Primary repair of complete sternal cleft associated with absent anterior pericardium

2017 ◽  
Vol 32 (5) ◽  
pp. 316-317
Author(s):  
Amr A. Arafat ◽  
Ayman A. Sallam ◽  
Amr A. Abdelwahab ◽  
Abdel-Hady M. Taha
Keyword(s):  
2013 ◽  
Vol 17 (6) ◽  
pp. 1036-1037 ◽  
Author(s):  
Quentin Ballouhey ◽  
Mateo Armendariz ◽  
Virginie Vacquerie ◽  
Pierre Sylvain Marcheix ◽  
Daniel Berenguer ◽  
...  
Keyword(s):  

Author(s):  
R. Sekelyk ◽  
D. Kozhokar ◽  
I. Yusifli ◽  
R. Tammo ◽  
I. Yemets

Sternal cleft is a rare congenital abnormality that results from incomplete fusion of the two lateral mesodermal sternal bars. It is generally accepted that primary repair in the neonatal period is the best treatment option. However, significant distance between the sternal bars can be challenging because of cardiac compression. The aim. We report a case of a 7-day-old neonate with a subtotal sternal cleft successfully managed by direct closure. Material and methods. A full-term male neonate weighing 3 kg was referred to our clinic for evaluation of a chest wall defect. The chest X-ray and computed tomography were performed to evaluate the malformation. Results. Surgery was performed at the age of 7 days. Postoperative period was uneventful. The patient was discharged on the postoperative day 21. The first postoperative checkup after 3 months showed satisfactory cosmetic results and normal respiratory movements. Conclusion. Despite the significant diastasis between sternal bars, primary direct closure of the sternal cleft can be safely performed in neonates.


1996 ◽  
Vol 61 (3) ◽  
pp. 983-984 ◽  
Author(s):  
Brett J. Snyder ◽  
Robert C. Robbins ◽  
Douglas Ramos

2021 ◽  
Vol 17 (1) ◽  
Author(s):  
Halil Ibrahim Tanriverdi ◽  
Fulya Doğaneroğlu ◽  
Abdülkadir Genç ◽  
Ömer Yılmaz

Abstract Background Sternal cleft is a quite rare malformation. It is seen 1 out of 100,000 live births and makes up less than 1% of all chest wall deformities, seen more often among females. The deformity can be partial or complete. Partial deformities can be superior or inferior. It is generally diagnosed at birth when paradoxical respiratory movements are seen. Patients are often asymptomatic when they are born and generally other abnormalities accompany. As sternal clefts can be repaired primarily at early ages, they are repaired using autologous or synthetic grafts in the following years. We present a 2-month-old girl with superior partial sternal cleft repaired primary and accompanying hemangiomas in this case report. Case presentation A girl who was born in another center and had a sternal cleft, who did not have any problems in the early period, was admitted to our hospital with respiratory distress at the age of 43 days. The patient was monitored with mechanical ventilator support, and there were hemangiomas around his left ear and lips. There were paradoxical respiratory movements in front of the heart, in the upper midline of the chest. Three-dimensional computed tomography showed that the upper part of the sternum did not develop, and there were hypoplasic sternal bars on both sides. It was evaluated as superior partial sternal cleft, and surgery was planned. In the operation, the sternal bars were released from the pericardium and pleura. The periosteum in the medial of both sternal bars was then released and connected in the midline, in front of the pericardium. Conclusion Although neonates with a sternal cleft are asymptomatic at birth, respiratory symptoms may develop in later periods. In addition, because the structures are more flexible in the neonatal period, the primary repair of the cleft is easier and the risk of cardiac compression is lower. In our case, sternal bars could be approached primary, and no chondral grafts, patches, or steel wires were required.


2020 ◽  
Vol 73 (6) ◽  
pp. 1267-1271
Author(s):  
Iryna M. Benzar ◽  
Anatolii F. Levytskyi ◽  
Vlasii M. Pylypko

The aim is to determine the risk factors of sternal cleft and segmental facial hemangiomas association in children with PHACES syndrome. Materials and methods: 32 inpatient children with segmental facial hemangiomas and 19 children with sternal cleft were investigated concerning the Metry criteria of PHACES syndrome. Results: In 6 children PHACE syndrome was diagnosed. Patients with bilateral S3 hemangiomas (50%, 3/6) had airway involvement with respiratory disorders. Conservative treatment was propranolol monotherapy (66.7%, 4/6), or combination of prednisolone and propranolol (33.3%, 2/6). Duration of propranolol treatment in children with PHACES syndrome was on an average 24.25 � 4.49 months exceeding the duration of propranolol therapy in children with isolated soft tissue lesions (p<0.05). Primary surgical treatment of sternal cleft performed in children aged 2 (n=3) and 4 (n=1) months. The later period of surgery associated with the localization of hemangioma in the surgery region. Primary repair of sternal cleft was completed successfully in all cases; partial resection of the thymus made closure easier. Conclusions: Primary surgical correction of a sternal cleft performed in young children provides good results. Partial resection of the thymus prevents respiratory and cardiovascular complications. Preoperative propranolol treatment averts the hemorrhagic complications in children with hemangiomas in surgical region.


2008 ◽  
Vol 43 (10) ◽  
pp. e39-e41 ◽  
Author(s):  
Eyad B. Baqain ◽  
Isam M. Lataifeh ◽  
Wadah M. Khriesat ◽  
Nayef M. Fraiwan ◽  
Mohamed A. Armooti

Author(s):  
Raina Sinha ◽  
Jennifer Knod ◽  
Katerina Dukleska ◽  
Dennis Mello

We present a full-term neonate with a postnatal diagnosis of a sternal cleft. Cardiac evaluation was otherwise remarkable for a patent ductus arteriosus and patent foramen ovale. Computed tomography scan confirmed the absence of a sternum except for a small inferior portion, including the xyphoid process. The patient underwent primary repair at five days of age through a midline incision where an absence of pericardium anteriorly was noted. She was extubated successfully the next day and discharged home on postoperative day 3. On follow-up examination, her sternum has been healing well without any clinical concerns. We advocate early repair of such defects in order to allow primary closure in a tension-free manner.


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