Fibrous Dysplasia of the Temporal Bone Presenting With Facial Nerve Palsy and Conductive Hearing Loss

The case of a five year old boy who presented with a lower motor neurone facial nerve palsy secondary to primary non-Hodgkin’s lymphoma (NHL) of the middle ear is discussed. Any child who presents with a facial nerve palsy and conductive hearing loss requires thorough evaluation to exclude the possibility of temporal bone malignancy.

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Hearing loss

10.1093/med/9780199568741.003.0051 ◽

2018 ◽

Author(s):

James Ramsden

Keyword(s):

Hearing Loss ◽

Facial Nerve ◽

Middle Ear ◽

Cranial Nerve ◽

Nerve Palsy ◽

Facial Nerve Palsy ◽

Conductive Hearing Loss ◽

Ear Canal ◽

Eighth Cranial Nerve ◽

Conductive Hearing

Hearing loss must be divided into conductive hearing loss (CHL) and sensorineural hearing loss (SNHL). CHL is caused by sound not reaching the cochlear (abnormality of the ear canal, tympanic membrane, middle ear, or ossicles), whereas SNHL is a condition affecting the cochlear or auditory (eighth cranial) nerve. Hearing loss may be accompanied by other cardinal signs of ear disease, such as pain or discharge from the ear, vertigo, facial nerve palsy, and tinnitus, which guide the diagnosis. This chapter describes the approach to the patient with hearing loss.

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Double Intratemporal Congenital Cholesteatomas Combined with Ossicular Anomalies

Annals of Otology Rhinology & Laryngology ◽

10.1177/000348948609500415 ◽

1986 ◽

Vol 95 (4) ◽

pp. 401-403 ◽

Cited By ~ 9

Author(s):

Tsun-Sheng Huang

Keyword(s):

Hearing Loss ◽

Early Detection ◽

Temporal Bone ◽

Nerve Palsy ◽

Surgical Intervention ◽

Facial Nerve Palsy ◽

Conductive Hearing Loss ◽

The Other ◽

Presenting Symptoms ◽

Conductive Hearing

A 15-year-old patient had unilateral double congenital cholesteatomas, one isolated to the mastoid and the other located in the petrous pyramid. The presenting symptoms were facial palsy and a conductive hearing loss on the affected side. The case is interesting, not only in that there were two isolated cholesteatomas in the same temporal bone, but also because of the combination of ossicular anomalies. The unusually early detection and surgical intervention in this instance suggest that similar cases of multicentric cholesteatomas may have occurred, but may have been concealed because of the later detection and possible linkage of the cholesteatomas. I would therefore emphasize Sheehy's recommendation that temporal bone radiography never be omitted where idiopathic facial nerve palsy exists.

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Neglected keratosis obturans causing facial nerve palsy

The Journal of Laryngology & Otology ◽

10.1017/s0022215106001137 ◽

2006 ◽

Vol 120 (9) ◽

pp. 784-785 ◽

Cited By ~ 9

Author(s):

F Glynn ◽

I J Keogh ◽

H Burns

Keyword(s):

Hearing Loss ◽

Facial Nerve ◽

External Auditory Canal ◽

Nerve Palsy ◽

Facial Nerve Palsy ◽

Conductive Hearing Loss ◽

Conductive Hearing

Keratosis obturans is characterized by the accumulation of desquamated keratinous material in the bony portion of the external auditory canal. Classically, it is reported to present with severe otalgia, conductive hearing loss and global widening of the external auditory canal. Extensive erosion of the bony meatus, with exposure of the facial nerve, has been previously reported, but no case of facial nerve palsy has as yet been published. We report the first published case, to our knowledge, of a unilateral facial nerve palsy secondary to neglected keratosis obturans.

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TEMPORAL BONE FRACTURES: THREE IDENTICAL CASES OF LATERAL MIDDLE EAR FRACTURES WITH FACIAL NERVE INJURY AND CONDUCTIVE HEARING LOSS

The Laryngoscope ◽

10.1288/00005537-197304000-00014 ◽

1973 ◽

Vol 83 (4) ◽

pp. 587-593

Author(s):

James R. Leonard ◽

Mark L. Belafsky

Keyword(s):

Hearing Loss ◽

Facial Nerve ◽

Temporal Bone ◽

Nerve Injury ◽

Middle Ear ◽

Conductive Hearing Loss ◽

Bone Fractures ◽

Facial Nerve Injury ◽

Conductive Hearing

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Congenital internal auditory canal stenosis

The Journal of Laryngology & Otology ◽

10.1258/002221503770716205 ◽

2003 ◽

Vol 117 (10) ◽

pp. 784-787 ◽

Cited By ~ 20

Author(s):

