Anomalous Origin of the Circumflex or Left Anterior Descending Artery From the Pulmonary Artery

2020 ◽  
Vol 11 (6) ◽  
pp. 765-775
Author(s):  
Timothy M. Guenther ◽  
Elan A. Sherazee ◽  
Joshua D. Gustafson ◽  
Curtis J. Wozniak ◽  
Julie Brothers ◽  
...  

Anomalous origin of the circumflex or left anterior descending artery from the pulmonary artery (ACxAPA and ALADAPA, respectively) are rare congenital coronary anomalies with clinical presentation varying from an asymptomatic murmur to sudden cardiac arrest. A systematic review was performed, and 46 cases of ACxAPA and 51 cases of ALADAPA were identified in 87 articles. Data were collected and analyzed from each case. A better understanding of ACxAPA/ALADAPA can provide information to providers who encounter this lesion as well as provide insight into coronary artery development which may help in the understanding of coronary artery anomalies.

2018 ◽  
Vol 11 (24) ◽  
pp. e203-e205
Author(s):  
Bharat Marwaha ◽  
Owais Idris ◽  
Mobasser Mahmood ◽  
Archana Gundabolu ◽  
Syed Sohail Ali ◽  
...  

2012 ◽  
Vol 23 (3) ◽  
pp. 381-386 ◽  
Author(s):  
Giulia Tuo ◽  
Maurizio Marasini ◽  
Claudio Brunelli ◽  
Lucio Zannini ◽  
Manrico Balbi

AbstractObjectivesTo describe our experience in the management of coronary artery anomalies both in an adult and in a paediatric population and to compare the two groups for finding out differences in terms of angiographic incidence and treatment.Patients and methodsDatabases at the Department of Cardiology of San Martino Adult's Hospital and of Gaslini Children's Hospital were searched for all patients with a diagnosis of coronary artery anomaly who underwent coronary angiography between 1994 and 2006.ResultsCoronary anomalies were diagnosed in 76 (1%) adult patients. Anomalous left circumflex artery was the commonest coronary anomaly (25%). Anomalous left coronary artery from pulmonary artery and myocardial bridges were the only anomalies responsible for angina-like symptoms. No patients except the one with anomalous left coronary artery from pulmonary artery needed surgical intervention. In the paediatric population, we found 28 (0.9%) patients with coronary anomalies. Anomalous left coronary artery from pulmonary artery was the most common anomaly (48%) and always required emergency surgical treatment; in addition there were two patients with stenosis of the left main coronary artery.ConclusionCoronary artery anomalies may be associated with very acute, even life-threatening symptoms in children, whereas they are usually clinically silent and detected by accident on coronary angiography in adults. Recognition of coronary artery anomalies enables early treatment or close follow-up in children, whereas it could be useful in case of cardiac surgery in adults.


2014 ◽  
Vol 24 (5) ◽  
pp. 774-791 ◽  
Author(s):  
Julien I.E. Hoffman

AbstractAnomalous origin of a coronary artery from the aorta is a potentially serious anomaly that occurs in about 0.1–0.2% of the population. This percentage is small; however, it translates into about 4000 annual births with these anomalies. The clinical presentation of these anomalies is rare, and hence most are and will remain asymptomatic. The various anatomic anomalies are described, with anomalous origin of the left coronary artery that then passes between the aorta and pulmonary artery being the most serious of these anomalies. The pathophysiology resulting from these anomalies is described, as are methods for identifying those who require treatment; however, we still do not know the best methods of determining which patients need treatment.


Author(s):  
Cristina Basso ◽  
Carla Frescura ◽  
Stefania Rizzo ◽  
Gaetano Thiene

Despite the low prevalence in the general population, congenital coronary artery anomalies (CAAs) are well recognized as a major cause of sudden cardiac death (SCD). Not all CAAs have the same prognostic impact and each of them should be discussed individually. Apart from anomalous origin of a coronary artery (CA) from the pulmonary artery, the anomalous origin from the wrong aortic sinus, either the left main CA from the right sinus or the right CA from the left sinus, are traditionally considered as the highest risk of SCD. CAAs with an inter-arterial course carry the highest risk of ischaemia, particularly during exercise. Several pathophysiological mechanisms have been postulated, including compression of the anomalous CA between the aorta and the pulmonary artery, the acute angle take-off, the proximal intra-mural aortic course, and a superimposed CA spasm. The diagnostic work-up, including ischaemia provocation test imaging tools, and current management strategies, from sport restriction to surgical intervention, are discussed.


2018 ◽  
Vol 11 (4) ◽  
pp. NP136-NP139 ◽  
Author(s):  
Nischal R. Pandya ◽  
Prem Venugopal ◽  
Jason Wildschut ◽  
Nelson Alphonso

The incidence of congenital coronary artery anomalies in the general population is low. The combination of various significant coronary artery anomalies in a single patient is not very common. We describe a case of a 20-month-old child with a unique combination of congenital coronary anomalies (atresia, stenosis, fistula) which were accurately delineated by multimodal imaging and successfully managed surgically.


1970 ◽  
Vol 1 (1) ◽  
pp. 117-121
Author(s):  
AW Chowdhury ◽  
MA Muttalib ◽  
MA Baqui ◽  
S Dutta ◽  
MM Alam ◽  
...  

Anomalous origin of coronary arteries is a rare cause of cardiac disease. One of the very rare coronary anomalies is origin of left main coronary artery from pulmonary trunk. Most of these patients die in the first year of life and only 10-15% survive in adulthood. We are reporting a rare case of anomalous origin of left coronary artery from pulmonary artery who survives into sixth decade of life. Key words: Anomalous origin of coronary artery, Pulmonary artery, Left coronary artery DOI: http://dx.doi.org/10.3329/cardio.v1i1.8209 Cardiovasc. j. 2008; 1(1) : 117-121


2021 ◽  
Vol 24 (2) ◽  
pp. E293-E295
Author(s):  
Yueqiu Su ◽  
Zhongze Cao ◽  
Yunfei Ling ◽  
Yong jun Qian

An anomalous right coronary artery arising from the pulmonary artery (ARCAPA) is among the least common form of congenital coronary anomalies, accounted for the incidence of only 0.002% in the general population. Most ARCAPA patients have no symptoms but may develop myocardial ischemia. Surgical correction of the anomaly is recommended to prevent subsequent fatal outcomes. Here, we reported a case of a 2-year-old female child initially hospitalized for diarrhea, but later diagnosed with an ARCAPA through echocardiogram and computed tomography. Surgical reimplantation of the right coronary artery from the pulmonary artery to the ascending aorta was performed. The patient recovered well from the surgery with no postoperative complications. In the follow-up assessments, normal coronary function and myocardial effusion were demonstrated.


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