THROMBOSED BRAINSTEM DEVELOPMENTAL VENOUS ANOMALY CAUSING HYDROCEPHALUS

Developmental venous anomaly (DVA) is a commonly encountered congenital abnormality of the venous drainage system. Spontaneous thrombosis of DVA is rare. We present a case of thrombosed brainstem DVA leading to venous infarction and oedema within the posterior fossa.A 49 year old, previously fit gentleman presented to the local hospital with a one day history of headache, slurred speech and incoordination. Examination demonstrated GCS of 13/15, cerebellar dysarthria, horizontal nystagmus to the left, mild right sided pyramidal weakness, right sided cerebellar ataxia and bilateral extensor plantars.CT venogram revealed a cerebellar DVA with thrombosis of one of the veins. There was surrounding venous infarction and oedema within the posterior fossa, causing compression of the fourth ventricle and dilatation of the lateral ventricles. MRI demonstrated extensive T2 change in the right cerebellar hemisphere, dorsal pons and right cerebral peduncle. No underlying thrombotic tendency was identified. He was treated successfully with intravenous heparin infusion. He improved over the next 3 weeks, and was discharged on warfarin with mild right sided ataxia and cerebellar dysarthria.Our case demonstrates that DVAs, generally considered as common insignificant anatomical variants, can uncommonly lead to significant complications.

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Teaching NeuroImages: A giant developmental venous anomaly in the absence of a superficial venous drainage system

Neurology ◽

10.1212/wnl.0b013e3181feb247 ◽

2010 ◽

Vol 75 (21) ◽

pp. e88-e88

Author(s):

A. M. G. Fuhler ◽

J. M. C. van Dijk ◽

K. Koopman ◽

G. J. Luijckx

Keyword(s):

Drainage System ◽

Venous Drainage ◽

Developmental Venous Anomaly ◽

Venous Anomaly

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Developmental Venous Anomaly with Contralateral Impaired Venous Drainage in a 17-Year-Old Male

Interventional Neuroradiology ◽

10.1177/159101991301900110 ◽

2013 ◽

Vol 19 (1) ◽

pp. 67-72 ◽

Cited By ~ 3

Author(s):

Jmn Enslin ◽

D. Lefeuvre ◽

A. Taylor

Keyword(s):

Young Patient ◽

Right Hemisphere ◽

Neural Tissue ◽

Venous Drainage ◽

Developmental Venous Anomaly ◽

Venous Anomaly ◽

Drainage Pattern ◽

Venous Outflow ◽

Developmental Venous Anomalies ◽

The Right

Developmental venous anomalies (DVA) drain normal neural tissue and are mostly discovered incidentally. We describe a young patient with a left hemisphere superficial to deep DVA and right hemisphere venous outflow restriction presenting with a seizure. The right hemisphere drainage variation is not typical of a DVA but represents another drainage pattern on the border of normality.

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Infantile Dural Arteriovenous Shunt Draining into a Developmental Venous Anomaly

Interventional Neuroradiology ◽

10.1177/159101990701300109 ◽

2007 ◽

Vol 13 (1) ◽

pp. 67-74 ◽

Cited By ~ 10

Author(s):

S. Geibprasert ◽

T. Krings ◽

V. Pereira ◽

P. Lasjaunias

Keyword(s):

Cerebral Hemisphere ◽

Venous Drainage ◽

Developmental Venous Anomaly ◽

Venous Anomaly ◽

Adult Type ◽

Sagittal Sinus ◽

Right Cerebral Hemisphere ◽

Arteriovenous Shunts ◽

Dural Arteriovenous Shunts ◽

The Right

A three-year-old girl with an incidentally discovered infantile type of dural arteriovenous shunts (DAVs) along the superior sagittal sinus during investigation of a minor head trauma is presented. The DAVs drained into a developmental venous anomaly of the right cerebral hemisphere. In addition, there was a small cavernoma within the territory drained by the DVA. The patient underwent multiple transarterial embolizations to decrease the shunt flow and thus the constrained venous drainage of the DVA and right cerebral hemisphere. Pediatric dural arteriovenous shunts are a different entity from the adult type DAVs and should be managed according to the growth and development of the child. DVAs are extreme variations of the venous system with reduced flexibility to increased venous drainage. Regardless of the type of treatment employed, the DVA and its drainage pathway must be preserved.

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Rare Abnormality of the Posterior Fossa: Unilateral İsolated Cerebellar Hypoplasia

Journal of Pediatric Neurology ◽

10.1055/s-0040-1713110 ◽

2020 ◽

Author(s):

Merter Keçeli

Keyword(s):

Posterior Fossa ◽

Male Patient ◽

Cerebellar Vermis ◽

Cerebellar Hemisphere ◽

Cerebellar Hypoplasia ◽

Developmental Abnormalities ◽

Neuromuscular Abnormalities ◽

Left Cerebellar Hemisphere ◽

The Right ◽

Neuromotor Development

AbstractThe cerebellum abnormalities may be hypoplastic, dysplastic, or hypoplastic. It is very rare that the cerebellar hemisphere is affected unilaterally in the posterior fossa abnormalities. The reason for this effect is mostly sequela. This pathology presents with neuromotor developmental abnormalities. In this presentation, isolated left cerebellar hypoplasia is described radiologically in a 21-month-old male patient with neuromotor development defects. Dysplastic appearance was noticeable in the observable part of the left cerebellar hemisphere and folia. The cerebellar vermis could not be shaped. The right cerebellar hemisphere, other posterior fossa formations, and supratentorial area were natural. In patients with neuromuscular abnormalities, the posterior fossa is applied with care. It should be remembered that cerebellar hypoplasia and dysplasia can be unilateral.

