scholarly journals Type V Pouch Colon, Prune Belly Syndrome, and Congenital Anterior Urethrocutaneous Fistula

2017 ◽  
Vol 6 (2) ◽  
pp. 38 ◽  
Author(s):  
Prince Raj ◽  
Hirendra Birua
Keyword(s):  
Anorectal Malformation ◽  
Male Child ◽  
Prune Belly Syndrome ◽  
Urethrocutaneous Fistula ◽  
Rare Type ◽  
Prune Belly ◽  
Short Colon ◽  
Congenital Pouch Colon ◽  
Pouch Colon ◽  
Type V

Congenital pouch colon (CPC) or short colon syndrome is a rare type of anorectal malformation(ARM). Type V is the rarest form of CPC. We present a 1-day-old male child with type V CPC with prune belly syndrome and congenital anterior urethrocutaneous fistula (CAUF).

Congenital pouch colon with prune belly syndrome and megalourethra

2005 ◽  
Vol 21 (6) ◽  
pp. 474-477 ◽  
Author(s):  
A. K. Bangroo ◽  
Shashi Tiwari ◽  
Ramji Khetri ◽  
Mohit Sahni
Keyword(s):  
Prune Belly Syndrome ◽  
Prune Belly ◽  
Congenital Pouch Colon ◽  
Pouch Colon

scholarly journals A case of prenatally diagnosed prune belly syndrome variant and congenital pouch colon in the United States: A case report

2021 ◽  
Vol 10 ◽  
pp. 45
Author(s):  
Mignote Yilma ◽  
Karen Trang ◽  
Marisa Schwab ◽  
Max Bowman ◽  
Mark Sugi ◽  
...  
Keyword(s):  
United States ◽  
Case Report ◽  
The United States ◽  
Prune Belly Syndrome ◽  
Fetal Imaging ◽  
Prune Belly ◽  
Tertiary Center ◽  
Clinical Instability ◽  
Congenital Pouch Colon ◽  
Pouch Colon

Background: Prune belly syndrome (PBS) and congenital pouch colon (CPC) are rare congenital syndromes with a low incidence in the United States (U.S.) with most CPC cases being from India. In this case report, we describe, to the best of our knowledge, the first PBS variant and CPC patient in the U.S. Case Presentation: A 30-year-old G2P0010 woman was referred to a tertiary center after an 18-week ultrasound showed a fetal abdominal mass. A prenatal MRI showed a dilated loop of bowel containing a mixture of urine and meconium, oligohydramnios, and a protuberant abdominal wall. Born at 37 weeks, the child’s physical exam was notable for a distended abdomen with thin abdominal musculature, non-palpable bilateral testes, no anal opening, and flat buttocks. Intra-operatively, a dilated cecum/ascending colon was noted with an abrupt change in caliber at the transverse colon, bilateral enlarged ureters, a left testis at the internal ring and no visualized right testis. A colostomy and mucous fistula were created 5 cm from the sigmoid pouch. Conclusion: While most reported cases of CPC undergo single stage repair (one operation) at 1 day of life, our patient underwent the first procedure of a staged repair at 16 hours of life given his clinical instability at the time as well as his unknown urological anatomy in the setting of urinary obstruction. This case demonstrates the importance of fetal imaging, multidisciplinary approach at a tertiary care center, and reinforces a staged repair when necessary.

scholarly journals Prune belly syndrome with congenital pouch colon

2013 ◽  
Vol 18 (2) ◽  
pp. 79
Author(s):  
VenkateshM Annigeri ◽  
RashmiV Annigeri ◽  
ManjunathT Bhat ◽  
HariharV Hegde ◽  
AnilB Halgeri
Keyword(s):  
Prune Belly Syndrome ◽  
Prune Belly ◽  
Congenital Pouch Colon ◽  
Pouch Colon

scholarly journals Varied Presentation of Congenital Segmental Dilatation of the Intestine in Neonates: Report of Three Cases

