Temporal Bone Histopathology of Osteopetrosis

1976 ◽  
Vol 85 (1) ◽  
pp. 15-24 ◽  
Author(s):  
Fumiro Suga ◽  
John R. Lindsay

The histopathology of the temporal bone of an eight and one-half-year-old girl with osteopetrosis (Albers-Schönberg disease) was studied to evaluate the pathogenesis of its frequent complications in hearing and facial nerve function. The patient was blind and had acute otitis media, but facial paralysis was not noted. Although the size of the temporal bone pyramid was markedly increased due to enormously thickened periosteal layer, changes in the endosteal and endochondral layers were less marked. Exostotic growth of periosteal bone was seen in the middle ear wall, and the tympanic cavity appeared to be narrowed. At the oval window region, the facial nerve was pushed down towards the stapes due to extreme overgrowth of periosteal bone of the epitympanum, and the superstructure of the stapes was imbedded deeply into the dislocated facial nerve and had strongly compressed it. Although the footplate was free from ankylosis, the crus of the stapes appeared to be immobilized because it was lodged in the facial nerve. Such changes appeared to be the pathogenesis of one form of facial nerve paralysis and conductive hearing loss associated with osteopetrosis.

2015 ◽  
Vol 4 (1) ◽  
Author(s):  
Jacky Munilson ◽  
Yan Edward ◽  
Dedy Rusdi

AbstrakPendahuluan: Paralisis saraf fasialis merupakan salah satu komplikasi fraktur tulang temporal. Fraktur tulang temporal dapat berupa fraktur longitudinal, transversal maupun campuran. Paralisis saraf fasialis lebih banyak ditemukan pada fraktur tulang transversal dibandingkan longitudinal. Penatalaksanaan paralisis saraf fasialis akibat fraktur tulang temporal masih kontroversi, dapat berupa terapi medikamentosa maupun terapi bedah. Metode: Satu kasus paralisis saraf fasialis akibat fraktur temporal longitudinal tahun yang ditatalaksana dengan terapi medikamentosa. Hasil: Terdapat peningkatan fungsi saraf pasialis dengan terapi medikamentosa pada paralisis parsial saraf fasialis akibat fraktur temporal longitudinal. Diskusi: Penatalaksanaan paralisis saraf fasialis akibat fraktur tulang temporal masih merupakan hal yang kontroversial. Pasien dengan paralisis parsial (House Brackmann II-V) cukup dilakukan observasi dan terapi dengan steroid berupa prednison, sedangkan pada paralisis komplit (House Brackmann VI), terapi medikamentosa dengan steroid dapat dikombinasikan dengan terapi bedah berupa dekompresi atau grafting. Pertimbangan untuk melakukan pembedahan tergantung dari pemeriksaan CT Scan dan tes elektrofisiologisKata kunci: Paralisis saraf fasialis, fraktur tulang temporal, terapi medikamentosaAbstractFacial nerve paralysis is one of the temporal bone fracture complications. Temporal bone fracture is classified as longitudinal, transversal and mixed type. Facial nerve paralysis is more common in transversal rather than longitudinal type. The treatment of facial nerve paralysis due to temporal bone fracture still remain controversial, whether its medical therapy or surgical approach.Methode: One case of facial nerve paralysis caused by longitudinal type of temporal bone fracture has been treated by medical therapy. Result: There is an increase of facial nerve function treated with medical therapy in a case of partial nerve paralysis due to longitudinal type of temporal bone fracture. Discussion: Management of facial nerve paralysis due to temporal bone fracture is still controversial. Patient with partial paralysis (House Brackmann II-V) treated with observation and medical therapy using steroid, whereas complete paralysis (House Brackmann VI) treated with medical therapy using steroid, combine with decompression and grafting surgery. Considerations for surgery depend on computed tomography and electrophysiology examination.Keywords: Facial nerve paralysis, temporal bone fracture, medical therapy


