Assessment of vascular phenotype using a novel very high resolution ultrasound technique in adolescents after aortic coarctation repair and/or stent implantation: relationship to central haemodynamics and left ventricular mass

Abstract Background Cardiac fibroma and aortic coarctation are rarely observed concomitantly in the same patient. We report a case of cardiac fibroma with aortic coarctation treated with a hybrid surgical procedure. To the best of our knowledge, this is the first case of these two abnormalities existing in one patient. Case summary A 22-year-old female patient visited the clinic with a 10-year history of hypertension. Physical examination revealed blood pressure of the upper extremities 50 mmHg higher than that of the lower extremities. Computed tomography angiography revealed a post-ductal-type aortic coarctation at the beginning segment of the descending aorta along with a 7.7 cm × 5.1 cm left ventricular mass. Transthoracic echocardiogram showed a mass at the middle segments of the lateral wall and apex and posterior wall of the left ventricle. Cardiac magnetic resonance imaging also showed the mass with hypointense signal on T1, hyperintense signal on T2, and intense signal on late gadolinium enhancement. No evidences of metastatic lesions were observed on 18F-fluorodeoxyglucose positron emission tomography. The patient underwent a hybrid surgery involving aortic stent implantation and complete left ventricular mass removal. The gradient between stenosis returned to <10 mmHg after the procedure. Pathologic findings revealed cardiac fibroma. Discussion It is rare to encounter a patient suffering from both cardiac fibroma and aortic coarctation. No evidences indicated a single cause or syndrome resulting in the coexistence of these two abnormalities. A hybrid surgery involving aortic stent implantation and complete cardiac mass resection could optimize the treatment in such cases.

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Inappropriately high left ventricular mass: marker of very high cardiovascular risk in patients with chronic kidney disease?

Hypertension Research ◽

10.1038/hr.2012.64 ◽

2012 ◽

Vol 35 (8) ◽

pp. 800-801 ◽

Cited By ~ 1

Author(s):

Emilio Nardi ◽

Alessandro Palermo ◽

Giuseppe Mulè

Keyword(s):

Chronic Kidney Disease ◽

Cardiovascular Risk ◽

Kidney Disease ◽

Left Ventricular Mass ◽

Left Ventricular ◽

High Cardiovascular Risk ◽

Ventricular Mass ◽

Very High

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Angular (Gothic) aortic arch leads to enhanced systolic wave reflection, central aortic stiffness, and increased left ventricular mass late after aortic coarctation repair: Evaluation with magnetic resonance flow mapping

Journal of Thoracic and Cardiovascular Surgery ◽

10.1016/j.jtcvs.2007.03.059 ◽

2008 ◽

Vol 135 (1) ◽

pp. 62-68 ◽

Cited By ~ 81

Author(s):

Phalla Ou ◽

David S. Celermajer ◽

Olivier Raisky ◽

Odile Jolivet ◽

Fanny Buyens ◽

...

Keyword(s):

Magnetic Resonance ◽

Aortic Arch ◽

Left Ventricular Mass ◽

Aortic Coarctation ◽

Aortic Stiffness ◽

Wave Reflection ◽

Left Ventricular ◽

Flow Mapping ◽

Ventricular Mass ◽

Resonance Flow

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A successful management of late-presenting transposition with intact septum and severe coarctation of the aorta

SAGE Open Medical Case Reports ◽

10.1177/2050313x20956412 ◽

2020 ◽

Vol 8 ◽

pp. 2050313X2095641

Author(s):

Pribadi Wiranda Busro ◽

Alvin Ariyanto Sani ◽

Michael Caesario

Keyword(s):

Left Ventricular Mass ◽

Aortic Coarctation ◽

Left Ventricular Mass Index ◽

Ductus Arteriosus ◽

Left Ventricular ◽

Ventricular Septum ◽

Intact Ventricular Septum ◽

Ventricular Mass Index ◽

Arterial Switch ◽

Ventricular Mass

A 13-week-old baby was referred with dextrocardia, situs inversus, transposition of the great arteries, intact ventricular septum, patent foramen ovale, right aortic arch with severe preductal aortic coarctation and large patent ductus arteriosus. Left ventricular mass index as well as thickness was adequate, 118 g/m2 and 5.9 mm, respectively; thus, a primary arterial switch with aortic coarctation repair was performed. The patient made a full recovery without the need for extracorporeal life support. Adequate left ventricular mass index and thickness in late-presenting transposition of the great arteries with intact ventricular septum might justify primary arterial switch.

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