Anomalous right coronary artery from the pulmonary artery presenting with angina and aneurysmal left ventricular dilatation

1989 ◽  
Vol 118 (1) ◽  
pp. 182-184 ◽  
Author(s):  
Hooman Mahdyoon ◽  
James F. Brymer ◽  
Mohsin Alam ◽  
Fareed Khaja
Author(s):  
Matthew C Schwartz ◽  
◽  
William Hammill ◽  
Thomas S Maxey ◽  
◽  
...  

Echocardiogram (Figure 1A-B) in an asymptomatic 6 month-old raised suspicion for anomalous Right Coronary Artery (RCA) from the Pulmonary Artery (ARCAPA) with retrograde flow from the RCA to the main pulmonary artery. The patient’s left ventricular systolic function was normal. Subsequent cardiac catheterization confirmed the diagnosis as angiography showed that the RCA arose from the anterior aspect of the main pulmonary artery and filled retrograde via a collateral network from the Left Coronary Artery (LCA) system (Figure 1C-D). At 10 months of age, the patient underwent surgical translocation of the RCA to the aorta. On direct visualization, the RCA arose from the anterior wall of the main pulmonary artery and the robust collateral supply of the RCA from the LCA was visualized on the heart’s epicardium (Figure 2). The patient did well and was discharged home several days later. Three months after the operation, the patient continues to do well with normal left ventricular systolic flow and prograde flow into the reimplanted RCA.


2013 ◽  
Vol 16 (4) ◽  
pp. 210 ◽  
Author(s):  
Sachin Talwar ◽  
Aandrei Jivendra Jha ◽  
Shiv Kumar Choudhary ◽  
Saurabh Kumar Gupta ◽  
Balram Airan

Between January 2002 and December 2012, five patients (4 female) underwent corrective surgery for anomalous left coronary artery from pulmonary artery (ALCAPA). They were older than 1 year (range, 3-56 years). One of the 2 patients younger than 10 years had presented with congestive heart failure, and the other had experienced repeated episodes of lower respiratory tract infection since childhood. Of the remaining 3 adult patients, 2 had experienced angina with effort, and 1 patient had had repeated respiratory tract infections since childhood, with mild dyspnea on effort of New York Heart Association (NYHA) class II. Three patients had the anomalous left coronary artery implanted directly into the ascending aorta via coronary-button transfer, and 2 patients underwent coronary artery bypass with obliteration of the left main ostium. Two patients underwent concomitant mitral valve repair procedures, and 1 patient underwent direct closure of a perimembranous ventricular septal defect. Four patients survived the surgery, and 1 patient died because of a persistently low cardiac output. Follow-up times ranged from 3 months to 4 years. All survivors are in NYHA class I and have left ventricular ejection fractions of 45% to 60%, with moderate (n = 1), mild (n = 1), or no (n = 2) mitral insufficiency. We conclude that a few naturally selected patients with ALCAPA do survive beyond infancy and can undergo establishment of 2 coronary systems with satisfactory results.


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