2018 ◽  
Vol 132 (10) ◽  
pp. 885-890
Author(s):  
L Zhao ◽  
J Li ◽  
S Gong

AbstractObjectiveTo evaluate the therapeutic effect that the titanium partial ossicular reconstruction prosthesis and autologous ossicles have on hearing loss after reconstruction of a damaged ossicular chain.MethodsForty-two medical records of treatments carried out from 2013 to 2015 for ossicular chain damage with facial nerve paralysis due to temporal bone fractures were reviewed. The study assessed: causes of damage, pre-operative pure tone audiometry findings, types of intra-operative ossicular chain damage, intra-operative ossicular chain repair methods (titanium partial ossicular reconstruction prosthesis or autologous ossicles) and post-operative pure tone audiometry results.ResultsThe titanium partial ossicular reconstruction prosthesis was used in 26 cases; the average air–bone gap was 32.3 ± 5.3 dB pre-operatively and 12.8 ± 5.3 dB post-operatively. Autologous ossicles were used in 16 cases; the average air–bone gap was 33.4 ± 4.5 dB pre-operatively and 17.8 ± 7.8 dB post-operatively.ConclusionOssicular chain reconstruction is an effective way of improving hearing in patients with ossicular chain damage. The results suggest that repair with either the titanium partial ossicular reconstruction prosthesis or autologous ossicles can improve hearing following ossicular chain injury with facial nerve paralysis caused by a temporal bone fracture.


2004 ◽  
Vol 40 (8) ◽  
pp. 483-486 ◽  
Author(s):  
E Gaio ◽  
G Marioni ◽  
C de Filippis ◽  
A Tregnaghi ◽  
S Caltran ◽  
...  

2021 ◽  
pp. 40-40
Author(s):  
Zoran Dudvarski ◽  
Nenad Arsovic ◽  
Milovan Dimitrijevic ◽  
Sasa Jakovljevic ◽  
Novica Boricic ◽  
...  

Introduction. Late metastases of malignant tumors in the temporal bone are very rare lesions. They can be asymptomatic for a long time, and usually manifest themselves in the form of hearing loss, dizziness, tinnitus, and paralysis of the facial nerve. Modern radiological diagnostics and explorative surgery with biopsy are essential for diagnosis. Case report. We present a rare and unusual case of a 66-year-old female patient with a facial nerve paralysis that appeared as the first sign of metastatic breast cancer in the temporal bone 10 years after treatment. A sudden hearing loss and dizziness occurred six months later and value of CA 15-3 was elevated. Scintigraphy pointed to susceptible metastatic deposits of the axial skeleton, without lesions in the temporal bone. Finally, repeated computerized tomography revealed osteolytic changes of the temporal bone six months after that. Immunohistochemical analysis of mastoid tissue samples confirmed that it was a breast cancer metastasis. One year after palliative radiotherapy and oral hormone therapy, a patient has a good general condition with better function of the facial nerve. Conclusion. A high degree of clinical suspicion sometimes requires repeated radiological diagnostics in order to detect osteolytic metastatic changes in the temporal bone, but also in other bone structures within the hematogenous dissemination of the malignant disease.


2020 ◽  
Vol 19 (5) ◽  
pp. 502-509
Author(s):  
Alexander V Zotov ◽  
Jamil A Rzaev ◽  
Sergey V Chernov ◽  
Alexander B Dmitriev ◽  
Anton V Kalinovsky ◽  
...  

Abstract BACKGROUND Facial nerve paralysis (FP) is a possible complication of cerebellopontine angle tumor surgery. Several donor nerves have been used in the past for facial reanimation. We report the results of 30 cases of masseter-to-facial anastomosis. OBJECTIVE To prospectively evaluate the efficacy of V to VII anastomosis after FP. METHODS In a prospective study, we included 30 consecutive patients with FP (20 women and 10 men) whose mean age was 48.8 yr (32-76 yr). In almost all cases, FP developed after cerebellopontine angle tumor surgery (29 patients), whereas in one case, FP occurred after skull base trauma. Pre- and postoperative evaluation of facial nerve function was performed using the House-Brackmann (HB) scale and the Sokolovsky scale, as well as by electromyography. Follow-up ranged from 11 to 51 mo and averaged 22 mo. RESULTS All patients achieved functional recovery of the facial nerve from VI to either III or IV HB degree. Patients with short time FP showed significantly better postoperative recovery. CONCLUSION The results of the V to VII anastomosis demonstrate a significant improvement of facial nerve function and virtually no complications.


Open Medicine ◽  
2014 ◽  
Vol 9 (2) ◽  
pp. 226-230
Author(s):  
Ljiljana Vlaški ◽  
Nada Vučković ◽  
Danijela Dragičević ◽  
Vladimir Kljajić ◽  
Slavica Seničar

Abstract


Sign in / Sign up

Export Citation Format

Share Document