scholarly journals Erosive Arthritis, Fibromatosis, and Keloids: A Rare Dermatoarthropathy

2018 ◽  
Vol 2018 ◽  
pp. 1-5
Author(s):  
Fawad Aslam ◽  
Jonathan A. Flug ◽  
Yousif Yonan ◽  
Shelley S. Noland
Keyword(s):  
Rare Disease ◽  
Peyronie’S Disease ◽  
Dupuytren’S Contracture ◽  
Erosive Arthritis ◽  
Dupuytren's Contracture ◽  
Rare Syndrome ◽  
Knuckle Pads ◽  
Peyronie's Disease ◽  
Plantar Fibromatosis ◽  
Palmar Fibromatosis

Polyfibromatosis is a rare disease characterized by fibrosis manifesting in different locations. It is commonly characterized by palmar fibromatosis (Dupuytren’s contracture) in variable combinations with plantar fibromatosis (Ledderhose’s disease), penile fibromatosis (Peyronie’s disease), knuckle pads, and keloids. There are only three reported cases of polyfibromatosis and keloids with erosive arthritis. We report one such case and review the existing literature on this rare syndrome.

Palmar fibromatosis (Dupuytren's contracture)

1984 ◽  
Vol 405 (1) ◽  
pp. 41-53 ◽  
Author(s):  
H. Iwasaki ◽  
H. M�ller ◽  
H. J. Stutte ◽  
U. Brennscheidt
Keyword(s):  
Dupuytren’S Contracture ◽  
Dupuytren's Contracture ◽  
Palmar Fibromatosis

Dupuytren’s Contracture: An Update of Biomolecular Aspects and Therapeutic Perspectives

2005 ◽  
Vol 30 (6) ◽  
pp. 557-562 ◽  
Author(s):  
A. CORDOVA ◽  
M. TRIPOLI ◽  
B. CORRADINO ◽  
P. NAPOLI ◽  
F. MOSCHELLA
Keyword(s):  
Extracellular Matrix ◽  
Surgical Excision ◽  
Dupuytren’S Contracture ◽  
Palmar Fascia ◽  
Dupuytren's Disease ◽  
The Real ◽  
Practical Applications ◽  
Dupuytren's Contracture ◽  
Palmar Fibromatosis

The so-called fibrogenic cytokines, able to induce the growth of fibroblasts and their differentiation into myofibroblasts and to stimulate their production of extracellular matrix, are involved in the genesis of Dupuytren’s contracture. Although many studies have been made of biomolecular aspects of palmar fibromatosis, practical applications from them are still far from imminent because of the real difficulty of blocking their action in vivo, even in a chronic, progressive lesion such as Dupuytren’s disease. Consequently, surgical excision of the palmar fascia still remains the treatment of choice.

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