scholarly journals VP007 MULTIRECIDIVATED DESMOÍD TUMOR OF THE THORAX-ABDOMINAL WALL

2021 ◽  
Vol 108 (Supplement_8) ◽  
Author(s):  
Luis Blázquez Hernando ◽  
Belén Porrero Guerrero ◽  
Antonio Mena ◽  
Jose Manuel Molina Villar ◽  
David Saldaña ◽  
...  

Abstract Aim Treatment of recurrent desmoid tumors represents a real challenge for the surgeon. The purpose of the video is to show the treatment of a multirecidivated complex desmoid tumor that affects the lateral thoracoabdominal wall. Material and Methods 24-year-old woman with the diagnosis of recurrent desmoid tumor. She was operated in 2014 for a 10 cm desmoid tumor in the left chest wall with affected margins in the biopsy. In 2016 she underwent surgery for a 5 cm recurrence, which was excised en bloc along with the 6th, 7th, 8th and 9th rib arches. In 2018 she presented a recurrence in the scar treated by radiotherapy. She now presents a recurrence that in the CT scan is seen as an 8 cm tumor that affects the thoraco-abdominal wall. Results We perform a complete resection with free margins and “en bloc” resection of the 8th, 9th, 10th and 11th rib arches. We repair the defect using a reverse TAR and rebuild the wall with the Madrid APPROACH technique with BioA and polypropylene meshes. The patient was discharged 11 days after surgery without any complications. The pathological study showed an 8 cm desmoid tumor with free surgical margins. The patient a year after surgery remains disease free. Conclusions The resection of a desmoid tumor that affects the abdominal and/or thoracic wall, especially if it is recurrent, represents a challenge for the surgeon. Component separation techniques and Madrid APPROACH may be very useful to achieve an optimal repair.

2009 ◽  
Vol 10 (5) ◽  
pp. 397-403 ◽  
Author(s):  
Dean Chou ◽  
Frank Acosta ◽  
Jordan M. Cloyd ◽  
Christopher P. Ames

En bloc resection of chordoma has been shown to be critical for prolonging long-term survival and disease-free intervals in patients. Cervical spine chordomas pose special challenges because of the vertebral arteries and critical nerve roots involved. Multilevel chordomas pose even greater challenges because of the need to remove multiple segments of the spine in 1 piece without tumor violation. Although there have been 2 case reports describing multilevel spondylectomy for cervical chordoma, to the authors' knowledge, there are no reports of parasagittal osteotomies for en bloc resection of multilevel cervical chordomas. The use of these osteotomies allows us to avoid intralesional resection and adhere to the oncological principle of en bloc tumor excision. The authors report their management of 3 multilevel cervical chordomas and describe their technique of en bloc tumor removal using parasagittal osteotomy.


Neurosurgery ◽  
2010 ◽  
Vol 67 (2) ◽  
pp. 435-445 ◽  
Author(s):  
Jordan M. Cloyd ◽  
Frank L. Acosta ◽  
Mei-Yin Polley ◽  
Christopher P. Ames

Abstract BACKGROUND The efficacy of en bloc resection for spinal tumors is unknown because most of the current evidence is provided by small, single-institution clinical series or case reports. OBJECTIVE To combine all previously published reports of en bloc resection for primary and metastatic spinal tumors, to describe the overall pattern of disease-free survival, and to investigate potentially prognostic factors for recurrence. METHODS A complete MEDLINE search for all articles reporting survival data for en bloc resection of spinal tumors was undertaken; 44 articles met inclusion criteria from which 306 eligible patients were identified. RESULTS There were 229 cases of primary tumors with a mean follow-up of 65.0 months and 77 cases of solitary metastatic tumors with a mean follow-up of 26.5 months. Median time to recurrence was 113 months for the primary group and 24 months for the metastatic group. Disease-free survival rates at 1, 5, and 10 years were 92.6%, 63.2%, and 43.9%, respectively, for the primary group and 61.8%, 37.5%, and 0%, respectively, for the metastatic group; 5-year disease-free survival rates were 58.4% for chordoma and 62.9% for chondrosarcoma. After adjusting for covariates, age, male sex, metastatic tumors, and osteosarcomas were significantly associated with a tumor recurrence. CONCLUSION This study provides the largest published series of patients undergoing en bloc resection for spinal tumors. Median time to recurrence reached almost 10 years in patients with primary tumors; however, it was only 2 years in those with isolated metastatic tumors.


2021 ◽  
Vol 94 (2) ◽  
pp. 256-259
Author(s):  
Miana Pop ◽  
Dana Bartos ◽  
Ofelia Anton ◽  
Ioana Rusu ◽  
Lidia Ciobanu ◽  
...  

Desmoid tumors (DT) are rare non-metastatic neoplasms that occur through myofibroblast proliferation in musculoaponeurotic or fascial structures of the body, being commonly diagnosed in young women during pregnancy or in the post-partum period. We present the case of a 38-year-old woman, who recently gave birth, manifesting non-specific abdominal symptoms. Computed tomography indicated the presence of a solitary tumor arising from the intestinal wall or from the mesentery. Surgery confirmed the diagnosis, revealing a tumor that was localized at the level of the jejunal mesentery, having about 7 cm in diameter, in tight contact with the duodenum and the mesenteric vessels. ‘‘En bloc’’ resection of the tumor was performed, together with the involved enteral loops followed by end-to-end anastomosis of the jejunum. Histopathological examination of the surgical specimen sustained the diagnosis of desmoid tumor.


Medicine ◽  
2015 ◽  
Vol 94 (27) ◽  
pp. e1019 ◽  
Author(s):  
Mathew David Sewell ◽  
Kimberly-Anne Tan ◽  
Nasir A. Quraishi ◽  
Corina Preda ◽  
Peter P. Varga ◽  
...  

2008 ◽  
Vol 65 (2) ◽  
pp. 175-177
Author(s):  
Vojkan Stanic ◽  
Tatjana Vulovic ◽  
Davor Stamenovic ◽  
Gordana Djordjevic

Background. Sternal benign neoplasms are extremely rare. Chondroma is a benign tumor of cartilage and can be single or multiple. Case report. We presented a case of 28-year-old woman with chondroma of the sternum treated by "en bloc" resection of the tumor (subtotal sternectomy). The chest wall defect was repaired by the placement of Marlex mesh and metylmethacrylate ("sandwich method") for stabilization of the thoracic wall. This place was covered with pectoralis major muscle and skin. The postoperative course was uneventful and the wounds healed by primary intention. Conclusion. The functional and cosmetic results in the usage of Marlex mesh with metylmethacrylate to repair a large full-thickness defect after subtotal sternectomy caused by chondroma were good and the patient was able to resume her preoperative level of activity.


CHEST Journal ◽  
1982 ◽  
Vol 81 (2) ◽  
pp. 203-207 ◽  
Author(s):  
Joseph F. Paone ◽  
Everett K. Spees ◽  
Charles G. Newton ◽  
Keith D. Lillemoe ◽  
Richard F. Kieffer ◽  
...  

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