Cor triatriatum sinister with an intact interatrial septum and a decompressing vein in a toddler

AbstractCor triatriatum sinister is a very rare cardiac anomaly that may lead to pulmonary hypertension, right ventricular dilation, and eventually right heart failure. We report a case of a toddler who presented with respiratory distress and cardiomegaly and was found to have cor triatriatum sinister with a restrictive communication, decompressing vertical vein, pulmonary hypertension, severe tricuspid regurgitation, and severe right ventricular dysfunction. She underwent a successful surgical repair, with normalisation of right ventricular function and pulmonary artery pressure.

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Severe right heart failure and pulmonary hypertension because of cor triatriatum sinister in a 54year-old patient

International Journal of Cardiology ◽

10.1016/j.ijcard.2010.04.071 ◽

2011 ◽

Vol 151 (1) ◽

pp. e29-e31 ◽

Cited By ~ 1

Author(s):

Erkan İlhan ◽

Mehmet Ergelen ◽

Özer Soylu ◽

Rodi Tosu ◽

Tolga Sinan Güvenç ◽

...

Keyword(s):

Heart Failure ◽

Pulmonary Hypertension ◽

Right Heart Failure ◽

Cor Triatriatum ◽

Right Heart ◽

Cor Triatriatum Sinister

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Right ventricular dysfunction and pulmonary hypertension: a neglected presentation of thyrotoxicosis

Endocrinology Diabetes and Metabolism Case Reports ◽

10.1530/edm-18-0012 ◽

2018 ◽

Vol 2018 ◽

Cited By ~ 2

Author(s):

Carolina Shalini Singarayar ◽

Foo Siew Hui ◽

Nicholas Cheong ◽

Goay Swee En

Keyword(s):

Heart Failure ◽

Pulmonary Hypertension ◽

Right Ventricular ◽

Left Ventricular Dysfunction ◽

Ventricular Dysfunction ◽

Right Ventricular Dysfunction ◽

Right Heart Failure ◽

Left Ventricular ◽

Newly Diagnosed ◽

Right Heart

Summary Thyrotoxicosis is associated with cardiac dysfunction; more commonly, left ventricular dysfunction. However, in recent years, there have been more cases reported on right ventricular dysfunction, often associated with pulmonary hypertension in patients with thyrotoxicosis. Three cases of thyrotoxicosis associated with right ventricular dysfunction were presented. A total of 25 other cases of thyrotoxicosis associated with right ventricular dysfunction published from 1994 to 2017 were reviewed along with the present 3 cases. The mean age was 45 years. Most (82%) of the cases were newly diagnosed thyrotoxicosis. There was a preponderance of female gender (71%) and Graves’ disease (86%) as the underlying aetiology. Common presenting features included dyspnoea, fatigue and ankle oedema. Atrial fibrillation was reported in 50% of the cases. The echocardiography for almost all cases revealed dilated right atrial and or ventricular chambers with elevated pulmonary artery pressure. The abnormal echocardiographic parameters were resolved in most cases after rendering the patients euthyroid. Right ventricular dysfunction and pulmonary hypertension are not well-recognized complications of thyrotoxicosis. They are life-threatening conditions that can be reversed with early recognition and treatment of thyrotoxicosis. Signs and symptoms of right ventricular dysfunction should be sought in all patients with newly diagnosed thyrotoxicosis, and prompt restoration of euthyroidism is warranted in affected patients before the development of overt right heart failure. Learning points: Thyrotoxicosis is associated with right ventricular dysfunction and pulmonary hypertension apart from left ventricular dysfunction described in typical thyrotoxic cardiomyopathy. Symptoms and signs of right ventricular dysfunction and pulmonary hypertension should be sought in all patients with newly diagnosed thyrotoxicosis. Thyrotoxicosis should be considered in all cases of right ventricular dysfunction or pulmonary hypertension not readily explained by other causes. Prompt restoration of euthyroidism is warranted in patients with thyrotoxicosis complicated by right ventricular dysfunction with or without pulmonary hypertension to allow timely resolution of the abnormal cardiac parameters before development of overt right heart failure.

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A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation

Case Reports in Pediatrics ◽

10.1155/2020/8825215 ◽

2020 ◽

Vol 2020 ◽

pp. 1-3

Author(s):

Can Yilmaz Yozgat ◽

Erkan Cakir ◽

Hakan Yazan ◽

Hafize Otcu Temur ◽

Kahraman Yakut ◽

...

