Robotic Adrenalectomy for Pheochromocytoma in a Patient with Fontan Physiology

2020 ◽  
Vol 34 (9) ◽  
pp. 2446-2451
Author(s):  
Jared J. Cummings ◽  
Kara K. Siegrist ◽  
Robert J. Deegan ◽  
Carmen C. Solórzano ◽  
Susan S. Eagle
Keyword(s):  
Robotic Adrenalectomy ◽  
Fontan Physiology

The Perioperative Management of a Patient With Fontan Physiology for Pheochromocytoma Resection

2008 ◽  
Vol 22 (5) ◽  
pp. 748-750 ◽  
Author(s):  
Koichi Yuki ◽  
Robert C. Shamberger ◽  
Francis X. McGowan ◽  
Christian Seefelder
Keyword(s):  
Perioperative Management ◽  
Fontan Physiology

Exercise Performance in Adolescents with Fontan Physiology (From the Pediatric Heart Network Fontan Public Data Set)

2021 ◽  
Author(s):  
Michael D. Seckeler ◽  
Brent J. Barber ◽  
Jamie N. Colombo ◽  
Alyssa M. Bernardi ◽  
Andrew W. Hoyer ◽  
...  
Keyword(s):  
Exercise Performance ◽  
Data Set ◽  
Public Data ◽  
Fontan Physiology

Intravascular Mechanical Cavopulmonary Assistance for Patients With Failing Fontan Physiology

2009 ◽  
Vol 33 (11) ◽  
pp. 977-987 ◽  
Author(s):  
Sonya S. Bhavsar ◽  
Jugal Y. Kapadia ◽  
Steven G. Chopski ◽  
Amy L. Throckmorton
Keyword(s):  
Fontan Physiology ◽  
Failing Fontan

Rebuttal

2004 ◽  
Vol 14 (S1) ◽  
pp. 114-114 ◽  
Author(s):  
Leonard L. Bailey
Keyword(s):  
Coronary Disease ◽  
Reconstructive Surgery ◽  
Fontan Circulation ◽  
Actuarial Survival ◽  
Term Survival ◽  
Long Term Survival ◽  
Fontan Physiology ◽  
Failing Fontan

The portrayal of a beautiful youngster performing uninhibited acrobatics based on Fontan physiology, as presented by Marshall Jacobs, is a brilliant and beautiful thing for us to see. It is, perhaps, all about will over physiology. But it is, nevertheless, happening for that child. Marshall mentioned the need for re-transplantation, whether the beginning strategy was transplantation or reconstructive surgery. Indeed, a relatively small percentage of children transplanted will require re-transplantation because of severe graft coronary disease. Remarkably, in the Loma Linda experience, 10-year actuarial survival for 26 patients following elective re-transplantation is over 85%, exceeding overall actuarial survival at 10 years for children following primary transplantation. Many of the transplanted infants, however, seem to be realistically hopeful that one heart will last their entire lifetime. Of course, the hope is that their's will be a long and healthy lifetime. The requirement for late transplantation following Fontan procedures, however, seems almost inevitable. We'll simply have to keep these children with Fontan circulation under surveillance to see when, in the course of their lives, transplantation will become necessary. Unfortunately, operative and long-term survival among children who are transplanted for failing Fontan physiology have, as yet, been somewhat suboptimal.

Case Report: Pediatric Robotic Adrenalectomy for Virilizing Adrenal Tumor in a 4-year-old Female

Urology ◽  
2021 ◽  
Author(s):  
Thomas Lowrey ◽  
David Cochran ◽  
Dominic Frimberger ◽  
Bhalaajee Meenakshi Sundaram ◽  
Shelly Mercer ◽  
...  
Keyword(s):  
Case Report ◽  
Adrenal Tumor ◽  
Robotic Adrenalectomy

Abstract 14773: Biventricular Conversion After Fontan Completion: A Preliminary Experience

Circulation ◽  
2020 ◽  
Vol 142 (Suppl_3) ◽  
Author(s):  
Ilias P Doulamis ◽  
Supreet P Marathe ◽  
Breanna L Piekarski ◽  
Rebecca S Beroukhim ◽  
Gerald R Marx ◽  
...  
Keyword(s):  
Fontan Circulation ◽  
Exercise Intolerance ◽  
Optimal Timing ◽  
Atrioventricular Canal ◽  
Protein Losing Enteropathy ◽  
Systolic Volume ◽  
Hepatic Congestion ◽  
Atrioventricular Canal Defect ◽  
Fontan Physiology ◽  
Failing Fontan

