Tetralogy of Fallot With Interatrial Communication of the Inferior Sinus Venosus Type: A Rare Association Causing Post-Operative Desaturation

This case report describes a rare association of tetralogy of Fallot with interatrial communication of the inferior sinus venosus type (inferior sinus venosus defect). The patient underwent intracardiac repair for tetralogy of Fallot at 8 months of age. His postoperative course was complicated by desaturation. On reexploration, interatrial communication of the inferior sinus venosus type was revealed which went unnoticed on transthoracic echocardiogram as well as on computerized tomogram.

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Septum primum malposition defect and inferior sinus venosus defect: a rare association

Cardiology in the Young ◽

10.1017/s1047951114001899 ◽

2014 ◽

Vol 25 (7) ◽

pp. 1389-1392 ◽

Cited By ~ 1

Author(s):

Deepa Prasad ◽

Christopher Snyder ◽

Ravi Ashwath

Keyword(s):

Respiratory Distress ◽

Pulmonary Veins ◽

Atrial Septum ◽

Sinus Venosus ◽

Rare Association ◽

Septum Primum ◽

Sinus Venosus Defect ◽

The Right ◽

Inferior Sinus Venosus Defect ◽

Septum Secundum

AbstractWe present a case of a 2-year-old girl who presented with respiratory distress and umbilical abscess, and was found to have an inferior sinus venosus defect, malposition of the atrial septum primum, absent septum secundum, and anomalous drainage of the right upper and lower pulmonary veins to the right atrium.

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Magnetic Resonance Imaging-Aided Diagnosis of an Inferior Sinus Venosus Defect: A Case Report

Pediatric Cardiology ◽

10.1007/s00246-010-9643-7 ◽

2010 ◽

Vol 31 (4) ◽

pp. 564-566 ◽

Cited By ~ 1

Author(s):

Daryl Schantz ◽

Deborah Thompson ◽

Andrew Warren

Keyword(s):

Magnetic Resonance Imaging ◽

Case Report ◽

Magnetic Resonance ◽

Sinus Venosus ◽

Resonance Imaging ◽

Sinus Venosus Defect ◽

Aided Diagnosis ◽

Inferior Sinus Venosus Defect

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Echocardiographic diagnosis of inferior sinus venosus defects

Cardiology in the Young ◽

10.1017/s1047951100007903 ◽

1992 ◽

Vol 2 (4) ◽

pp. 338-341 ◽

Cited By ~ 11

Author(s):

José A. Ettedgui ◽

Ralph D. Siewers ◽

James R. Zuberbuhler ◽

Robert H. Anderson

Keyword(s):

Correct Diagnosis ◽

Pulmonary Veins ◽

Sinus Venosus ◽

Caval Vein ◽

Diagnostic Features ◽

Cross Sectional ◽

Interatrial Communication ◽

Inferior Caval Vein ◽

Sinus Venosus Defect ◽

Inferior Sinus Venosus Defect

AbstractSinus venosus defects are relatively uncommon forms of interatrial communication in which one of the caval veins has a biatrial connection, and partial anomalous pulmonary venous connections are the rule. The variety related to the inferior caval vein is much the rarer of the two forms, and here the defect is posterior and inferiorly placed. To determine whether an inferior sinus venosus defect could be identified preoperatively, we reviewed retrospectively the available echocardiograms and cineangiograms of the five patients with an inferior sinus venosus defect who underwent surgical repair between January 1983 and December 1991. A cross-sectional echocardiogram had been performed preoperatively in four of these patients, but the correct diagnosis had been made in only one case. Retrospective study, however, showed that the extent of the true atrial septum and the nature of the junction of the inferior caval vein with the atriums could be evaluated from the subcostal position in three of these four patients. Each of the three had an interatrial communication located posteriorly and inferiorly adjacent to the atrial connection of the inferior caval vein, along with abnormally connected right pulmonary veins. The oval fossa was intact and the coronary sinus was normal in all. Cardiac catheterization had been performed in three of the five patients. Anomalous return of right pulmonary veins was noted in each, and the posterior and inferior location of the interatrial communication was evident in two. An interatrial communication adjacent to the atrial connection of the inferior caval vein, along with anomalous connection of the right-sided pulmonary veins, are the diagnostic features of the inferior variety of sinus venosus defects. These features can be demonstrated by cross-sectional echocardiography from the subcostal position.

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