Bilateral Vesicoureteral Reflux in Congenital Nephrotic Syndrome

: Congenital nephrotic syndrome (CNS) is a rare genetic kidney disorder. Different associations between CNS and other organ anomalies have been reported previously. However, urologic abnormalities are not common. This case report can show the association of CNS as a genetic disorder with other abnormalities with a genetic basis. However, the association with urinary abnormalities is rare. We have reported a 25-day-old male newborn, who was referred to our hospital with generalized edema. During the initial evaluation, CNS was diagnosed. The baby, then four months old, was admitted to the hospital with high fever and poor feeding, and a diagnosis of febrile urinary tract infection was made. A voiding cystouretrography was performed that revealed bilateral high-grade vesicoureteral reflux. According to our findings in this case and the genetic basis of CNS and urinary tract anomalies, we recommend the investigation of the urinary tract in CNS patients if indicated.