Bicornuate Uterus with Incomplete Vaginal Septum and Unilateral Renal Agenesis

Radiology ◽  
1979 ◽  
Vol 133 (2) ◽  
pp. 455-457 ◽  
Author(s):  
Lewis Shenker ◽  
Fred E. Brickman
Keyword(s):  
Renal Agenesis ◽  
Vaginal Septum ◽  
Unilateral Renal Agenesis ◽  
Bicornuate Uterus

scholarly journals Transverse vaginal septum with menouria and unilateral renal agenesis-case report

Gynecology ◽  
2015 ◽  
Vol 3 (1) ◽  
pp. 1
Author(s):  
Baafuor Kofi Opoku ◽  
Richard Owusu Kwarteng ◽  
Philip Agyeman Prempeh
Keyword(s):  
Case Report ◽  
Renal Agenesis ◽  
Vaginal Septum ◽  
Unilateral Renal Agenesis ◽  
Transverse Vaginal Septum

Unilateral Renal Agenesis Associated with Bicornuate Uterus

1988 ◽  
Vol 43 (6) ◽  
pp. 352-355
Author(s):  
Teruhiro Nakada ◽  
Takashi Katayama ◽  
Jun Shimazaki
Keyword(s):  
Renal Agenesis ◽  
Unilateral Renal Agenesis ◽  
Bicornuate Uterus

Exstrophy of Bladder Associated with Unilateral Renal Agenesis and Bicornuate Uterus: A Case Report

2001 ◽  
Vol 12 (6) ◽  
pp. 410-411 ◽  
Author(s):  
L. N. Dorairajan ◽  
G. Roby ◽  
S. Kumar ◽  
H. Singh ◽  
D. Gowri
Keyword(s):  
Case Report ◽  
Renal Agenesis ◽  
Unilateral Renal Agenesis ◽  
Bicornuate Uterus

scholarly journals The case number 506 of Mostyn Embrey Syndrome: Imaging Studies and Ethics of Naming Syndromes

2021 ◽  
Vol 4 (5) ◽  
pp. 01-17
Author(s):  
Aamir Jalal Al Mosawi
Keyword(s):  
Reproductive Tract ◽  
Renal Agenesis ◽  
Imaging Modality ◽  
Delayed Diagnosis ◽  
Female Reproductive Tract ◽  
Imaging Studies ◽  
Vaginal Septum ◽  
Unilateral Renal Agenesis ◽  
First Case ◽  
Case Number

Background: Mostyn Embrey syndrome is a rare disorder associated with unilateral renal agenesis and malformations of the female reproductive tract. Delayed diagnosis is associated with serious diagnostic difficulties that may lead to inappropriate management including harmful surgery. The aim of this paper is to present imaging studies of case number 506 of the syndrome which was the first case of this rare syndrome in Iraq, and was originally reported in 2016. Ethics of naming syndromes relevant to this syndrome is discussed. Patients and methods: An 18-year-old female presented with acute abdominal pain and poor urine output associated with retention of urine; about three years after the onset of menses. The pain was radiating to the back and pelvis. Her menstrual cycles started at the age of fifteen, and were lasting seven days. Cycles were associated with normal flow. The first physician the patient consulted considered the diagnosis of uterine tumor and the need for hysterectomy, but the family of the patient consultedanother physician. Vaginal exam was performed and showed bulging left vaginal wall. The diagnosis of hematocolpos was made. A clotted blood was drained by trans- vaginal approach. Results: It was difficult to identify the two separate uteri and two separate cervices and to make a diagnosis of didelphys uterus on hysterosalpingography. Abdominal MRI showed left renal agenesis, and two uterine bodies, cervices, and vaginas with normal myometrium and endometrium (uterine didelphys), and normal ovaries. Conclusions: It is recommended that pediatricians, and pediatric nephrologists need to be aware of this syndrome to avoid unexpected presentations which may lead to delayed diagnosis and sometimes to inappropriate management. The imaging modalities that can be used to diagnose Mostyn Embrey syndrome include ultrasonography, hysterosal pingography and MRI. In this case, hysterosal pingography was not of much help. Ultrasound is affordable, non-invasive, widely available imaging modality that contributes to the accurate diagnosis of Mostyn Embrey syndrome. However, there can be difficulties in visualizing the vaginal septum on ultrasound which best shown on MRI. MRI can facilitate early diagnosis and thus help in the prevention of further complications. Syndromes in medicine are often named after the physician or group of physicians that discovered them or initially provided the full clinical picture or the best description of the syndrome. Unfortunately, Mostyn Embrey syndromes has been attributed unfairly and inappropriately to physicians other that those first described them in almost all previous papers.

