Complete restoration of congenital conductive hearing loss by staged surgery: A case report

The Bonebridge and Vibrant Soundbridge systems are semi-implanted hearing devices, which have been widely applied in patients with congenital conductive hearing loss. However, comparison between these two hearing devices is rare, especially in the same patient. We report a 23-year-old man who underwent successive implantation of Vibrant Soundbridge and Bonebridge devices in the same ear because of dysfunction of the Vibrant Soundbridge. We provide insight on the patient’s experience and compare the audiological and subjective outcomes of satisfaction.

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The first reported treatment of Nager syndrome associated hearing loss with bone-anchored hearing aids: case report

The Journal of Laryngology & Otology ◽

10.1017/s0022215111002738 ◽

2011 ◽

Vol 126 (1) ◽

pp. 76-78 ◽

Cited By ~ 4

Author(s):

G P Davies ◽

I J M Johnson

Keyword(s):

Hearing Loss ◽

Case Report ◽

Literature Review ◽

Current Literature ◽

Hearing Aids ◽

Clinical Case ◽

Conductive Hearing Loss ◽

First Case ◽

Nager Syndrome ◽

Conductive Hearing

AbstractObjective:To report the first case of treatment of Nager syndrome associated conductive hearing loss with bone-anchored hearing aids, in a three-year-old boy.Method:Clinical case report and current literature review regarding the use of bone-anchored hearing aids in the treatment of conductive hearing loss in children.Results:A three year eight month old boy with Nager syndrome was successfully treated for conductive hearing loss using bilateral bone-anchored hearing aids.Conclusion:This is the first case report of the use of bone-anchored hearing aids to treat Nager syndrome associated conductive hearing loss. Treatment was safe and successful in this case.

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Middle Ear Adenoma: Case Report and Discussion

Case Reports in Otolaryngology ◽

10.1155/2014/342125 ◽

2014 ◽

Vol 2014 ◽

pp. 1-4

Author(s):

D. Isenring ◽

T. F. Pezier ◽

B. Vrugt ◽

A. M. Huber

Keyword(s):

Hearing Loss ◽

Case Report ◽

Middle Ear ◽

Conductive Hearing Loss ◽

Surgical Excision ◽

Histological Techniques ◽

Preoperative Ct ◽

Middle Ear Adenoma ◽

Conductive Hearing ◽

Ct And Mri

Introduction. Despite modern radiological workup, surgeons can still be surprised by intraoperative findings or by the pathologist’s report.Materials & Methods. We describe the case of a 52-year-old male who was referred to our clinic with a single sided conductive hearing loss. He ultimately underwent middle ear exploration and excision of a middle ear tumour followed by second look and ossiculoplasty a year later.Results. Though preoperative CT and MRI scanning were suggestive of a congenital cholesteatoma, the pathologist’s report diagnosed a middle ear adenoma.Discussion. Middle ear glandular tumors are extremely rare and, despite numerous histological techniques, continue to defy satisfactory classification. Most surgeons advocate surgical excision though evidence of the tumour’s natural course and risk of recurrence is lacking.

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Delayed-Onset NOG Gene-Related Syndromic Conductive Deafness: A Case Report

Ear Nose & Throat Journal ◽

10.1177/0145561320944639 ◽

2020 ◽

pp. 014556132094463

Author(s):

Huiying Sun ◽

Yufei Qiao ◽

Na Chen ◽

Hua Yang ◽

Zhiqiang Gao ◽

...

Keyword(s):

Hearing Loss ◽

Case Report ◽

Otoacoustic Emissions ◽

Normal Development ◽

Conductive Hearing Loss ◽

Newborn Hearing Screening ◽

Delayed Onset ◽

Conductive Deafness ◽

Newborn Hearing ◽

Conductive Hearing

We report a 6-year-old girl with progressive bilateral conductive hearing loss for 2 years. She passed the newborn hearing screening conducted with otoacoustic emissions testing and had a normal development of speech and language, which indicated that her deafness was delayed-onset. She also had congenital proximal interphalangeal joints. Proximal symphalangism was confirmed by genetic testing ( NOG gene: c.406C > T, p.R136C). Bilateral stapes ankyloses were proved by surgery and her hearing was improved after stapedotomy by over 30 dB. Besides, this case should remind clinicians to carefully distinguish NOG gene-related deafness from congenital ossicular malformation and pediatric otosclerosis.

