Cardiac hydatidosis is a rare presentation of echinococcus granulosus infestation. We report the case of 57-year-old man who presented with syncope due to ventricular tachycardia and was managed with antiarrhythmic drugs for an acute episode. Echocardiography and cardiac magnetic resonance imaging suggested a 1 cm right ventricular hydatid cyst. In view of the control of arrhythmia on antiarrhythmic drugs and the small size of the cyst, the patient was treated with albendazole 400 mg twice a day for 4 weeks. He was asymptomatic with normal liver function during follow-up, and repeat echocardiography after 1 year revealed disappearance of the intramyocardial lesion.