scholarly journals Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome Rare Obstructive Uterovaginal Anomaly: A Case Report

2020 ◽  
Vol 58 (230) ◽  
Author(s):  
Tulasa Basnet ◽  
Tarun Pradhan ◽  
Punita Yadav ◽  
Manoj Kumar Sah ◽  
Jyotsna Yadav ◽  
...  
Keyword(s):  
Renal Agenesis ◽  
Pelvic Mass ◽  
Vaginal Septum ◽  
Renal Anomaly ◽  
Unilateral Renal Agenesis ◽  
Obstructed Hemivagina ◽  
Specific Symptoms ◽  
Ovarian Abscess ◽  
Symptoms And Signs

Obstructed Hemivagina and Ipsilateral Renal Anomaly syndrome is a rare obstructive uterovaginal anomaly involving both mesonephric and paramesonephric ducts. It usually presents after menarche with non-specific symptoms like pelvic pain, dysmenorrhea, or paravaginal mass and examination findings of paravaginal or pelvic mass. Because of non-specific symptoms and signs, the diagnosis is usually overlooked, which leads to complications like endometriosis, tubo-ovarian abscess compromising patient’s fertility, and quality of life. Therefore, in presence of these nonspecific clinical features along with imaging findings of uterine didelphys and unilateral renal agenesis, this syndrome should be considered in the diagnosis. We present a case of a 17-year-old lady with Obstructed Hemivagina and Ipsilateral Renal Anomaly syndrome, diagnosed by finding of paravaginal mass on examination and uterine didelphys with ipsilateral renal agenesis in USG and managed successfully by resection of vaginal septum.    

scholarly journals Herlyn-Werner-Wunderlich Syndrome: A Case Report

2020 ◽  
Vol 18 (2) ◽  
pp. 70-73
Author(s):  
SM Saiful Islam
Keyword(s):  
Developmental Disorder ◽  
Renal Agenesis ◽  
Lower Abdominal Pain ◽  
Pediatric Emergency ◽  
Vaginal Opening ◽  
Vaginal Septum ◽  
Unilateral Renal Agenesis ◽  
Abdominal Mri ◽  
Obstructed Hemivagina ◽  
The Right

Herlyn-Werner-Wunderlich Syndrome (HWWS) is a rare developmental disorder of female urogenital tract consisting of paired uterus, obstructed hemivagina and unilateral renal agenesis. Here, authors described a case of a 10 years old girl with HWWS who presented to pediatric emergency with recurrent lower abdominal pain shortly following menstruation and dysmenorrhea. The diagnosis was confirmed by abdominal MRI. Examination under anesthesia revealed two vaginal opening, of which left is widely open and the right is completely closed with bulging hymen. A hymeneal incision was made with evacuation of the cavity. At present, the preferred surgical option is resection of as completely of the obstructing vaginal septum as possible and marsupialization for patients with completely obstructed hemivagina with blind hemivagina and incompletely obstructed hemivagina. The outcome of patients with HWWS is generally good with early detection of illness and prompt management. They can have normal sexual relations with preserved fertility. Chatt Maa Shi Hosp Med Coll J; Vol.18 (2); July 2019; Page 70-73

Renal Dysplasia with Unilateral Renal Agenesis in a Dog

2005 ◽  
Vol 133 (1) ◽  
pp. 64-67 ◽  
Author(s):  
T. Morita ◽  
Y. Michimae ◽  
M. Sawada ◽  
T. Uemura ◽  
Y. Araki ◽  
...  
Keyword(s):  
Renal Agenesis ◽  
Renal Dysplasia ◽  
Unilateral Renal Agenesis

Unilateral Renal Agenesis in 2 Siblings

2006 ◽  
Vol 47 (9) ◽  
pp. 1019 ◽  
Author(s):  
Yong Duk You ◽  
Kong Jo Kim ◽  
Hee Jo Yang ◽  
Hyun Ki Jo ◽  
Doo Sang Kim ◽  
...  
Keyword(s):  
Renal Agenesis ◽  
Unilateral Renal Agenesis
Sign in / Sign up

Export Citation Format

Share Document