Duplicated mullerian duct remnants associated with unilateral renal agenesis

1993 ◽  
Vol 18 (2) ◽  
Author(s):  
Vincent McDermott ◽  
JohnD. Orr ◽  
S.Roger Wild
2012 ◽  
Vol 19 (05) ◽  
pp. 723-729
Author(s):  
SARWAT ARA ◽  
TASNEEM ALI

Background: Müllerian duct anomalies (MDAs) occur with an incidence estimated to be 4.3%. A unicornuate uterus with orwithout a rudimentary horn; is a type of mullerian duct abnormality with a frequency of 0.4%. Rudimentary horn pregnancies are rare obstetriccomplication and may cause difficulty in diagnosis and subsequent management. Objective: To alert about Mullerian duct abnormalitiesespecially unicornuate uterus with or without rudimentary horn. Design: Case series. Setting: Study was conducted in the department ofGynecology and obstetrics unit1, Allied Hospital Faisalabad. Duration of study: Cases detected during September 2006-0ctober 2011.Subjects and methods: All admitted cases of MDA whether obstetric or gynecological were included. We calculated cases of unicornuateUterus with or without rudimentary horn, also included cases of rudimentary horn pregnancy with or without rupture. Results: There were120cases of MDA out of which 8 (6.6%) were of unicornuate uterus. Out of 8 unicornuate uteri, 7/8 (87.5%) were with rudimentary horn and1/8(12.5%) without rudimentary horn. Left rudimentary horn in 4/8 patient (50%), right in 3/8 (37.5%) without horn1/8 (12.5%).Out of 7 rudimentaryhorn 1/7 gynecologic and 6/7 were obstetric, 5/7 (71.42%) ruptured in second trimester, and1/7 (14.28%) term pregnancy. In 1/7 (14.28%) hornnot removed because tubal ligation was done. Unilateral renal agenesis was present in 3/8 patient (37.5 %). Ovaries were preserved in 3/7patients (66%). Conclusions: There must be high index of suspicion for Mullerian duct abnormalities especially rudimentary horn for achievinggood success in diagnosis and management.


2021 ◽  
Vol 14 (3) ◽  
pp. e238688
Author(s):  
Manisha Jhirwal ◽  
Pratibha Singh ◽  
Charu Sharma ◽  
Pushpinder Khera

The obstructed haemivagina with ipsilateral renal agenesis (OHVIRA) syndrome also known as Herlyn-Werner-Wunderlich syndrome, a rare congenital malformation in females, results due to developmental abnormality in the müllerian duct. We are reporting a case of a 14-year-old girl who presented with pain and a lump in abdomen for the last 5 months. The MRI abdomen and pelvis confirmed the diagnosis of OHVIRA syndrome. The patient underwent haematocolpos and haematometra drainage, followed by vaginal septum resection.


2010 ◽  
Vol 65 (1) ◽  
pp. 89-93 ◽  
Author(s):  
M. Kopec ◽  
A.B. Rosenkrantz ◽  
R. Rivera ◽  
J.L. Wells ◽  
R.E. Berg ◽  
...  

2021 ◽  
pp. 875647932110126
Author(s):  
Alec Sunyecz ◽  
Megan Snider ◽  
Elizabeth Minniear ◽  
Omar Duenas-Garcia ◽  
Amber Payton ◽  
...  

During fetal development, abnormalities during Mullerian duct formation can lead to varied types of uterine, cervical, or vaginal anomalies. Herlyn-Werner-Wunderlich Syndrome (HWWS) is a rare, congenital Mullerian duct anomaly characterized by the triad of uterine didelphys, obstructed hemi-vagina, and ipsilateral renal agenesis. If the diagnosis is delayed or missed, permanent sequalae such as chronic pain, infection, and infertility can result. This is a case of a 16-year-old woman with heavy vaginal bleeding and menstrual cramping in which sonography was used in the diagnosis of HWWS. Sonography plays a vital role in this diagnosis, as it is the most common initial imaging examination. For this reason, it is important that the characteristics of uterine anomalies, like HWWS, be recognized with sonography. It is important that this diagnosis is made early and treatment can be initiated to prevent irreversible complications.


Sign in / Sign up

Export Citation Format

Share Document