Rare and life-threatening cardiovascular complication of chronic thromboembolic pulmonary hypertension diagnosed by trans-thoracic echocardiography

2016 ◽  
Vol 203 ◽  
pp. 450-452 ◽  
Author(s):  
Caroline Birgy ◽  
Didier Bresson ◽  
Elena Duculescu ◽  
Maxime Carpentier ◽  
Francois Philit ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Chronic Thromboembolic Pulmonary Hypertension ◽  
Cardiovascular Complication ◽  
Thromboembolic Pulmonary Hypertension ◽  
Life Threatening

scholarly journals Novel Insight into How Nurses Working at PH Specialist Clinics in Sweden Perceive Their Work

Healthcare ◽  
2020 ◽  
Vol 8 (2) ◽  
pp. 180
Author(s):  
Bodil Ivarsson ◽  
Barbro Kjellström
Keyword(s):  
Pulmonary Hypertension ◽  
Personal Development ◽  
Qualitative Content Analysis ◽  
Chronic Thromboembolic Pulmonary Hypertension ◽  
Life Threatening Illness ◽  
Good Patient Care ◽  
Information And Communication ◽  
Thromboembolic Pulmonary Hypertension ◽  
Life Threatening ◽  
Specialist Knowledge

Outpatient pulmonary hypertension (PH) specialist centers have an important role in the optimal management of pulmonary arterial hypertension (PAH) and chronic thromboembolic pulmonary hypertension (CTEPH). The aim of the present study was to gain an understanding of the work facing nurses at the outpatient PH specialist centers in Sweden. All nurses (n = 14) working at the outpatient PH specialist centers in Sweden were included. Qualitative content analysis was employed to analyze the interviews, wherein an overarching theme emerged: “Build and maintain a relationship with the patient”. Three categories described the nurses’ experiences: “Ambiguous satisfaction regarding information and communication”, “Acting as a coordinator” and “Professional and personal development”. To provide good patient care, the nurses described the key components as the ability to give information on all aspects of the disease and their availability by phone for patients, their relatives, and other healthcare resources. This requires evidence-based, specialist knowledge about the disease, its care, and treatments as well as experience. In conclusion, working as a nurse at the outpatient PH specialist centers highlight the advantages, expectations, and difficulties in working with patients with a rare and life-threatening illness. The overall knowledge and skills were high, but the nurses expressed a need for in-depth and continued training.

scholarly journals Organization of pharmacological support of patients with rare diseases in moscow as exemplified by pulmonary arterial hypertension

2018 ◽  
pp. 24-31
Author(s):  
M. V. Zhuravleva ◽  
A. Yu. Lebedeva
Keyword(s):  
Pulmonary Hypertension ◽  
Rare Diseases ◽  
Chronic Thromboembolic Pulmonary Hypertension ◽  
Legal Environment ◽  
Orphan Diseases ◽  
Thromboembolic Pulmonary Hypertension ◽  
Life Threatening ◽  
Pulmonary Arterial ◽  
Vulnerable Population Groups

Orphan diseases are life-threatening, chronic, progressive and leading to a reduction in life expectancy or disability conditions. Patients with rare diseases are one of the vulnerable population groups, which is caused by several factors, such as insufficient awareness of practitioners about such diseases, complicated and lengthy diagnosis, and imperfection of legal environment in the area of pharmacological support of orphan diseases, when only 24 orphan diseases (List-24) are determined, which are treated at the expense of the RF subjects.Imperfection of federal orphan diseases legislation is shown on the example of providing patients with PAH-specific therapy: only idiopathic form of pulmonary hypertension is included in the federal List-24, there is no well-established mechanism of pharmacological support for patients with chronic thromboembolic pulmonary hypertension (CTEPH) that is not included in the List-24. The article describes the successful experience in providing patients with orphan diseases, regardless of the inclusion of nosology in List-24 in Moscow, through the creation and implementation of the transparent medical and pharmacological support regulation for patients with orthopaedic diseases, which settled the timely process of provision of patients with the necessary therapy. As a result, patients with CTEPH also have access to existing pathogenetic treatment that can prolong life and improve the quality of life of such patients. 

