scholarly journals Conventional Repair of an Intraoperatively Diagnosed Congenitally Corrected Transposition of the Great Arteries in an Adult

2021 ◽  
Vol 24 (4) ◽  
pp. E769-E771
Author(s):  
Muhammad Arza Putra ◽  
Rubiana Sukardi ◽  
Jonathan Grantomo ◽  
Jenni Pratita
Keyword(s):  
Rare Condition ◽  
Mitral Valve Regurgitation ◽  
Normal Activity ◽  
Disease Diagnosis ◽  
Careful Examination ◽  
Valve Regurgitation ◽  
Early Management ◽  
Right Ventricle Dysfunction ◽  
Congenitally Corrected Transposition ◽  
Corrected Transposition

Background: Congenitally corrected transposition of the great arteries (ccTGA) is a rare condition that accounts for just 1% of all congenital heart disease. Diagnosis of ccTGA often is missed in adulthood, despite imaging and cardiology consultation. Case report: We present the case of an intraoperatively diagnosed ccTGA with severe tricuspid valve regurgitation and secundum atrial septal defect in a 54-year-old woman, who preoperatively was diagnosed with mitral valve regurgitation in atrioventricular and ventriculoarterial concordance heart. Intraoperatively, options considered were anatomical repair with atrial-arterial double switch operation after retraining the left ventricle or a conventional repair that focused on the associated defects without addressing the discordant connections. Considering our patient’s age and condition, we decided to carry on with the conventional repair to prevent further systemic right ventricle dysfunction that may lead to poor outcome and decreased survival. She was discharged one week after surgery and resumed her normal activity at 3-month follow up. Conclusion: Although it rarely happens, CHD such as ccTGA in an adult must always be considered. Careful examination is essential. The treatment of ccTGA in an adult is challenging, with more limited options compared with pediatric patients. However, early management could still provide favorable outcomes.

Pulmonary Artery Banding for Congenitally Corrected Transposition of the Great Arteries With Hydrops Fetalis: A Case Report

2019 ◽  
Vol 11 (4) ◽  
pp. NP247-NP250
Author(s):  
Yuka Takeda ◽  
Nobuo Momoi ◽  
Mariko Hayashi ◽  
Kisei Endo ◽  
Yoshimichi Aoyagi ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Main Pulmonary Artery ◽  
Mitral Valve Regurgitation ◽  
Hydrops Fetalis ◽  
Pulmonary Artery Banding ◽  
Valve Regurgitation ◽  
Switch Operation ◽  
Double Switch ◽  
Congenitally Corrected Transposition ◽  
Corrected Transposition

At 32 weeks of gestation, a male fetus with congenitally corrected transposition of the great arteries developed hydrops fetalis caused by a combination of mitral valve regurgitation and tricuspid valve regurgitation (TR). We performed a pulmonary artery banding (PAB) at 108 days old for gradually progressing TR, after confirming that a balloon dilatation test in the main pulmonary artery reduced TR. As the patient grew, the PAB became tighter and systolic blood pressure in the morphological left ventricle increased. At present, the patient is waiting for a double switch operation.

scholarly journals Congenitally corrected transposition of great arteries: a case series of five unoperated African children

2020 ◽  
Vol 4 (1) ◽  
Author(s):  
Bernard Obongonyinge ◽  
Judith Namuyonga ◽  
Hilda Tumwebaze ◽  
Twalib Aliku ◽  
Peter Lwabi ◽  
...  
Keyword(s):  
Right Ventricular ◽  
Tricuspid Valve ◽  
Pulmonary Stenosis ◽  
Valve Regurgitation ◽  
Ventricular Failure ◽  
Tricuspid Valve Regurgitation ◽  
Transposition Of Great Arteries ◽  
Anatomic Repair ◽  
Congenitally Corrected Transposition ◽  
Corrected Transposition

Abstract Background Congenitally corrected transposition of great arteries (ccTGA) is rare. It is commonly associated with ventricular septal defect (VSD), pulmonary stenosis and heart block. Early anatomic repair is recommended between 3 and 6 months of age to prevent development of tricuspid valve regurgitation and systemic right ventricular failure. Case presentation We retrospectively identified five cases of ccTGA. Cases were between one and 13 years of age. All the cases were unoperated. Four of the five cases had associated intracardiac defects/complications. These included: VSD, pulmonary stenosis, tricuspid valve regurgitation, right ventricular systolic dysfunction and heart block. Conclusion These cases demonstrate the challenges of access to early diagnosis and surgery in a low resource setting. This delay in anatomic repair leads to complications of tricuspid valve regurgitation and systemic right ventricular failure.

scholarly journals A Case of Congenitally Corrected Transposition of the Great Arteries Discovered on Coronary Computed Tomography

2013 ◽  
Vol 2013 ◽  
pp. 1-3
Author(s):  
Adam T. Marler ◽  
Jennifer N. Slim ◽  
Travis Batts ◽  
James Watts ◽  
Ahmad M. Slim
Keyword(s):  
Computed Tomography ◽  
Right Ventricular Outflow Tract ◽  
Rare Condition ◽  
Ventricular Outflow Tract ◽  
The United States ◽  
Related Quality ◽  
Cardiology Clinic ◽  
Health Related ◽  
Congenitally Corrected Transposition ◽  
Corrected Transposition

