Cerebrospinal fluid otorrhea and recurrent bacterial meningitis in a pediatric case with Mondini dysplasia

2013 ◽  
Vol 23 (1) ◽  
pp. 57-59 ◽  
Author(s):  
Mete İşeri
Neurosurgery ◽  
1982 ◽  
Vol 11 (3) ◽  
pp. 356-362 ◽  
Author(s):  
Tae Sung Park ◽  
Harold J. Hoffman ◽  
Robin P. Humphreys ◽  
Sylvester H. Chuang

Abstract Unrecognized spontaneous cerebrospinal fluid (CSF) otorrhea led to recurrent bacterial meningitis in three children. The underlying cause of the spontaneous CSF otorrhea was proved to be a congenital cystic dilatation of the cochlear aqueduct and Mondini dysplasia of the temporal bone. The CSF leak recurred in all patients after an initial surgical attempt to close the defects through a tympanotomy. A suboccipital approach was used successfully to obliterate the CSF fistulas in two children; a translabyrinthine approach was used in the other. A search of the literature revealed that Mondini dysplasia is a congenital anomaly that can commonly cause spontaneous CSF otorrhea in children. The authors discuss the management of this uncommon entity on the basis of a literature review and their own experience.


2014 ◽  
Vol 2014 ◽  
pp. 1-3
Author(s):  
Eda Kepenekli-Kadayifci ◽  
Ayşe Karaaslan ◽  
Serkan Atıcı ◽  
Adem Binnetoğlu ◽  
Murat Sarı ◽  
...  

Mondini dysplasia, also known as Mondini malformation, is a developmental abnormality of the inner and middle ears that can cause hearing loss, cerebrospinal fluid (CSF) leakage, and recurrent bacterial meningitis (RBM), which is defined as two or more episodes of meningitis separated by a period of convalescence and the complete resolution of all signs and symptoms. An accurate diagnosis of the underlying pathology is crucial to prevent further episodes from occurring. Herein, we present a three-year-old boy with RBM and unilateral sensorineural hearing loss. During the evaluation to determine the etiology of the RBM, cystic malformation in the cochlea and vestibular dilatation consistent with Mondini dysplasia were detected via computerized tomography (CT) of the temporal bone.


2015 ◽  
Vol 31 (9) ◽  
pp. 1613-1616 ◽  
Author(s):  
R. Nick Hernandez ◽  
Abhinav R. Changa ◽  
Luigi Bassani ◽  
Robert W. Jyung ◽  
James K. Liu

2017 ◽  
Vol 2 ◽  
pp. 16-18
Author(s):  
Mariah E. Small ◽  
Matthew D. Cox ◽  
Adam B. Johnson ◽  
John L. Dornhoffer

1990 ◽  
Vol 16 (4-5) ◽  
pp. 260-264 ◽  
Author(s):  
James T. Wilson ◽  
Sander W. Leivy ◽  
Robert A. Sofferman ◽  
Steven L. Wald

2021 ◽  
Author(s):  
Katsuya Sakai ◽  
Kazutaka Shiomi ◽  
Hitoshi Mochizuki ◽  
Md Nurul Islam ◽  
Hiroki Nabekura ◽  
...  

2016 ◽  
Vol 17 (3) ◽  
pp. 371-377 ◽  
Author(s):  
Jeffrey C. Rastatter ◽  
Patrick C. Walz ◽  
Tord D. Alden

The authors of this report present a pediatric case involving the use of a tunneled temporoparietal fascia flap to reconstruct a skull base defect for a multiply recurrent clival chordoma and cerebrospinal fluid leak, demonstrate the surgical technique through illustrations and intraoperative photos, and review the pertinent literature. A 9-year-old female patient underwent extensive clival chordoma resection via both the endoscopic and open approaches, which ultimately exhausted the bilateral nasoseptal flaps and other intranasal reconstructive options. Following proton beam radiation and initiation of chemotherapy, tumor recurrence was managed with further endoscopic resection, which was complicated by a recalcitrant cerebrospinal fluid leak. A tunneled temporoparietal fascia flap was used to provide vascular tissue to augment an endoscopic repair of the leak and reconstruction of the skull base. While the nasoseptal flap remains the workhorse for many pediatric and adult endoscopic skull base reconstructions, the tunneled temporoparietal fascia flap has a demonstrated efficacy in adults when the nasoseptal flap and other intranasal flaps are unavailable. This report documents a pediatric case, serving as a step toward establishing this technique in the pediatric population.


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