Seung Kuk Baek ◽

Sung Won Chae ◽

Hak Hyun Jung

Keyword(s):

Hearing Loss ◽

High Resolution ◽

Facial Nerve ◽

Ct Scan ◽

Sensorineural Hearing Loss ◽

Temporal Bone ◽

Nerve Palsy ◽

Facial Nerve Palsy ◽

Internal Auditory Canal ◽

Canal Stenosis

Congenital internal auditory canal stenosis is a rare cause of sensorineural hearing loss in children. A retrospective analysis including clinical manifestation and radiological findings was made for seven patients who were diagnosed with congenital internal auditory canal stenosis from 1996 to 2002. Chief presenting symptoms were hearing loss, facial nerve palsy, dizziness, and tinnitus. Hearing loss including deafness was found in five cases, vestibular function loss in four cases, and profound functional loss of facial nerve in two cases. In all cases, the diameter of the internal auditory canal was less than 2 mm on high-resolution temporal bone computed tomography (CT) scan. Two cases revealed bilateral internal auditory canal stenosis, and others were unilaterally involved cases. Congenital internal auditory canal stenosis can be an important cause of sensorineural hearing loss, facial nerve palsy, and vestibular dysfunction. High resolution temporal bone CT scan and magnetic resonance (MR) imaging were important tools for diagnosis.

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Facial nerve palsy as the presenting feature of metastatic prostatic cancer in the temporal bone

Acta Oto-Laryngologica Case Reports ◽

10.1080/23772484.2020.1865165 ◽

2020 ◽

Vol 6 (1) ◽

pp. 1-5

Author(s):

Daichi Fujii ◽

Hikari Shimoda ◽

Natsumi Uehara ◽

Takeshi Fujita ◽

Masanori Teshima ◽

...

Keyword(s):

Facial Nerve ◽

Temporal Bone ◽

Prostatic Cancer ◽

Nerve Palsy ◽

Facial Nerve Palsy ◽

Metastatic Prostatic Cancer

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Bilateral Temporal Bone Fractures with Bilateral Facial Nerve Palsy

Indian Journal of Neurotrauma ◽

10.1055/s-0036-1597749 ◽

2016 ◽

Vol 13 (03) ◽

pp. 168-170

Author(s):

Kanjully Sabarigirish ◽

Sanjeev Saxena ◽

Himanshu Swami ◽

Angshuman Dutta ◽

Lohith BR

Keyword(s):

Facial Nerve ◽

Temporal Bone ◽

Nerve Palsy ◽

Facial Nerve Palsy ◽

Bone Fractures

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Concomitant Dehiscences of the Temporal Bone: A Case-Based Study

Ear Nose & Throat Journal ◽

10.1177/0145561320973782 ◽

2020 ◽

pp. 014556132097378

Author(s):

Maurizio Barbara ◽

Valerio Margani ◽

Anna Voltattorni ◽

Simonetta Monini ◽

Edoardo Covelli

Keyword(s):

Hearing Loss ◽

Inner Ear ◽

Temporal Bone ◽

Conductive Hearing Loss ◽

Acoustic Energy ◽

Superior Semicircular Canal Dehiscence ◽

Local Bone ◽

Tegmen Tympani ◽

Vestibular Symptoms ◽

Conductive Hearing

Otic capsule dehiscences create a pathological third window in the inner ear that results in a dissipation of the acoustic energy consequent to the lowered impedance. Superior semicircular canal dehiscence (SSCD) was identified by Minor et al in 1998 as a syndrome leading to vertigo and inner ear conductive hearing loss. The authors also reported the relation between the dehiscence and pressure- or sound-induced vertigo (Tullio’s phenomenon). Prevalence rates of SSCD in anatomical studies range from 0.4% to 0.7% with a majority of patients being asymptomatic. The observed association with other temporal bone dehiscences, as well as the propensity toward a bilateral or contralateral “near dehiscence,” raises the question of whether a specific local bone demineralization or systemic mechanisms could be considered. The present report regard a case of a patient with a previous episode of meningitis, with a concomitant bilateral SSCD and tegmen tympani dehiscence from the side of meningitis. The patient was affected by dizziness, left moderate conductive hearing loss, and pressure/sound-induced vertigo. Because of disabling vestibular symptoms, the patient underwent surgical treatment. A middle cranial fossa approach allowed to reach both dehiscences on the symptomatic side, where bone wax and fascia were used for repair. At 6 months from the procedure, hearing was preserved, and the vestibular symptoms disappeared.

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