scholarly journals Fear of COVID-19, Anxiety and Depression in Patients with Pulmonary Arterial Hypertension and Chronic Thromboembolic Pulmonary Hypertension during the Pandemic

2021 ◽  
Vol 10 (18) ◽  
pp. 4195
Author(s):  
Maria Wieteska-Miłek ◽  
Sebastian Szmit ◽  
Michał Florczyk ◽  
Beata Kuśmierczyk-Droszcz ◽  
Robert Ryczek ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Chronic Thromboembolic Pulmonary Hypertension ◽  
Physical And Mental Health ◽  
Increased Risk ◽  
Thromboembolic Pulmonary Hypertension ◽  
Life Threatening ◽  
History Of ◽  
Pulmonary Arterial ◽  
Multicenter Prospective Study ◽  
Age Range

The COVID-19 pandemic has affected the physical and mental health of people around the world. This may be particularly true for patients with life-threatening diseases. We analyzed the level of fear of COVID-19 (FCV-19S), the prevalence of anxiety (HADS-A) and depression (HADS-D) in pulmonary arterial and chronic thromboembolic pulmonary hypertension (PAH and CTEPH) patients during the COVID-19 pandemic. In this multicenter prospective study, 223 patients (63% females, 66% PAH) with age range 18–90 years were included. The fear of COVID-19 was high, at a mean level of 18.9 ± 7.4 points. Anxiety (HADS-A ≥ 8 points) was diagnosed in 32% of all patients, depression (HADS-D ≥ 8 points) in 21%, and anxiety or depression in 38%. FCV-19S was higher in woman and in elderly people (p = 0.02; p = 0.02, respectively). In the multivariate analysis, FCV-19S higher than the median increased the odds ratio of anxiety, but not of depression (R 6.4 (95%CI 2.0–20.0), p = 0.002; OR 1.9 (0.9–3.9), p = 0.06, respectively). History of COVID-19 increased risk of both HADS-A and HADS-D. Patients with PAH and CTEPH, especially woman over 65 years and those who had been infected with COVID-19, may need additional psychological support due to fear of COVID-19, anxiety or depression.

scholarly journals Chronic thromboembolic pulmonary hypertension following long-term peripherally inserted central venous catheter use

2019 ◽  
Vol 9 (2) ◽  
pp. 204589401985947
Author(s):  
Abigail Masding ◽  
Stephen D. Preston ◽  
Mark Toshner ◽  
Joseph Barnett ◽  
Carl Harries ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Chronic Thromboembolic Pulmonary Hypertension ◽  
Venous Catheter ◽  
Type I ◽  
First Case ◽  
Thromboembolic Pulmonary Hypertension ◽  
Mobile Mass ◽  
Life Threatening ◽  
The Right

A 36-year-old woman presented with recurrent pulmonary emboli (PE) despite oral anticoagulation. She was a type I diabetic with severe gastroparesis requiring insertion of multiple long-term peripherally inserted central catheters (PICC) over a 10-year period. Imaging at presentation demonstrated a PICC-associated mobile mass in the right atrium and signs of pulmonary hypertension (PH). She was thrombolyzed and fully anticoagulated, and diabetic management without PICC strongly recommended. PH persisted, however, and she developed chronic thromboembolic pulmonary hypertension (CTEPH), for which successful pulmonary endarterectomy (PEA) surgery led to symptomatic and hemodynamic improvement. This was the first case of CTEPH reported related to long-term PICC use outside the setting of malignant disease, and a novel observation that the PEA specimen contained multiple plastic fragments. Long-term PICC placement increases the risk of CTEPH, a life-threatening, albeit treatable, complication.

IP-10 and IL-6 as biomarkers in Chronic Thromboembolic Pulmonary Hypertension

Pneumologie ◽  
2013 ◽  
Vol 67 (05) ◽  
Author(s):  
D Zabini ◽  
Z Bálint ◽  
C Nagarai ◽  
V Foris ◽  
G Kwapiszewska ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Chronic Thromboembolic Pulmonary Hypertension ◽  
Thromboembolic Pulmonary Hypertension
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