Management options of congenital pouch colon—a rare variant of anorectal malformation

Congenital segmental dilatation (CSD) of the intestine is a rare developmental anomaly characterized by sharply demarcated dilatation of a gastrointestinal segment and may present with intestinal obstruction. We report three cases of CSD of the intestine in neonates with varied presentation. First patient was mistaken as pneumoperitoneum on abdominal radiograph, which led to initial abdominal drain placement. The 2nd patient was a case of anorectal malformation associated with congenital pouch colon (CPC) and CSD of ileum; and the third case presented as neonatal intestinal obstruction and found to have CSD of ileum. All the patients were successfully managed in our department.

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Type V Pouch Colon, Prune Belly Syndrome, and Congenital Anterior Urethrocutaneous Fistula

Journal of Neonatal Surgery ◽

10.21699/jns.v6i2.481 ◽

2017 ◽

Vol 6 (2) ◽

pp. 38 ◽

Cited By ~ 1

Author(s):

Prince Raj ◽

Hirendra Birua

Keyword(s):

Anorectal Malformation ◽

Male Child ◽

Prune Belly Syndrome ◽

Urethrocutaneous Fistula ◽

Rare Type ◽

Prune Belly ◽

Short Colon ◽

Congenital Pouch Colon ◽

Pouch Colon ◽

Type V

Congenital pouch colon (CPC) or short colon syndrome is a rare type of anorectal malformation(ARM). Type V is the rarest form of CPC. We present a 1-day-old male child with type V CPC with prune belly syndrome and congenital anterior urethrocutaneous fistula (CAUF).

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Congenital pouch colon associated with anorectal malformation: A rare anomaly of Asian Region – Experience of kurdish centre

African Journal of Paediatric Surgery ◽

10.4103/ajps.ajps_84_16 ◽

2018 ◽

Vol 15 (1) ◽

pp. 10

Author(s):

Rossella Angotti ◽

QadirQadir Mohamed Salih ◽

Francesco Molinaro ◽

Francesco Ferrara ◽

Marina Sica ◽

...

Keyword(s):

Anorectal Malformation ◽

Asian Region ◽

Rare Anomaly ◽

Congenital Pouch Colon ◽

Pouch Colon

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Type V congenital pouch colon: An extremely rare variant of anorectal malformations

Journal of Indian Association of Pediatric Surgeons ◽

10.4103/jiaps.jiaps_233_16 ◽

2017 ◽

Vol 22 (2) ◽

pp. 122 ◽

Cited By ~ 1

Author(s):

Sudhir Singh ◽

JD Rawat ◽

Nitin Pant ◽

Digamber Chaubey

Keyword(s):

Rare Variant ◽

Anorectal Malformations ◽

Congenital Pouch Colon ◽

Pouch Colon ◽

Type V

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Congenital pouch colon with colonic atresia- An unusual embryological association: A case report

Journal of Neonatal Surgery ◽

10.47338/jns.v10.989 ◽

2021 ◽

Vol 10 ◽

pp. 33

Author(s):

Praveen Mathur ◽

Sharanabasappa Gubbi ◽

Aadil Farooq ◽

Priyanka Mittal ◽

Gunjan Sharma

Keyword(s):

Case Report ◽

Anorectal Malformation ◽

English Literature ◽

Abdominal Distension ◽

Case Presentation ◽

Male Baby ◽

Colonic Atresia ◽

Congenital Pouch Colon ◽

Pouch Colon

Background: Congenital pouch colon (CPC) is a rare variant of high anorectal malformation. More and more varied associations of CPC with other entities are being added to the literature. Case presentation: A 1-day-old male baby presented to the emergency room with marked abdominal distension and absent anal opening. On exploration, the baby was found to have CPC (Type 2) with colonic atresia. This association has not been reported in English literature. Conclusion: This is a report of a case of type 2 CPC with colonic atresia. To the best of our knowledge, such an association has not been reported so far. The final embryological outcome is dictated both by the topography and timing of vascular insult.

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