Keyword(s):

Pulmonary Hypertension ◽

Arteriovenous Malformation ◽

Pulmonary Arteries ◽

Venous Hypertension ◽

Pulmonary Arteriovenous Malformation ◽

Cor Triatriatum ◽

Cardiac Anomaly ◽

Congenital Cardiac Anomaly ◽

Cor Triatriatum Sinister ◽

Arteries And Veins

Cor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malformation (PAVM) is notorious for its aberrant blood flow between the pulmonary arteries and veins. Herein, we report a case of a 4-year-old toddler who had a unique form of pulmonary hypertension presenting with cor triatriatum sinister and diffuse PAVM. After the surgical treatment of cor triatriatum sinister, both pulmonary arteriovenous malformation and pulmonary hypertension disappeared.

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EXPRESS: Association of Right Ventricular Dysfunction and Pulmonary Hypertension with Adverse 30-Day Outcomes in COVID-19 Patients

Pulmonary Circulation ◽

10.1177/20458940211007040 ◽

2021 ◽

pp. 204589402110070

Author(s):

Karan Wats ◽

Daniel Rodriguez ◽

Kurt Prins ◽

Adnan Sadiq ◽

Joshua Fogel ◽

...

Keyword(s):

Pulmonary Hypertension ◽

Right Ventricular ◽

Clinical Utility ◽

Ventricular Dysfunction ◽

Systolic Dysfunction ◽

Right Ventricular Dysfunction ◽

Inpatient Mortality ◽

Ventricular Systolic Dysfunction ◽

Ventilator Support ◽

Severe Tricuspid Regurgitation

Background: Cardiac manifestations in COVID-19 are multifactorial and are associated with increased mortality. The clinical utility and prognostic value of echocardiography in COVID-19 inpatients is not clearly defined. We aim to identify echocardiographic parameters that are associated with 30-day clinical outcomes secondary to COVID-19 hospitalization. Methods: This retrospective cohort study was conducted in a large tertiary hospital in New York City during the COVID-19 pandemic. It included 214 adult inpatients with a laboratory confirmed diagnosis of COVID-19 by reverse transcriptase polymerase chain reaction assay (RT-PCR) for SARS-CoV-2 on nasopharyngeal swab and had a transthoracic echocardiogram performed during the index hospitalization. Primary outcome was 30-day all-cause inpatient mortality. Secondary outcomes were 30-day utilization of mechanical ventilator support, vasopressors, or renal replacement therapy. Results: Mild right ventricular systolic dysfunction [OR:3.51, 95% CI:1.63â7.57, p=0.001], moderate to severe right ventricular systolic dysfunction [OR:7.30, 95% CI:2.20â24.25, p=0.001], pulmonary hypertension [OR:5.39, 95% CI:1.96â14.86, p=0.001], and moderate to severe tricuspid regurgitation [OR:3.92, 95% CI:1.71â9.03, p=0.001] were each associated with increased odds of 30-day all-cause inpatient mortality. Pulmonary hypertension and moderate to severe right ventricular dysfunction were each associated with increased odds of 30-day utilization of mechanical ventilator support and vasopressors. Conclusions: Right ventricular dysfunction, pulmonary hypertension, and moderate to severe tricuspid regurgitation were associated with increased odds for 30-day inpatient mortality. This study highlights the importance of echocardiography and its clinical utility and prognostic value for evaluating hospitalized COVID-19 patients.

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Cor triatriatum with a left upper anomalous pulmonary venous return to the innominate vein

Cardiology in the Young ◽

10.1017/s1047951113000838 ◽

2013 ◽

Vol 24 (3) ◽

pp. 546-548 ◽

Cited By ~ 1

Author(s):

Claire Galoin-Bertail ◽

Marielle Gouton

Keyword(s):

Pulmonary Hypertension ◽

Atrial Septal Defect ◽

Septal Defect ◽

Venous Return ◽

Innominate Vein ◽

Cor Triatriatum ◽

Cardiac Anomaly ◽

Congenital Cardiac Anomaly ◽

Cor Triatriatum Sinister ◽

Anomalous Pulmonary Venous Return

AbstractCor triatriatum sinister is an uncommon congenital cardiac anomaly accounting for 0.1% of all congenital cardiac malformations, with an anomalous venous return being a frequently associated condition. We present the case of a 14-year-old girl misdiagnosed as having an atrial septal defect with pulmonary hypertension who actually had a cor triatriatum with a left upper anomalous pulmonary venous return to the innominate vein.

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