2016 ◽  
Vol 5 (4) ◽  
pp. 55 ◽  
Author(s):  
Binod Kumar Rai ◽  
Bilal Mirza ◽  
Imran Hashim ◽  
Muhammad Saleem
Keyword(s):  
Intestinal Obstruction ◽  
Anorectal Malformation ◽  
Developmental Anomaly ◽  
Abdominal Radiograph ◽  
Abdominal Drain ◽  
The Third ◽  
Neonatal Intestinal Obstruction ◽  
Segmental Dilatation ◽  
Congenital Pouch Colon ◽  
Pouch Colon

Congenital segmental dilatation (CSD) of the intestine is a rare developmental anomaly characterized by sharply demarcated dilatation of a gastrointestinal segment and may present with intestinal obstruction. We report three cases of CSD of the intestine in neonates with varied presentation. First patient was mistaken as pneumoperitoneum on abdominal radiograph, which led to initial abdominal drain placement. The 2nd patient was a case of anorectal malformation associated with congenital pouch colon (CPC) and CSD of ileum; and the third case presented as neonatal intestinal obstruction and found to have CSD of ileum. All the patients were successfully managed in our department.

scholarly journals Rare association of prune belly syndrome with pouch colon

2011 ◽  
pp. 9 ◽  
Author(s):  
Munisami Ragavan ◽  
Haripriya ◽  
Sarvavinothini
Keyword(s):  
Prune Belly Syndrome ◽  
Rare Association ◽  
Prune Belly ◽  
Pouch Colon

scholarly journals Congenital pouch colon associated with anorectal malformation: A rare anomaly of Asian Region – Experience of kurdish centre

2018 ◽  
Vol 15 (1) ◽  
pp. 10
Author(s):  
Rossella Angotti ◽  
QadirQadir Mohamed Salih ◽  
Francesco Molinaro ◽  
Francesco Ferrara ◽  
Marina Sica ◽  
...  
Keyword(s):  
Anorectal Malformation ◽  
Asian Region ◽  
Rare Anomaly ◽  
Congenital Pouch Colon ◽  
Pouch Colon

scholarly journals Type V congenital pouch colon: An extremely rare variant of anorectal malformations

2017 ◽  
Vol 22 (2) ◽  
pp. 122 ◽  
Author(s):  
Sudhir Singh ◽  
JD Rawat ◽  
Nitin Pant ◽  
Digamber Chaubey
Keyword(s):  
Rare Variant ◽  
Anorectal Malformations ◽  
Congenital Pouch Colon ◽  
Pouch Colon ◽  
Type V

scholarly journals Congenital pouch colon with colonic atresia- An unusual embryological association: A case report

2021 ◽  
Vol 10 ◽  
pp. 33
Author(s):  
Praveen Mathur ◽  
Sharanabasappa Gubbi ◽  
Aadil Farooq ◽  
Priyanka Mittal ◽  
Gunjan Sharma
Keyword(s):  
Case Report ◽  
Anorectal Malformation ◽  
English Literature ◽  
Abdominal Distension ◽  
Case Presentation ◽  
Male Baby ◽  
Colonic Atresia ◽  
Congenital Pouch Colon ◽  
Pouch Colon

Background: Congenital pouch colon (CPC) is a rare variant of high anorectal malformation. More and more varied associations of CPC with other entities are being added to the literature. Case presentation: A 1-day-old male baby presented to the emergency room with marked abdominal distension and absent anal opening. On exploration, the baby was found to have CPC (Type 2) with colonic atresia. This association has not been reported in English literature. Conclusion: This is a report of a case of type 2 CPC with colonic atresia. To the best of our knowledge, such an association has not been reported so far. The final embryological outcome is dictated both by the topography and timing of vascular insult.

scholarly journals Congenital pouch colon: A rare presentation of Anorectal malformation

2015 ◽  
Vol 57 (3) ◽  
pp. 193-197 ◽  
Author(s):  
Salah S. Mahmood ◽  
◽  
Ahmed Z. Zain ◽  
Raghad J. Aboalhab ◽  
◽  
...  
Keyword(s):  
Anorectal Malformation ◽  
Rare Presentation ◽  
Congenital Pouch Colon ◽  
Pouch Colon
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