◽

Cited By ~ 9

Author(s):

Na Zhang ◽

Qi Zeng ◽

Chenghao Chen ◽

Jie Yu ◽

Xu Zhang

Keyword(s):

Pulmonary Sequestration ◽

Diagnosis And Treatment

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Lung Ultrasound: A New Tool in the Management of Congenital Lung Malformation

American Journal of Perinatology ◽

10.1055/s-0039-1692131 ◽

2019 ◽

Vol 36 (S 02) ◽

pp. S99-S105 ◽

Cited By ~ 3

Author(s):

Michele Quercia ◽

Raffaella Panza ◽

Grazia Calderoni ◽

Antonio Di Mauro ◽

Nicola Laforgia

Keyword(s):

Ct Scan ◽

Lung Ultrasound ◽

Case Series ◽

Pulmonary Sequestration ◽

Type I ◽

Congenital Pulmonary Airway Malformation ◽

Congenital Lung Malformation ◽

First Case ◽

Pulmonary Airway

Objective This study was aimed to evaluate effectiveness of lung ultrasound (LUS) in the management of congenital pulmonary airway malformation and pulmonary sequestration in NICUs. Study Design This is a nonconsecutive case series of neonates admitted to the academic NICU of Policlinico of Bari, Italy, from 2010 to 2018, for suspected lung malformations and examined by LUS. Results Seven neonates were admitted for suspected pulmonary malformations, four neonates were diagnosed with pulmonary sequestration and three with congenital pulmonary airway malformation either type I (two cases) or type II (one case) according to Adzick classification. Prenatal scans had described lung malformations in six patients. Two underwent surgical intervention during the 1st month of life. All were successfully discharged home and their follow-up has been uneventful thereafter. In all the seven neonates, LUS easily detected the lesion showing a significantly high correspondence with computed tomography (CT) scan findings. Conclusion We described the first case series of neonates affected by complex pulmonary malformations, assessed by LUS. In our experience, LUS was safe and effective for the diagnosis with high degree of consistency with CT scan findings. We suggest that LUS might be an important diagnostic method for lung malformations in newborns and a useful technique for their follow-up and late management, avoiding multiple exposures to radiations.

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