Improved Outcomes in Management of Hypoplastic Left Heart Syndrome Associated With Congenital Diaphragmatic Hernia: an Algorithmic Approach

2018 ◽  
Vol 30 (2) ◽  
pp. 191-196 ◽  
Author(s):  
Kaitlin Balduf ◽  
T.K. Susheel Kumar ◽  
Umar Boston ◽  
Shyam Sathanandam ◽  
Marc V. Lee ◽  
...  
Keyword(s):  
Congenital Diaphragmatic Hernia ◽  
Hypoplastic Left Heart Syndrome ◽  
Diaphragmatic Hernia ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Algorithmic Approach ◽  
Improved Outcomes ◽  
Left Heart Syndrome

Hybrid Stage I Procedure as Initial Palliation for Neonate With Hypoplastic Left Heart Syndrome and Right Congenital Diaphragmatic Hernia

2017 ◽  
Vol 21 (2) ◽  
pp. 145-151 ◽  
Author(s):  
Draginja Cvetkovic ◽  
Joseph Giamelli ◽  
Michael Lyew ◽  
Markus Erb ◽  
Suvro Sett ◽  
...  
Keyword(s):  
Congenital Diaphragmatic Hernia ◽  
Hypoplastic Left Heart Syndrome ◽  
Diaphragmatic Hernia ◽  
Stage I ◽  
Pulmonary Vasculature ◽  
Coronary Perfusion ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Bilateral Pulmonary Artery Banding ◽  
Left Heart Syndrome

During the past decade, a hybrid procedure has emerged and dramatically evolved as an alternative stage I palliation to the conventional Norwood procedure in neonates with hypoplastic left heart syndrome (HLHS). The hybrid approach avoids the need for cardiopulmonary bypass (CPB) utilizing stenting of the arterial duct and bilateral pulmonary artery banding. Cerebral and coronary perfusion pressure is maintained, and the pulmonary vasculature is protected from higher systemic pressure. Elimination of risks associated with CPB gains vital time to stabilize the patient and correct coexisting noncardiac anomalies and allows growth in preparation for the later stages of the Fontan pathway. The association of HLHS with right congenital diaphragmatic hernia (CDH) is rare. We report performing a successful hybrid stage I palliation on a neonate with HLHS and severe right CDH.

Congenital right-sided diaphragmatic hernia and hypoplastic left heart syndrome

1985 ◽  
Vol 109 (1) ◽  
pp. 177-178 ◽  
Author(s):  
Iraj A. Kashani ◽  
Herbert Kimmons ◽  
Lilliam M. Valdes-Cruz ◽  
Richard E. Swensson ◽  
David J. Sahn ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Diaphragmatic Hernia ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Hypoplastic Left Heart Syndrome Associated with Congenital Right-Sided Diaphragmatic Hernia and Omphalocele

CHEST Journal ◽  
1992 ◽  
Vol 101 (1) ◽  
pp. 263-264 ◽  
Author(s):  
Masaji Nishimura ◽  
Akihiro Taniguchi ◽  
Hideaki Imanaka ◽  
Nobuyuki Taenaka
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Diaphragmatic Hernia ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Achieving a balance in the current approach to the surgical treatment of hypoplastic left heart syndrome

2004 ◽  
Vol 14 (S1) ◽  
pp. 127-130 ◽  
Author(s):  
James A. Quintessenza ◽  
Victor O. Morell ◽  
Jeffrey P. Jacobs
Keyword(s):  
Surgical Treatment ◽  
Hypoplastic Left Heart Syndrome ◽  
Cardiac Transplantation ◽  
State Of The Art ◽  
Current Approach ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Improved Outcomes ◽  
Technical Advances ◽  
Left Heart Syndrome

In this Supplement, and at its associated Symposium “Controversies of Hypoplastic Left Heart Syndrome”, various contributors presented a variety of topics regarding “state of the art” treatments for hypoplastic left heart syndrome. The extent of the differences within these various presentations attests to the very significant challenges that remain in optimizing care of these patients, and related ones with other types of functionally univentricular hearts. Of these challenges, the initial surgical approach, be it staged palliation or cardiac transplantation, has been a hotly debated issue, with diametrically opposed schools of thought.1Today, with further experience, technical advances, and dramatically improved outcomes, there seems to be an emerging complimentary role for both options, favoring a staged reconstructive approach in the majority of circumstances. We review here the salient issues that have lead to this position, and discuss strategies for maintaining a program offering both staged palliation and transplantation for patients with hypoplasia of the left heart.

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