Surgical treatment of tetralogy of Fallot with absent pulmonary valve syndrome

2015 ◽  
Vol 24 (5) ◽  
pp. 470-472
Author(s):  
Yuki Tanaka ◽  
Takashi Miyamoto ◽  
Yuji Naito ◽  
Shuichi Yoshitake
2001 ◽  
Vol 11 (6) ◽  
pp. 673-675
Author(s):  
Kazuhiro Takahashi ◽  
Takashi Kuwahara ◽  
Masayoshi Nagatsu

A newborn infant with tetralogy of Fallot and absent pulmonary valve was successfully corrected in two stages. Absent pulmonary valve syndrome presenting in early infancy manifests severe respiratory symptoms that still make challenging both management and surgical treatment. This is ascribed to tracheobronchial compression by the extremely dilated pulmonary arteries, and to the resultant pulmonary obstructive lesions. We report herein the first findings of 99m Technegas ventilation lung scanning in an infant with the syndrome to assess the pulmonary obstructive lesions.


2006 ◽  
Vol 132 (5) ◽  
pp. 1099-1104 ◽  
Author(s):  
Jonathan M. Chen ◽  
Julie S. Glickstein ◽  
Renee Margossian ◽  
Michelle L. Mercando ◽  
William E. Hellenbrand ◽  
...  

2017 ◽  
Vol 27 (9) ◽  
pp. 1740-1747 ◽  
Author(s):  
Estelle Tenisch ◽  
Marie-Josée Raboisson ◽  
Françoise Rypens ◽  
Julie Déry ◽  
Andrée Grignon ◽  
...  

AbstractObjectivesTetralogy of Fallot with absent pulmonary valve syndrome is a rare form of tetralogy of Fallot with dilatation of large pulmonary arteries. Prognosis is related to the severity of the cardiac malformation and to bronchial tree compression by dilated pulmonary arteries. This study analyses the prenatal echographic lung appearance in fetuses with tetralogy of Fallot with absent pulmonary valve and discusses its significance.MethodsWe carried out a retrospective review of fetal and postnatal files of nine fetuses diagnosed with tetralogy of Fallot with absent pulmonary valve syndrome in our institution. Correlations of prenatal ultrasound and cardiac imaging findings were obtained with outcome.ResultsAbnormal heterogeneous fetal lung echogenicity was detected in eight cases out of nine, always associated with significant lobar arterial dilatation. This aspect was well correlated with postnatal imaging and outcome in the four neonatal cases. The only fetus with normal lung echogenicity also had lower degree of pulmonary artery dilatation in the series.ConclusionsThis study demonstrates that a heterogeneous ultrasound appearance of the fetal lungs can be detected in utero in the most severe cases. This aspect suggests an already significant compression of the fetal bronchial tree by the dilated arteries that may have prognostic implications.


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