ABNORMAL INTRACRANIAL VASCULAR NETWORKS (“MOYAMOYA” DISEASE), POSSIBLY DUE TO OCCLUSION OF BILATERAL INTERNAL CAROTID ARTERIES - A CASE REPORT WITH HISTOMETRICAL ANALYSIS -

1976 ◽  
Vol 26 (1) ◽  
pp. 105-114
Author(s):  
Isao Okayasu ◽  
Akira Kajita ◽  
Masaaki Yamamoto
Author(s):  
Julius July

Moyamoya disease that manifests during childhood may pose a special challenge for surgeons. We report a case of a 10-year-old girl who suffered from moyamoya disease and was successfully treated with encephalo-duro-myo-arterio-pericranial synangiosis (EDMAPS). She presented with a recurrent transient ischemic attack that worsened for 1 year. She was aphasic globally (sensory and motor) and had slightly weak right extremities. Her magnetic resonance angiography and computed tomography angiography showed the typical features of moyamoya disease with bilateral stenosis at the terminal internal carotid artery, bilaterally abnormal vascular networks, and a left ischemic event involving the temporoparietal region. She was recovered well after underwent bilateral EDMAPS, fully regained her language function after 3 months, and gathered her strength back. Therefore, EDMAPS could be a good, safe, and effective treatment for moyamoya disease in children.


2013 ◽  
Vol 127 (2) ◽  
pp. 196-199 ◽  
Author(s):  
L-S Tseng ◽  
S-D Luo

AbstractObjective:We describe a rare case of sudden onset of unilateral sensorineural hearing loss occurring as the first symptom of moyamoya disease, which is characterised by progressive stenosis of the intracranial internal carotid arteries and their proximal anterior cerebral arteries and middle cerebral arteries.Method:Case report and review of the world literature regarding moyamoya disease with hearing loss.Results:The reported patient had moyamoya disease that initially presented as sudden, unilateral sensorineural hearing loss. Magnetic resonance imaging showed occlusion of the anterior cerebral, middle cerebral and distal internal carotid arteries bilaterally. The possible mechanism of this patient's sudden sensorineural hearing loss may have been vascular occlusion resulting from thrombotic narrowing or blockage by plaque.Conclusion:The described patient represents the first reported case of sudden onset, unilateral sensorineural hearing loss occurring as the first symptom of moyamoya disease. The possibility of a vascular lesion such as moyamoya disease should be considered in patients with sudden sensorineural hearing loss, especially children, young adults and Asian patients. Due to this disease's poor outcome, early diagnosis and treatment are important to prevent stroke.


2014 ◽  
Vol 6 (2) ◽  
Author(s):  
Sarmad Said ◽  
Chad J. Cooper ◽  
Haider Alkhateeb ◽  
Juan M. Galvis ◽  
German T. Hernandez ◽  
...  

Moyamoya disease was first described in 1957 as <em>hypoplasia of the bilateral internal carotid arteries</em>, the characteristic appearance of the associated network of abnormally dilated collateral vessels on angiography was later likened to something hazy, like a puff of cigarette smoke, which, in Japanese, is <em>moyamoya</em>. This paper describes two cases of moyamoya presentations, including moyamoya disease and moyamoya syndrome. Moyamoya may rarely occur in North American Hispanic patients. The presentation can vary significantly and ranges bwtween fulminant outcome and prolonged survival. Awareness about moyamoya and its different presentations may be beneficial for the patients and can improve the outcome.


2017 ◽  
Vol 4 (3) ◽  
pp. 67-69
Author(s):  
Toshiyuki Ohtani ◽  
Keiya Iijima ◽  
Kaoru Aishima ◽  
Hajime Wada ◽  
Nobuo Sasaguchi ◽  
...  

2021 ◽  
Author(s):  
Lidiane Moreira Lima Rebouças ◽  
Alexandra de Oliveira Lopes ◽  
Samara Belchior Gaído ◽  
Camila Maria Bomtempo Seba de Souza ◽  
Maria Carolina Albuquerque de Sousa Martins ◽  
...  

2009 ◽  
Vol 26 (4) ◽  
pp. E7 ◽  
Author(s):  
Ali A. Baaj ◽  
Siviero Agazzi ◽  
Zafar A. Sayed ◽  
Maria Toledo ◽  
Robert F. Spetzler ◽  
...  

Moyamoya disease (MMD) is a progressive, occlusive disease of the distal internal carotid arteries associated with secondary stenosis of the circle of Willis. Symptoms include ischemic infarcts in children and hemorrhages in adults. Bypass of the stenotic vessel(s) is the primary surgical treatment modality for MMD. Superficial temporal artery-to-middle cerebral artery bypass is the most common direct bypass method. Indirect techniques rely on the approximation of vascularized tissue to the cerebral cortex to promote neoangiogenesis. This tissue may be in the form of muscle, pericranium, dura, or even omentum. This review highlights the surgical options available for the treatment of MMD.


Sign in / Sign up

Export Citation Format

Share Document