Frosted-Branch-Angiitis – seltene Differenzialdiagnose einer retinalen Vaskulitis

Purpose: This work aims to present treatment and long-term follow-up of a 31-year-old woman with dermatomyositis who presented with hemorrhagic retinal vasculitis and macular edema. Methods: A retrospective case report is presented. Results: A 31-year-old woman with dermatomyositis treated with systemic immunosuppression was evaluated for acute, reduced vision. Best-corrected visual acuity was hand motion in the right eye and 20/200 in the left eye. Fundus examination revealed diffuse intraretinal hemorrhages, cotton-wool spots, and vascular sheathing with a frosted branch angiitis–like appearance. Optical coherence tomography revealed significant macular edema and subretinal fluid that quickly resolved after admission and treatment with intravenous steroids. Multimodal imaging at 7-year follow-up disclosed long-term sequelae including peripheral nonperfusion and retinal neovascularization. Conclusions: When vasculitis associated with dermatomyositis is treated aggressively with intravenous steroids at initial presentation, good visual acuity outcomes can be achieved, but long-term consequences of retinal nonperfusion and neovascularization persist.

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Secondary frosted branch angiitis in Neuro-Behçet's disease with serous macular detachment

Pediatrics International ◽

10.1111/j.1442-200x.2011.03343.x ◽

2011 ◽

Vol 53 (2) ◽

pp. 285-286 ◽

Cited By ~ 3

Author(s):

Rohana Ramachandran ◽

Edward Hughes ◽

Genevieve Larkin ◽

Elizabeth Graham ◽

Miles Stanford ◽

...

Keyword(s):

Behçet’S Disease ◽

Behcet’S Disease ◽

Behçet's Disease ◽

Serous Macular Detachment ◽

Behcet's Disease ◽

Macular Detachment ◽

Frosted Branch Angiitis

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POSTSURGICAL BACTERIAL ENDOPHTHALMITIS PRESENTING AS FROSTED BRANCH ANGIITIS: A CASE REPORT

Retinal Cases & Brief Reports ◽

10.1097/icb.0b013e318196b2b6 ◽

2010 ◽

Vol 4 (1) ◽

pp. 20-22 ◽

Cited By ~ 2

Author(s):

Dhanashree Ratra ◽

Shafiq Jafferji ◽

Jyotirmay Biswas

Keyword(s):

Case Report ◽

Bacterial Endophthalmitis ◽

Frosted Branch Angiitis

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Cases of cytomegalovirus retinitis in patients treated for cancer

Malaysian Journal of Ophthalmology ◽

10.35119/myjo.v2i1.96 ◽

2020 ◽

Vol 2 (1) ◽

pp. 69-74

Author(s):

Marium Jamaluddin Ahmad ◽

Tengku Ain Kamalden ◽

Nurliza Khaliddin ◽

Tajunisah Iqbal

Keyword(s):

Cancer Treatment ◽

Opportunistic Infection ◽

Case Series ◽

Cytomegalovirus Retinitis ◽

Immunocompromised Patients ◽

Blurred Vision ◽

Cmv Retinitis ◽

Frosted Branch Angiitis

Cytomegalovirus (CMV) retinitis is an opportunistic infection affecting immunocompromised patients. This case series describes 2 patients aged 19 and 10 years who were undergoing cancer treatment and were referred for complaints of worsening blurred vision. The retinal findings in the first patient showed multiple yellowishsubretinal areas with haemorrhages, while in the second patient there was presence of frosted branch angiitis. Confirmation of diagnosis was done using PCR of vitreous samples and blood CMV levels. Both tested negative for HIV. Both received intravitreal and systemic ganciclovir. It is important for ophthalmologists to consider CMVretinitis in all patients with any form of immunosuppression.

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