Airway-Centered Pleuroparenchymal Fibroelastosis Associated with Non-Necrotizing Granulomas: A Rare New Entity

Pathobiology ◽  
2018 ◽  
Vol 85 (5-6) ◽  
pp. 276-279 ◽  
Author(s):  
Elena Bargagli ◽  
Paola Rottoli ◽  
Elena Torricelli ◽  
Chiara Allegrini ◽  
Alessandra Dubini ◽  
...  
Keyword(s):  
Pleuroparenchymal Fibroelastosis ◽  
Necrotizing Granulomas

Pleuroparenchymal Fibroelastosis: Associations and Underlying Conditions

2014 ◽  
Vol 9 (4) ◽  
pp. 248-253 ◽  
Author(s):  
Farnoosh Tayyari ◽  
Tae-Bong Chung ◽  
David Hwang
Keyword(s):  
Pleuroparenchymal Fibroelastosis

scholarly journals Pleuroparenchymal fibroelastosis as a manifestation of chronic lung rejection?

2012 ◽  
Vol 41 (1) ◽  
pp. 243-245 ◽  
Author(s):  
T. Hirota ◽  
M. Fujita ◽  
T. Matsumoto ◽  
T. Higuchi ◽  
T. Shiraishi ◽  
...  
Keyword(s):  
Pleuroparenchymal Fibroelastosis

Prognostic role of KL‐6 in SSc‐ILD patients with pleuroparenchymal fibroelastosis

2021 ◽  
Author(s):  
Miriana d’Alessandro ◽  
Francesca Bellisai ◽  
Laura Bergantini ◽  
Paolo Cameli ◽  
Roberto D’Alessandro ◽  
...  
Keyword(s):  
Prognostic Role ◽  
Pleuroparenchymal Fibroelastosis

scholarly journals Severe and progressive platythorax disproportionate to lung fibrosis: A rare variant of idiopathic pleuroparenchymal fibroelastosis

2021 ◽  
pp. 101395
Author(s):  
Takato Ikeda ◽  
Yoshiaki Kinoshita ◽  
Yusuke Ueda ◽  
Tomoya Sasaki ◽  
Hisako Kushima ◽  
...  
Keyword(s):  
Rare Variant ◽  
Lung Fibrosis ◽  
Pleuroparenchymal Fibroelastosis

Pleuroparenchymal Fibroelastosis of the Lung: A Review

2016 ◽  
Vol 140 (8) ◽  
pp. 849-853 ◽  
Author(s):  
Shaun Kian Hong Cheng ◽  
Khoon Leong Chuah
Keyword(s):  
Bone Marrow ◽  
Bone Marrow Transplantation ◽  
Rare Disease ◽  
Marrow Transplantation ◽  
Lung Parenchyma ◽  
Current Understanding ◽  
Pleuroparenchymal Fibroelastosis ◽  
Pathologic Features ◽  
English Speaking ◽  
English Speaking World

Described in Japan by Amitani et al in 1992, the entity of idiopathic upper lobe fibrosis was subsequently given the name pleuroparenchymal fibroelastosis (PPFE) in the English-speaking world. Pleuroparenchymal fibroelastosis is believed to be a rare disease characterized by a fibrosing process affecting the pleura and the subpleural lung parenchyma, with a predilection for the upper lobes. Uniquely, the fibrosing process is elastotic in nature, being associated with intra-alveolar fibrosis. The etiology of PPFE is unclear at this juncture, with many cases being considered as idiopathic forms of the disease. Conditions associated with PPFE include infections, bone marrow transplantation, and autoimmunity. In this review, we explore the clinical, radiologic, and pathologic features associated with PPFE in light of current understanding of the disease. Recent studies implicated that PPFE may not be as uncommon as claimed. The various differential diagnoses and implications of diagnosing PPFE are discussed.

scholarly journals Clinical diagnosis of idiopathic pleuroparenchymal fibroelastosis: A retrospective multicenter study

2017 ◽  
Vol 133 ◽  
pp. 1-5 ◽  
Author(s):  
Yasunori Enomoto ◽  
Yutaro Nakamura ◽  
Yasuomi Satake ◽  
Hiromitsu Sumikawa ◽  
Takeshi Johkoh ◽  
...  
Keyword(s):  
Clinical Diagnosis ◽  
Multicenter Study ◽  
Pleuroparenchymal Fibroelastosis ◽  
Retrospective Multicenter Study

Heterogeneous clinical features in patients with pulmonary fibrosis showing histology of pleuroparenchymal fibroelastosis

2016 ◽  
Vol 54 (3) ◽  
pp. 162-169 ◽  
Author(s):  
Yuji Yoshida ◽  
Nobuhiko Nagata ◽  
Nobuko Tsuruta ◽  
Yasuhiko Kitasato ◽  
Kentaro Wakamatsu ◽  
...  
Keyword(s):  
Pulmonary Fibrosis ◽  
Clinical Features ◽  
Pleuroparenchymal Fibroelastosis

Pleuroparenchymal fibroelastosis with prominent thrombosis

2016 ◽  
Vol 67 (1) ◽  
pp. 56-58
Author(s):  
Kimberly van der Oord ◽  
Heleen Rietema ◽  
Jan H. von der Thusen ◽  
Eric Thunnissen
Keyword(s):  
Pleuroparenchymal Fibroelastosis

scholarly journals Pleuroparenchymal fibroelastosis as a late complication of chemotherapy agents

2014 ◽  
Vol 44 (2) ◽  
pp. 523-527 ◽  
Author(s):  
C. Beynat-Mouterde ◽  
G. Beltramo ◽  
G. Lezmi ◽  
D. Pernet ◽  
C. Camus ◽  
...  
Keyword(s):  
Late Complication ◽  
Pleuroparenchymal Fibroelastosis ◽  
Chemotherapy Agents
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