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Modified sleeve tympanotomy approach for removal of congenital cholesteatoma

The Journal of Laryngology & Otology ◽

10.1017/s0022215108003435 ◽

2008 ◽

Vol 122 (12) ◽

pp. 1365-1367 ◽

Cited By ~ 3

Author(s):

H J Park ◽

G H Park ◽

J E Shin ◽

S O Chang

Keyword(s):

Hearing Loss ◽

Case Report ◽

Tympanic Membrane ◽

Middle Ear ◽

Conductive Hearing Loss ◽

Tympanic Cavity ◽

Operative Techniques ◽

Congenital Cholesteatoma ◽

The Right ◽

Conductive Hearing

AbstractObjective:We present a technique which we have found useful for the management of congenital cholesteatoma extensively involving the middle ear.Case report:A five-year-old boy was presented to our department for management of a white mass on the right tympanic membrane. This congenital cholesteatoma extensively occupied the tympanic cavity. It was removed through an extended tympanotomy approach using our modified sleeve technique. The conventional tympanotomy approach was extended by gently separating the tympanic annulus from its sulcus in a circular manner. The firm attachment of the tympanic membrane at the umbo was not severed, in order to avoid lateralisation of the tympanic membrane.Conclusion:Although various operative techniques can be used, our modified sleeve tympanotomy approach provides a similarly sufficient and direct visualisation of the entire middle ear, with, theoretically, no possibility of lateralisation of the tympanic membrane and subsequent conductive hearing loss.

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The Use of a Custom Earmold to Prevent Recurrent External Auditory Canal Stenosis

Journal of the American Academy of Audiology ◽

10.3766/jaaa.19.3.7 ◽

2008 ◽

Vol 19 (03) ◽

pp. 233-236 ◽

Cited By ~ 2

Author(s):

Christopher Garvey ◽

Heather Turner

Keyword(s):

Hearing Loss ◽

Case Report ◽

External Auditory Canal ◽

Conductive Hearing Loss ◽

Canal Stenosis ◽

Conductive Hearing

The treatment of external auditory canal (EAC) stenoses often requires the prolonged use of a stent or splint. Traditional stents often occlude the EAC, resulting in a temporary conductive hearing loss. This case report describes a custom canal earmold with a large bore used as a stent in a patient with EAC stenosis. The customized earmold stent successfully prevented restenosis, while the large bore provided ventilation and improved hearing subjectively during the stenting phase. El tratamiento de la estenosis del conducto auditivo externo (EAC) a menudo requiere del uso prolongado de un stent o una férula. Los stents tradicionales a menudo ocluyen el EAC, provocando una hipoacusia conductiva temporal. Este reporte describe un caso un molde auditivo hecho a la medida con un agujero grande utilizado como stent en un paciente con estenosis del EAC. El stent de molde auditivo a la medida fue exitoso en prevenir la re-estenosis, mientras que el gran agujero aportó ventilación y mejoró subjetivamente la audición durante la fase de mantenimiento del stent.