Hypothesis: Biventricular conversion (BiVC) following takedown of Fontan circulation is feasible and results in improved hemodynamics. Methods: Retrospective analysis of patients who had takedown of Fontan circulation and conversion to BiV circulation at a single center from September 2007 to April 2020. Failing Fontan physiology was defined as Fontan circulation pressure >15 mmHg. Results: There were 23 patients (median age: 10.0 (7.5-13.0) years); 15 (65%) had failing Fontan physiology and 8 (35%) underwent elective takedown of their Fontan circulation. Of the 15 patients with failing Fontan physiology, 4 had exercise intolerance or cyanosis, 3 had hepatic congestion or cirrhosis, 3 had end-organ damage and 1 patient had protein losing enteropathy; the rest 4 patients had no other sign of SVP complications. A subset of patients (n=6) underwent recruitment of the non-dominant ventricle prior to conversion. HLHS (p<0.01) and sub-/aortic stenosis (p<0.01) were more common in these patients. BiVC with or without staged ventricular recruitment led to a significant increase in indexed end-diastolic volume (p<0.01), indexed end-systolic volume (p<0.01) and ventricular mass (p<0.01) of the non-dominant ventricle (14 RV, 9 LV). There were 1 (4%) early and 4 (17%) late deaths. All who underwent elective BiVC survived, while 2-year survival rate for patients with a failing Fontan circulation was 72.7% (95% CI: 37-90%) (Figure 1). The overall, 1-year reintervention free survival was 44.1% (95% CI: 21-65%). Left dominant atrioventricular canal defect (p<0.01) and early year of BiVC (p=0.02) were significant predictors for mortality. Conclusions: BiVC is feasible in patients with failing Fontans, and has promising outcomes after elective takedown of Fontan circulation. A staged approach for ventricular recruitment does not seem inferior to primary BiVC. The optimal timing for BiVC in Fontan patients needs further evaluation.

scholarly journals Protein-Losing Enteropathy and Plastic Bronchitis After the Fontan Operation

2018 ◽  
Vol 38 (6) ◽  
pp. e5-e12 ◽  
Author(s):  
Christine Peyton
Keyword(s):  
Heart Failure ◽  
Congestive Heart Failure ◽  
Complex Disease ◽  
Fontan Procedure ◽  
Fontan Operation ◽  
Venous Pressure ◽  
Venous Hypertension ◽  
Plastic Bronchitis ◽  
Protein Losing Enteropathy ◽  
Fontan Physiology

Protein-losing enteropathy and plastic bronchitis remain challenging to treat despite recent treatment advances. Protein-losing enteropathy and plastic bronchitis have been diagnosed in patients with cardiomyopathy, constrictive pericarditis, and congestive heart failure. This article focuses on patients with protein-losing enteropathy or plastic bronchitis following the Fontan procedure. Patients with single-ventricle physiology who have undergone the Fontan procedure are at risk for these conditions. Fontan physiology predisposes patients to chronically low cardiac output, increased central venous pressure, and congestive heart failure. These altered hemodynamics lead to increased mesenteric vascular resistance, resulting in venous hypertension and congestion in protein-losing enteropathy. Plastic bronchitis is a complex disease in which chronic high lymphatic pressures from Fontan physiology cause acellular bronchial casts to develop. These entities may also occur in patients with normal Fontan hemodynamics. This article also covers medical and surgical interventions for protein-losing enteropathy and plastic bronchitis. (Critical Care Nurse. 2018;38[6]:e5–e12)

PULMONARY ARTERY WALL THICKNESS IN CHILDREN WITH FONTAN PHYSIOLOGY – AN OPTICAL COHERENCE TOMOGRAPHY CASE CONTROL STUDY

2017 ◽  
Vol 33 (10) ◽  
pp. S6-S7
Author(s):  
E. McGovern ◽  
C. Voss ◽  
S. Duncombe ◽  
M. Hosking ◽  
K. Harris
Keyword(s):  
Optical Coherence Tomography ◽  
Pulmonary Artery ◽  
Wall Thickness ◽  
Case Control Study ◽  
Case Control ◽  
Optical Coherence ◽  
Artery Wall ◽  
Fontan Physiology ◽  
Control Study

scholarly journals MACITENTAN USE AS SERIAL THERAPY IN FAILING FONTAN PHYSIOLOGY

2017 ◽  
Vol 69 (11) ◽  
pp. 632
Author(s):  
Tabitha Grace Moe
Keyword(s):  
Fontan Physiology ◽  
Failing Fontan

A cost-conscious approach to robotic adrenalectomy

2018 ◽  
Vol 12 (4) ◽  
pp. 607-611 ◽  
Author(s):  
Zuliang Feng ◽  
Michael P. Feng ◽  
David P. Feng ◽  
Mark J. Rice ◽  
Carmen C. Solórzano
Keyword(s):  
Robotic Adrenalectomy
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