LEFT VENTRICULAR OUTFLOW TRACT OBSTRUCTION (LVOTO) FROM CARDIAC RHABDOMYOMA AND TUBEROUS SCLEROSIS COMPLEX (TSC) IN A NEONATE

2004 ◽  
Vol 32 (Supplement) ◽  
pp. A185
Author(s):  
Cindy S Barrett ◽  
Ira Cheifetz ◽  
James Jaggers
Keyword(s):  
Tuberous Sclerosis ◽  
Tuberous Sclerosis Complex ◽  
Left Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Left Ventricular ◽  
Outflow Tract ◽  
Cardiac Rhabdomyoma ◽  
Ventricular Outflow Tract Obstruction ◽  
Left Ventricular Outflow

Everolimus treatment in a 3-month-old infant with tuberous sclerosis complex cardiac rhabdomyoma, severe left ventricular outflow tract obstruction, and hearing loss

2021 ◽  
pp. 1-4
Author(s):  
Mecnun Çetin ◽  
Aysun A. Aydın ◽  
Kamuran Karaman
Keyword(s):  
Hearing Loss ◽  
Tuberous Sclerosis ◽  
Tuberous Sclerosis Complex ◽  
Protein Complex ◽  
Left Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Left Ventricular ◽  
Outflow Tract ◽  
The Body ◽  
Left Ventricular Outflow

Abstract Tuberous sclerosis complex is a rare multisystem genetic disorder characterised by the growth of numerous tumour-like malformations in many parts of the body including skin, kidneys, brain, lung, eyes, liver, and heart. Mutations in the TSC1 or TSC2 genes have been reported to cause disruption in the TSC1–TSC2 intracellular protein complex, causing over-activation of the mammalian target of rapamycin protein complex. In this study, we present a 3-month-old male infant diagnosed with tuberous sclerosis, bilateral neurosensorial hearing loss, Wolff–Parkinson–White syndrome on electrocardiography, multiple cardiac rhabdomyomas with severe stenosis in the left ventricular outflow tract, who responded well to the Everolimus therapy.

scholarly journals Norepinephrine-associated left ventricular outflow tract obstruction and systolic anterior movement

2019 ◽  
Vol 12 (12) ◽  
pp. e225879 ◽  
Author(s):  
Warner Mbuila Mampuya ◽  
Jonathan Dumont ◽  
Francois Lamontagne
Keyword(s):  
Blood Pressure ◽  
Left Ventricular Outflow Tract ◽  
Myocardial Hypertrophy ◽  
Ventricular Outflow Tract ◽  
Left Ventricular ◽  
Outflow Tract ◽  
Increase Blood Pressure ◽  
Ventricular Outflow Tract Obstruction ◽  
Left Ventricular Outflow ◽  
Systolic Anterior Movement

In the perioperative setting, norepinephrine is used to increase blood pressure, an effect mediated mostly via arterial and venous vasoconstriction. Thus, norepinephrine is, allegedly, less likely to cause or worsen left ventricular outflow tract obstruction (LVOTO) than other inotropes. We report a case of norepinephrine-associated dynamic LVOTO and systolic anterior movement in a predisposed patient. This report highlights that unrecognised dynamic LVOTO may worsen shock parameters in patients treated with norepinephrine who have underlying myocardial hypertrophy.

scholarly journals Unstable angina complicated with dynamic left ventricular outflow tract obstruction

2021 ◽  
Vol 23 (4) ◽  
pp. 181-188
Author(s):  
Kazuyuki Ozaki ◽  
Takeshi Okubo ◽  
Kenichi Hagiya ◽  
Naoki Kubota ◽  
Keiichi Tsuchida ◽  
...  
Keyword(s):  
Unstable Angina ◽  
Left Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Left Ventricular ◽  
Outflow Tract ◽  
Ventricular Outflow Tract Obstruction ◽  
Left Ventricular Outflow
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