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Pleomorphic adenoma presenting with conductive hearing loss in the ear canal: a case report and review of the literature

Journal of Medical Case Reports ◽

10.1186/1752-1947-8-178 ◽

2014 ◽

Vol 8 (1) ◽

Cited By ~ 3

Author(s):

Ayako Maruyama ◽

Takao Tokumaru ◽

Ken Kitamura

Keyword(s):

Hearing Loss ◽

Case Report ◽

Pleomorphic Adenoma ◽

Conductive Hearing Loss ◽

Review Of The Literature ◽

Ear Canal ◽

Conductive Hearing

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Congenital stapedial suprastructure fixation with normal footplate mobility: case report

The Journal of Laryngology & Otology ◽

10.1017/s0022215109991290 ◽

2009 ◽

Vol 124 (6) ◽

pp. 680-683 ◽

Cited By ~ 3

Author(s):

J H Lee ◽

S H Jung ◽

H C Kim ◽

C H Park ◽

S M Hong

Keyword(s):

Hearing Loss ◽

Case Report ◽

Rare Case ◽

Conductive Hearing Loss ◽

Branchial Arch ◽

Fallopian Canal ◽

Stapes Footplate ◽

The Right ◽

Conductive Hearing

AbstractObjective:We report a case of bilateral conductive hearing loss caused by stapedial suprastructure fixation with normal footplate mobility.Case report:A 50-year-old woman had suffered hearing loss in both ears since childhood. Exploratory tympanotomy revealed immobility of the stapes due to a bony bridge between the stapedial suprastructure and the fallopian canal. The incus was missing, while the malleus handle was minimally deformed. The mobility of the stapes footplate was normal. Post-operatively, the hearing in the right ear improved both subjectively and audiographically, while that in the left ear did not improve because of footplate subluxation during surgery.Conclusion:This is a rare case of congenital stapedial suprastructure fixation with normal footplate mobility. In this patient, development of the second branchial arch was arrested. When performing exploratory tympanotomy for stapedial fixation, one must keep in mind that normal footplate mobility is possible.

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A large osteoid osteoma of the mandibular condyle causing conductive hearing loss: a case report and review of literature

Journal of the Korean Association of Oral and Maxillofacial Surgeons ◽

10.5125/jkaoms.2017.43.2.106 ◽

2017 ◽

Vol 43 (2) ◽

pp. 106 ◽

Cited By ~ 1

Author(s):

Sunil Richardson ◽

Rakshit Vijay Khandeparker ◽

Kapil Sharma

Keyword(s):

Hearing Loss ◽

Case Report ◽

Osteoid Osteoma ◽

Conductive Hearing Loss ◽

Mandibular Condyle ◽

Review Of Literature ◽

Conductive Hearing

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Development and Resolution of Nasal Fricatives in a Child With Repaired Bilateral Cleft Lip and Palate: A Case Report

Perspectives of the ASHA Special Interest Groups ◽

10.1044/2021_persp-21-00028 ◽

2021 ◽

pp. 1-12

Author(s):

David J. Zajac ◽

Juliana Powell ◽

Margaret McQuillan

Keyword(s):

Hearing Loss ◽

Case Report ◽

Cleft Lip ◽

Speech Therapy ◽

Cleft Lip And Palate ◽

Conductive Hearing Loss ◽

Multiple Factors ◽

Air Emission ◽

Bilateral Cleft Lip ◽

Conductive Hearing

Purpose This case report describes the development, characteristics, and resolution of anterior nasal fricatives (ANFs)—a learned maladaptive articulation error—in a young girl with repaired bilateral cleft lip and palate. Method The girl was observed every 2 months from 12 to 24 months of age with follow-ups at 36, 48, and 67 months of age. Results At 12 months of age, the girl nasalized /b/ inconsistently and had mild conductive hearing loss. At 18 months of age, she exhibited audible nasal air emission on some plosives and used ANFs to replace /s/ and /z/, often with a nasal grimace. At 24 months of age, the child continued to experience mild conductive hearing loss, obligatory nasal air emission, and ANFs for /s/ and /z/. At 36 months of age, pressure-flow testing documented significant velopharyngeal (VP) dysfunction. The girl then used ANFs for /f/ and /s/, phonetically marked by different oral stops. At 48 months of age, although VP impairment continued, speech therapy largely eliminated ANFs. By 67 months of age, VP closure was nearly normal. Conclusions Multiple factors including VP dysfunction, audible nasal air emission, and conductive hearing loss contributed to the development of ANFs. Clinical and etiological implications are discussed.

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