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Thrombosis of a Drainage Vein in Developmental Venous Anomaly (DVA) Leading Venous Infarction: A Case Report and Review of the Literature

Journal of Neuroimaging ◽

10.1111/j.1552-6569.2009.00399.x ◽

2011 ◽

Vol 21 (2) ◽

pp. 197-201 ◽

Cited By ~ 13

Author(s):

Yilmaz Kiroglu ◽

Ismail Oran ◽

Tayfun Dalbasti ◽

Nevzat Karabulut ◽

Cem Calli

Keyword(s):

Case Report ◽

Developmental Venous Anomaly ◽

Venous Anomaly ◽

Review Of The Literature ◽

Venous Infarction ◽

Drainage Vein

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Developmental Venous Anomaly Complicated by Cerebral Venous Infarction

Radiology Case Reports ◽

10.2484/rcr.v2i4.48 ◽

2007 ◽

Vol 2 (4) ◽

Cited By ~ 1

Author(s):

Brian J. Parker ◽

Brian J. Sabb

Keyword(s):

Developmental Venous Anomaly ◽

Venous Anomaly ◽

Venous Infarction

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A rare combination of a developmental venous anomaly with a varix

Journal of Neurosurgery Pediatrics ◽

10.3171/ped/2008/1/2/156 ◽

2008 ◽

Vol 1 (2) ◽

pp. 156-159 ◽

Cited By ~ 8

Author(s):

Sait Sirin ◽

Serdar Kahraman ◽

Selcuk Gocmen ◽

Ersin Erdogan

Keyword(s):

Surgical Intervention ◽

Cavernous Malformation ◽

Vascular Anomaly ◽

Venous Drainage ◽

Magnetic Resonance Images ◽

Developmental Venous Anomaly ◽

Venous Anomaly ◽

Computed Tomography Scans ◽

The Brain

✓The most common vascular anomaly associated with a developmental venous anomaly (DVA) is a cavernous malformation. A cerebral DVA is a rare vascular malformation of the brain when it is associated with a varix. The authors report on a 13-year-old girl who presented with 2 brief episodes of nonresponsiveness that mimicked absence seizures. The computed tomography scans, magnetic resonance images, and cerebral angiograms showed a left temporal DVA in combination with a sylvian fissure varix. To maintain normal parenchymal venous drainage, no surgical intervention was performed. Radiological and clinical follow-up was planned. This case report expands the present knowledge of the rare association of a cerebral DVA with a varix and emphasizes the need for meticulous neuroimaging to avoid unnecessary surgery.

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Posterior fossa gangliocytoma with facial nerve invasion: case report

Arquivos de Neuro-Psiquiatria ◽

10.1590/s0004-282x2003000200022 ◽

2003 ◽

Vol 61 (2A) ◽

pp. 274-276 ◽

Cited By ~ 6

Author(s):

Andrei Koerbel ◽

Daniel Monte-Serrat Prevedello ◽

Cláudio Esteves Tatsui ◽

Luciano Pellegrino ◽

Ricardo Alexandre Hanel ◽

...

Keyword(s):

Case Report ◽

Facial Nerve ◽

Posterior Fossa ◽

Cerebellar Hemisphere ◽

Facial Paresis ◽

Direct Extension ◽

Nerve Invasion ◽

Nerve Paresis ◽

The Right ◽

Diffuse Lesion

A 5 year-old boy with a cerebellar gangliocytoma with a peripheral right facial paresis and ataxia is presented. His MRI showed a heterogenous, diffuse lesion, isointense on T1 and hyperintense on T2-weigthed sequences, involving the right cerebellar hemisphere with direct extension into the right facial nerve. The present case is the first description of a gangliocytoma with direct facial nerve invasion, as demonstrated for the facial nerve paresis and supported by MRI and surgical inspection.

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Papilloedema, an unusual complication of mastoidectomy

The Journal of Laryngology & Otology ◽

10.1017/s0022215100135224 ◽

1996 ◽

Vol 110 (9) ◽

pp. 878-880 ◽

Cited By ~ 2

Author(s):

P. Harkness ◽

R. Dossetor ◽

J. Weighill

Keyword(s):

At Risk ◽

Unusual Case ◽

Drainage System ◽

Venous Drainage ◽

Unusual Complication ◽

Partial Occlusion ◽

Cortical Mastoidectomy ◽

Decompression Procedure ◽

The Right ◽

Intra Cranial Pressure

AbstractWe report a very unusual case of a patient with a previously undiagnosed congenital absence of the left dural venous drainage system and a prominent system on the right. Due to its prominence it was at risk during a cortical mastoidectomy performed as part of an endolymphatic sac decompression procedure. Manipulation of the lateral venous sinus resulted in partial occlusion of the already compromised venous drainage. The result was a rise in intra-cranial pressure and papilloedema, from which the patient recovered. The abnormality was only detected on post-operative imaging.

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