Pseudomembranous enterocolitis and hemorrhagic necrotizing enterocolitis in Hirschsprung's disease

Surgery Today ◽  
1994 ◽  
Vol 24 (3) ◽  
pp. 221-224 ◽  
Author(s):  
Naoto Urushihara ◽  
Sumio Kohno ◽  
Shiro Hasegawa
Keyword(s):  
Necrotizing Enterocolitis ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Pseudomembranous Enterocolitis

Paediatric surgery

2019 ◽  
pp. 725-732
Keyword(s):  
Abdominal Pain ◽  
Medical School ◽  
Surgical Management ◽  
Necrotizing Enterocolitis ◽  
Pyloric Stenosis ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Paediatric Surgery ◽  
Wide Range ◽  
Gastrointestinal Illnesses

This chapter on paediatric surgery covers procedures performed from fetus to 16 years of age. The wide range is succinctly covered with appropriate detail for both those looking to apply for medicine, and those in medical school. The chapter reviews oncological conditions, most importantly, leukaemia. It also studies common conditions such as abdominal pain, hernia, undescended testicles, and appendicitis. Surgical management of gastrointestinal illnesses such as pyloric stenosis, intussusception, and Hirschsprung’s disease is covered along with urological conditions such as hypospadias. It also discusses important neonatal presentations of necrotizing enterocolitis and gastrointestinal atresia, to name a few.

Paediatric surgery

2021 ◽  
pp. 521-552
Keyword(s):  
Abdominal Wall ◽  
Necrotizing Enterocolitis ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Undescended Testis ◽  
Oesophageal Atresia ◽  
Solid Tumours ◽  
Abdominal Wall Defects ◽  
Paediatric Surgery

This chapter outlines the principles of managing paediatric surgical cases. It provides an overview of the assessment of a child with abdominal wall defects, inguinal or scrotal swellings and neck swellings. Conditions such as oesophageal atresia, phyloric stenosis, malrotation and volvulus, intussusception, hirschsprung’s disease, necrotizing enterocolitis, childhood hernias, undescended testis and solid tumours of childhood.

Diagnosis of Hirschsprung's Disease: Accuracy of Barium Enema Findings

1997 ◽  
Vol 36 (4) ◽  
pp. 631
Author(s):  
Sue Yun Yu ◽  
Gye Yeon Lim ◽  
Ji Yeong Yun ◽  
Seong Tae Hahn ◽  
Hak Hee Kim ◽  
...  
Keyword(s):  
Barium Enema ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease

Calretinin Expression in Hirschsprung’s Disease – A Potential Marker of Ganglion Cells

2017 ◽  
Vol 11 (3) ◽  
pp. 181-186
Author(s):  
Mishal Sikandar ◽  
Abdul Hannan Nagi ◽  
Komal Sikandar ◽  
Nadia Naseem ◽  
Ihtisham Qureshi
Keyword(s):  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Ganglion Cells ◽  
Potential Marker

scholarly journals Outcomes in Hirschsprung’s disease with coexisting learning disability

2021 ◽  
Author(s):  
Joseph R. Davidson ◽  
Kristiina Kyrklund ◽  
Simon Eaton ◽  
Mikko P. Pakarinen ◽  
David Thompson ◽  
...  
Keyword(s):  
Quality Of Life ◽  
Learning Disability ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Core Outcome Set ◽  
Functional Results ◽  
Cross Sectional Study ◽  
Cross Sectional ◽  
Related Quality

AbstractThis study describes functional and health-related quality of life (HRQoL) outcomes in patients with Hirschsprung’s disease (HSCR) with associated learning disability or neurodevelopmental delay (LD), completing a core outcome set for HSCR. This was a cross-sectional study from a tertiary pediatric surgery center. Patients treated between 1977 and 2013 were prospectively contacted to complete an outcomes survey. Children under 12 and older patients with LD were assisted to complete these by a proxy. Bowel and urologic function were assessed (Rintala’s BFS and modified DanPSS) along with HRQoL (PedsQL/GIQLI/SF-36). Thirty-two patients with LD were compared to 186 patients with normal cognition. Patients with LD had 76% survival over the follow-up period, compared to 99% in the remainder of the cohort. Poor functional outcomes were common in the patients with LD, considerably higher than cognitively normal patients: with weekly issues withholding stool, soiling and fecal accidents in over half of patients surveyed (44–60%), and urinary incontinence in 46%. Use of permanent stoma was significantly higher (22% vs. 4%; p = 0.001). HRQoL was worse in domains of physical functioning in adults and children but not for social or emotional domains in adults. Subgroup analysis of patients with Down syndrome suggested similar functional results but better QoL. Multivariate analysis demonstrated a dramatically higher incidence of poor continence outcomes in patients with LD (adjusted OR 9.6 [4.0–23]).Conclusions: We provide LD-specific outcomes showing inferior function but similar HRQoL to other patients with HSCR, this is much needed in the counselling of families of these children. What is Known:• Hirschsprung’s disease is commonly associated with syndromes or other anomalies with resultant cognitive impairments.• The outcomes for these patients specifically have been poorly described in the literature. What is New:• Objective functional and quality of life surveys demonstrate significant differences from patients without cognitive impairment.• Patients with learning disability Patients with associated LD were almost ten times more likely to have an associated poor functional outcome, with very little impact on proxy-reported quality of life.

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