scholarly journals An extremely rare case of Rosai–Dorfman disease in the thymus

2021 ◽  
Vol 16 (1) ◽  
Author(s):  
Cheng Shen ◽  
Hu Liao

Abstract Background There were very few reports of Rosai–Dorfman disease in the thymus, which known as sinus histiocytosis with massive lymphadenopathy. It usually accompanied with other systemic symptoms such as fever, malaise, night sweats, or weight loss in the short term. Case presentation We herein report a rare case of RDD of thymic origin and a review of the literature concerning the clinical and pathological features of this disease, which is often misdiagnosed as thymoma. The patient was underwent thymectomy to extirpate the lesion completely by video-assisted thoracic surgery. Conclusions To the best of our knowledge, this is the fourth thymus occurring RDD case with proof via histology and IHC. Our findings suggest the difficulty of making a diagnosis before surgery and more cases will need to be reported in order to facilitate the preoperative diagnosis of such a rare tumor.

2016 ◽  
Vol 2 (2) ◽  
pp. 42-44
Author(s):  
S Parinita ◽  
KN Mohan Rao ◽  
Vivek LNU

ABSTRACT Localized fibrous tumors of the lung arise from the visceral pleura and are pedunculated. They also project into the pleural cavity. The tumor with an entirely pulmonary location is extremely rare. We present here a rare case of intrapulmonary localized fibrous tumor with review of the literature. How to cite this article Parinita S, Rao KNM, Vivek. Intrapulmonary Solitary Fibrous Tumor of the Lung: A Rare Case Presentation. J Med Sci 2016;2(2):42-44.


2020 ◽  
Author(s):  
Jianing Tong ◽  
Jianmin Niu ◽  
Qiaoyun Li ◽  
Li Hu ◽  
Hui Zhang

Abstract Background: Malignant ovarian Brenner tumors are extremely rare worldwide, accounting for only 1% of malignant ovarian tumors. Their clinical symptoms and pathology are complex and erratic, and the images are mostly non-specific. This poses difficulties in preoperative diagnosis and distinguishing them from other cystic solid ovarian tumors. Here this study has reported on a case of bilateral malignant ovarian Brenner tumor with peritoneal effusion. Case presentation: A 54-year-old woman presented with intermittent vaginal bleeding for more than two months and abdominal pain for one month. Two hard mass of five centimeters with poor movement could be touched at each side of the ovarian areas. The CT findings indicated the presence of two large cystic and solid masses in both adnexal regions. The operation had watched the size of the masses in the bilateral ovarian was both 6cmx6cmx5cm and their surface ulceration showed rotten fleshy tissue. After the operation, combined with morphological and immunohistochemical features, the ovarian specimens were consistent with bilateral ovarian malignant Brenner tumors.Conclusions: Although the incidence of bilateral malignant OBT is extremely low and this disease is extremely rare clinically, the gynecologists should be more informed of its diagnosis and treatment.


2019 ◽  
Vol 23 (3) ◽  
pp. 375-380
Author(s):  
Efe Can Sivrikaya ◽  
Burak Cezairli ◽  
Ferhat Ayranci ◽  
Mehmet Melih Omezli ◽  
Zerrin Unal Erzurumlu

2018 ◽  
Vol 2018 ◽  
pp. 1-5 ◽  
Author(s):  
Rashid AL Umairi ◽  
Danielle Blunt ◽  
Wedad Hana ◽  
Matthew Cheung ◽  
Anastasia Oikonomou

Rosai-Dorfman disease (RDD), also known as sinus histiocytosis with massive lymphadenopathy, is a rare nonmalignant lymphohistiocytic proliferative disorder. We report a patient with RDD who presented with multiple skin lesions, pulmonary involvement, and CT manifestations mimicking Langerhans cell histiocytosis, which improved after initiation of corticosteroid treatment.


2004 ◽  
Vol 59 (7) ◽  
pp. 625-630 ◽  
Author(s):  
A.R Geara ◽  
M.A Ayoubi ◽  
M.C Achram ◽  
N.M Chamseddine

2020 ◽  
Vol 18 (2) ◽  
pp. 161-164
Author(s):  
Iv. Novakov

Umbilical metastases, also termed Sister Mary Joseph's nodule, are reported rarely in medical literature and they are associated with advanced metastatic intra-abdominal and pelvic cancers. The purpose of this publication is to report a rare case of umbilical metastasis misdiagnosed as acomplicated umbilical hernia. Case presentation. A 74-years-old woman with nausea and painful umbilical swelling was misdiagnosed as incarcerated umbilical hernia оn the initial examination. Abdominal computed tomography revealed a huge pelvic cystic-solid mass, probably originates from right ovary. Conclusion. In conclusion, the presented case demonstrated that due to the lack of understanding Sister Mary Joseph’s nodule could be easily mistaken for incarcerated umbilical hernia.


2019 ◽  
pp. 1-4
Author(s):  
Aldo Franco De Rose ◽  
Francesca Ambrosini ◽  
Laura Tomasello ◽  
Francesco Boccardo ◽  
Carlo Terrone

2014 ◽  
Vol 18 (6) ◽  
pp. 424-429 ◽  
Author(s):  
Joshua M. Mercer ◽  
Paul Kuzel ◽  
Muhammad N. Mahmood ◽  
Alain Brassard

Introduction: We report a case of a 61-year-old woman with locally destructive vulvar pyoderma gangrenosum (PG) with pulmonary involvement who was refractory to numerous systemic therapies and developed complications resulting in her demise. Objective: To report a rare case of treatment-resistant vulvar PG with pulmonary involvement that proved to be fatal. Methods: PubMed was used to search for other reports that discuss PG, or more specifically perigenital PG, with pulmonary involvement. Results and Conclusion: A thorough review of the literature revealed 33 cases of PG with pulmonary involvement, with only 4 involving the perigenital region. We report the second case of a female with vulvar PG and pulmonary involvement. In contrast to the first case described, our patient did not respond to systemic therapy, and, ultimately, her disease was fatal. It is hoped that with continued documentation of this rare and potentially lethal presentation of PG, physicians will determine more effective treatments.


Author(s):  
Kalpana Giri ◽  
Ashok Baral ◽  
Niva Tiwari ◽  
Krishna Sharma

Rosai-Dorfman disease (RDD) is referred to as Sinus Histiocytosis Massive Lymphadenopathy (SHML) of unknown origin. We are reporting a rare case of Rosai Dorfman disease, a case of 6 years old male with a history of multiple painless bilateral submandibular and cervical lymphadenopathy.


Sign in / Sign up

Export Citation Format

Share Document