Congenitally corrected transposition of the great arteries is a rare condition accounting for less than 1% of all congenital cardiac diseases. The fundamental nature of this condition involves a blend of atrioventricular as well as ventriculoarterial discordance. Congenitally corrected transposition of the great arteries is classically associated with three additional abnormalities, including ventricular septal defect, right ventricular outflow tract obstruction, and tricuspid valve abnormalities. Patients with this anomaly have been shown to exhibit reduced exercise tolerance as well as reduced health-related quality of life when compared to patients with normal cardiovascular anatomy. We present the case of a 33-year-old active duty lieutenant in the United States Air Force referred to the cardiology clinic for evaluation of valvular heart disease with subsequent discovery of congenitally corrected transposition of the great arteries on cardiac gated computed tomography.

Abstract 17117: Prevalence of Systemic AV Valve Regurgitation in Patients With Congenitally Corrected Transposition of the Great Arteries: Anatomic versus Physiologic Repair

Circulation ◽  
2020 ◽  
Vol 142 (Suppl_3) ◽  
Author(s):  
Salima A Bhimani ◽  
Aisha ZIA ◽  
Paola Barrios ◽  
Anabila Moses ◽  
Jared Klein ◽  
...  
Keyword(s):  
Expectant Management ◽  
Medical Group ◽  
Valve Regurgitation ◽  
Cross Sectional ◽  
Associated Lesions ◽  
Double Switch ◽  
Systemic Ventricle ◽  
Congenitally Corrected Transposition ◽  
Corrected Transposition

Background: Congenitally corrected transposition of the great arteries (ccTGA) is a rare anomaly with highly variable time of diagnosis. Depending on time of diagnosis and associated lesions, multiple therapies exist, directed towards surgical correction. Anatomic repair (AR) involving double switch or atrial switch/Rastelli and physiologic repair (PR) leaving the right ventricle as the systemic ventricle are the two main surgical options. A subset of patients without associated lesions exist who can be followed expectantly over time. Systemic atrioventricular valve (SAVV) function is a major anatomic variable, determining eligibility for double switch and durability of physiologic repair or expectant management (medical group). We therefore sought to assess the prevalence of AV valve regurgitation in the different subgroups and its determinants, hypothesizing that SAVV regurgitation (SAVVR) was reduced in the AR group. Methods: Retrospective record review coupled with prospective cross-sectional follow-up of 240 patients with ccTGA treated at our center was performed. Echocardiographic imaging review was conducted to assess SAVV function and systemic ventricular function among the 3 subgroups. Results: Of 240 patients with ccTGA, 162 met inclusion. Median follow up was 10 years (mean +/- SD 11+/- 9 years). In the AR group majority (85%) had none/mild SAVVR. Prior PA band did not influence the severity of SAVVR following double switch. In the PR group, 22% underwent SAVV repair/replacement, and 75% had none/mild SAVVR; as opposed to only 65% with none/mild SAVVR in the medical group. Only 14% of patients were free of systemic ventricle dysfunction in PR group as opposed to 72% in the AR group. Conclusions: SAVV function is preserved in the AR group. In contrast patients in the PR group had higher prevalence of more than mild SAVVR followed by patients who were managed expectantly.

scholarly journals MitraClip Repair of Right-Sided Atrio-ventricular Valve in a Patient with Congenitally-Corrected Transposition of Great Arteries: Case Report

2021 ◽  
Author(s):  
Antonio Lewis ◽  
Emad Hakemi ◽  
David Lopez ◽  
Robert J Cubeddu
Keyword(s):  
Mitral Valve ◽  
Multimodality Imaging ◽  
Mitral Valve Regurgitation ◽  
Team Approach ◽  
Heart Team ◽  
Transposition Of Great Arteries ◽  
First Case ◽  
Complex Patients ◽  
Congenitally Corrected Transposition ◽  
Corrected Transposition

Abstract Background Patients with ccTGA often develop tricuspid valve (systemic atrioventricular valve (AV) dysfunction due to RV overload and dilatation, but isolated mitral valve disease is rarely found. Isolated Mitral (subpulmonic AV -valve) interventions, specifically catheter-directed, have not been reported up to date. Case Summary A man with congenitally corrected transposition of the great arteries (ccTGA) is evaluated for dyspnoea. Multimodality imaging assessment confirmed severe right-sided mitral valve regurgitation due to prolapse. In light of high surgical risk, a minimally invasive transcatheter MitraClip procedure was pursued. Discussion To our knowledge, this is the first case of successful mitral valve repair via percutaneous approach using MitraClip in a patient with ccTGA and biventricular failure. Our case illustrates the safety and feasibility of the edge-to-edge procedure in such a rare instance, but also the importance of multimodality imaging (both invasive and non-invasive) and the Heart Team approach when caring for these complex patients.

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