Clinical Characteristics and Outcomes in Adult Cystic Fibrosis Patients with Severe Lung Disease in Southern Brazil

Clinical characteristics and outcomes in adult cystic fibrosis patients with severe lung disease in Porto Alegre, southern Brazil

BMC Pulmonary Medicine ◽

10.1186/s12890-020-01223-6 ◽

2020 ◽

Vol 20 (1) ◽

Author(s):

Guilherme Figueiredo Silva ◽

Nicholas J. Simmonds ◽

Paulo de Tarso Roth Dalcin

Keyword(s):

Cystic Fibrosis ◽

Lung Disease ◽

Clinical Characteristics ◽

Southern Brazil ◽

Porto Alegre ◽

Severe Lung Disease ◽

Faculty Opinions recommendation of Effects of ivacaftor in patients with cystic fibrosis who carry the G551D mutation and have severe lung disease.

Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature ◽

10.3410/f.718276081.793491279 ◽

2014 ◽

Author(s):

James Chmiel ◽

Danielle Goetz

Keyword(s):

Cystic Fibrosis ◽

Lung Disease ◽

Severe Lung Disease ◽

P039 The clinical impact of triple CFTR modulator therapy in a cohort of people with cystic fibrosis and severe lung disease

10.1016/s1569-1993(21)01066-3 ◽

2021 ◽

Vol 20 ◽

pp. S50

Author(s):

O. Fanthorpe ◽

S. Caskey ◽

D.G. Downey

Keyword(s):

Cystic Fibrosis ◽

Lung Disease ◽

Clinical Impact ◽

Severe Lung Disease ◽

The use of ivacaftor in an adult with severe lung disease due to cystic fibrosis (ΔF508/G551D)

10.1016/j.jcf.2012.12.004 ◽

2013 ◽

Vol 12 (5) ◽

pp. 530-531 ◽

Cited By ~ 13

Author(s):

Hari M. Polenakovik ◽

Bradley Sanville

Keyword(s):

Cystic Fibrosis ◽

Lung Disease ◽

Severe Lung Disease ◽

P209 Use of lumacaftor/ivacaftor as rescue therapy and stabilisation treatment for severe lung disease in children with cystic fibrosis

10.1016/s1569-1993(19)30502-8 ◽

2019 ◽

Vol 18 ◽

pp. S116

Author(s):

L. Everitt ◽

G. Connett ◽

A. Dewar ◽

W. Verling

Keyword(s):

Cystic Fibrosis ◽

Lung Disease ◽

Rescue Therapy ◽

Severe Lung Disease ◽

P255 Clinical stabilisation following ivacaftor in patients with cystic fibrosis, severe lung disease and rare CFTR mutation: a report of two cases

10.1016/s1569-1993(19)30548-x ◽

2019 ◽

Vol 18 ◽

pp. S129

Author(s):

G. Spoletini ◽

N. Shaw ◽

C. Etherington ◽

I. Clifton ◽

P. Whitaker ◽

...

Keyword(s):

Cystic Fibrosis ◽

Lung Disease ◽

Severe Lung Disease ◽

Association of chronicCandida albicansrespiratory infection with a more severe lung disease in patients with cystic fibrosis

Pediatric Pulmonology ◽

10.1002/ppul.23302 ◽

2015 ◽

Vol 50 (11) ◽

pp. 1082-1089 ◽

Cited By ~ 22

Author(s):

Alex Gileles-Hillel ◽

David Shoseyov ◽

Itzhack Polacheck ◽

Maya Korem ◽

Eitan Kerem ◽

...

Keyword(s):

Cystic Fibrosis ◽

Lung Disease ◽

Severe Lung Disease ◽

A multicentre, observational cohort study to determine the efficacy and safety of lumacaftor/ivacaftor in patients with severe lung disease and cystic fibrosis

10.1183/13993003.congress-2019.oa2126 ◽

2019 ◽

Author(s):

Koliarne Tong ◽

Douglas Dorahy ◽

Megan France ◽

Lucy Burr ◽

Hugh Greville ◽

...

Keyword(s):

Cystic Fibrosis ◽

Cohort Study ◽

Lung Disease ◽

Observational Cohort Study ◽

Efficacy And Safety ◽

Observational Cohort ◽

Severe Lung Disease ◽

Sleep quality and daytime function in adults with cystic fibrosis and severe lung disease

European Respiratory Journal ◽

10.1183/09031936.02.00088702 ◽

2002 ◽

Vol 19 (3) ◽

pp. 504-510 ◽

Cited By ~ 59

Author(s):

D.R. Dancey ◽

E.D. Tullis ◽

R. Heslegrave ◽

K. Thornley ◽

P.J. Hanly

Keyword(s):

Cystic Fibrosis ◽

Sleep Quality ◽

Lung Disease ◽

Daytime Function ◽

Severe Lung Disease ◽

Effect of low altitude at the Dead Sea on exercise capacity and cardiopulmonary response to exercise in cystic fibrosis patients with moderate to severe lung disease

Pediatric Pulmonology ◽

10.1002/ppul.20342 ◽

2006 ◽

Vol 41 (3) ◽

pp. 234-241 ◽

Cited By ~ 17

Author(s):

Bareket Falk ◽

Asaph Nini ◽

Levana Zigel ◽

Yaacov Yahav ◽

Micha Aviram ◽

...

Keyword(s):

Cystic Fibrosis ◽

Lung Disease ◽

Exercise Capacity ◽

Dead Sea ◽

Low Altitude ◽

The Dead ◽

Response To Exercise ◽

Severe Lung Disease ◽