Characterization of the Adenosinetriphosphatase and Transport Activities of Purified Cystic Fibrosis Transmembrane Conductance Regulator†

Characterization of Defects in Ion Transport and Tissue Development in Cystic Fibrosis Transmembrane Conductance Regulator (CFTR)-Knockout Rats

PLoS ONE ◽

10.1371/journal.pone.0091253 ◽

2014 ◽

Vol 9 (3) ◽

pp. e91253 ◽

Cited By ~ 87

Author(s):

Katherine L. Tuggle ◽

Susan E. Birket ◽

Xiaoxia Cui ◽

Jeong Hong ◽

Joe Warren ◽

...

Keyword(s):

Cystic Fibrosis ◽

Ion Transport ◽

Tissue Development ◽

Characterization of Small Molecule Modulators of the Cystic Fibrosis Transmembrane Conductance Regulator using Backscattering Interferometry

Biophysical Journal ◽

10.1016/j.bpj.2014.11.3193 ◽

2015 ◽

Vol 108 (2) ◽

pp. 585a

Author(s):

Ashley Lockwood ◽

David Heidary ◽

Christopher Richards ◽

Michael Baksh ◽

M.G. Finn

Keyword(s):

Cystic Fibrosis ◽

Small Molecule ◽

Backscattering Interferometry ◽

Small Molecule Modulators ◽

Characterization of disease-associated mutations affecting an exonic splicing enhancer and two cryptic splice sites in exon 13 of the cystic fibrosis transmembrane conductance regulator gene

Human Molecular Genetics ◽

10.1093/hmg/ddg215 ◽

2003 ◽

Vol 12 (16) ◽

pp. 2031-2040 ◽

Cited By ~ 39

Author(s):

I. Aznarez

Keyword(s):

Cystic Fibrosis ◽

Regulator Gene ◽

Splice Sites ◽

Exonic Splicing Enhancer ◽

Cryptic Splice Sites ◽

Cystic Fibrosis Transmembrane ◽

Splicing Enhancer

Expression and characterization of the cystic fibrosis transmembrane conductance regulator

Nature ◽

10.1038/347382a0 ◽

1990 ◽

Vol 347 (6291) ◽

pp. 382-386 ◽

Cited By ~ 222

Author(s):

Richard J. Gregory ◽

Seng H. Cheng ◽

Devra P. Rich ◽

John Marshall ◽

Sucharita Paul ◽

...

Keyword(s):

Cystic Fibrosis ◽

Functional Characterization of a Recombinant Adeno- Associated Virus 5-Pseudotyped Cystic Fibrosis Transmembrane Conductance Regulator Vector

Human Gene Therapy ◽

10.1089/hum.2004.15.832 ◽

2004 ◽

Vol 15 (9) ◽

pp. 832-841 ◽

Cited By ~ 9

Author(s):

Jeffrey Sirninger ◽

Christian Muller ◽

Sofia Braag ◽

Qiushi Tang ◽

Hungwen Yue ◽

...

Keyword(s):

Cystic Fibrosis ◽

Functional Characterization ◽

Adeno Associated Virus ◽

Characterization of the cAMP Response Element of the Cystic Fibrosis Transmembrane Conductance Regulator Gene Promoter

Journal of Biological Chemistry ◽

10.1074/jbc.271.50.31869 ◽

1996 ◽

Vol 271 (50) ◽

pp. 31869-31877 ◽

Cited By ~ 61

Author(s):

Randolph P. Matthews ◽

G. Stanley McKnight

Keyword(s):

Cystic Fibrosis ◽

Gene Promoter ◽

Regulator Gene ◽

Camp Response Element ◽

Response Element ◽

The cystic fibrosis transmembrane conductance regulator. Overexpression, purification, and characterization of wild type and delta F508 mutant forms of the first nucleotide binding fold in fusion with the maltose-binding protein.

Journal of Biological Chemistry ◽

10.1016/s0021-9258(20)80530-4 ◽

1993 ◽

Vol 268 (32) ◽

pp. 24330-24338

Author(s):

Y.H. Ko ◽

P.J. Thomas ◽

M.R. Delannoy ◽

P.L. Pedersen

Keyword(s):

Cystic Fibrosis ◽

Nucleotide Binding ◽

Maltose Binding Protein ◽

Wild Type ◽

Purification And Characterization ◽

Mutant Forms ◽

641: Characterization of the cystic fibrosis transmembrane conductance regulator–associated lncRNAs in the innate immune response in cystic fibrosis

Journal of Cystic Fibrosis ◽

10.1016/s1569-1993(21)02064-6 ◽

2021 ◽

Vol 20 ◽

pp. S304-S305

Author(s):

H. Levy ◽

J. Domenico ◽

X. Zhang ◽

C. Moore ◽

J. Knapp ◽

...

Keyword(s):

Cystic Fibrosis ◽

Immune Response ◽

Innate Immune Response ◽

Innate Immune ◽

Characterization of the oligosaccharide structures associated with the cystic fibrosis transmembrane conductance regulator

Glycobiology ◽

10.1093/glycob/10.11.1225 ◽

2000 ◽

Vol 10 (11) ◽

pp. 1225-1233 ◽

Cited By ~ 17

Author(s):

C. R. O'Riordan ◽

A. L. Lachapelle ◽

J. Marshall ◽

E. A. Higgins ◽

S. H. Cheng

Keyword(s):

Cystic Fibrosis ◽

Cystic Fibrosis Transmembrane ◽

Oligosaccharide Structures

Molecular and functional characterization of the cystic fibrosis transmembrane conductance regulator from the Australian common brushtail possum, Trichosurus vulpecula

Journal of Comparative Physiology B ◽

10.1007/s00360-009-0433-6 ◽

2009 ◽

Vol 180 (4) ◽

pp. 545-561 ◽

Cited By ~ 2

Author(s):

K. J. Demmers ◽

D. Carter ◽

S. Fan ◽

P. Mao ◽

N. J. Maqbool ◽

...

Keyword(s):

Cystic Fibrosis ◽

Functional Characterization ◽

Brushtail Possum ◽

Trichosurus Vulpecula ◽

Common Brushtail Possum ◽