scholarly journals Benign cutaneous ancient schwannoma masquerading as well differentiated nerve sheath tumor: a case report

2019 ◽  
Vol 6 (8) ◽  
pp. 2970
Author(s):  
Swaminathan Ganesan ◽  
Balakrishnan Subramani
Keyword(s):  
Malignant Tumors ◽  
Excision Biopsy ◽  
Nerve Sheath Tumor ◽  
Rare Entity ◽  
Diagnostic Dilemma ◽  
Nerve Sheath ◽  
Recklinghausen Disease ◽  
Well Differentiated ◽  
High Degree ◽  
Von Recklinghausen

Ancient schwannomas are a rare entity of benign cutaneous nerve sheath tumor in patients without von Recklinghausen disease. Head and neck, mediastinal, retroperitoneal ancient schwannomas have been reported and has high degree for malignant transformation. Ancient schwannoma of the peripheries have been reported in only few cases and in hand only two cases have been reported. We present this case for its rarity and the diagnostic dilemma occurring with FNAC. Thus these tumors if present in periphery and in non-neurofibromatosis patient can masquerade as malignant tumors but still can safely are treated with excision biopsy alone and with almost nil recurrence.

scholarly journals Malignant primary nerve sheath tumor of the cauda equina in a patient without Von Recklinghausen disease

2017 ◽  
Vol 02 (03) ◽  
pp. 291-293
Author(s):  
Virendra Atam ◽  
Liza Das ◽  
Mallagouda Patil ◽  
Besthenahalli Yathish ◽  
Sciddhartha Kunwar ◽  
...  
Keyword(s):  
Cauda Equina ◽  
Nerve Sheath Tumor ◽  
Von Recklinghausen Disease ◽  
Nerve Sheath ◽  
Recklinghausen Disease ◽  
Von Recklinghausen

Malignant Peripheral Nerve Sheath Tumor of the Urinary Bladder in von Recklinghausen Disease

2002 ◽  
Vol 69 (2) ◽  
pp. 156-159 ◽  
Author(s):  
Panagiotis Kalafatis ◽  
Nikolaos Kavantzas ◽  
Petros M. Pavlopoulos ◽  
Emmanuel Agapitos ◽  
Mary Politou ◽  
...  
Keyword(s):  
Urinary Bladder ◽  
Peripheral Nerve ◽  
Nerve Sheath Tumor ◽  
Peripheral Nerve Sheath Tumor ◽  
Von Recklinghausen Disease ◽  
Nerve Sheath ◽  
Recklinghausen Disease ◽  
Von Recklinghausen

scholarly journals A Case of High-grade Lung Metastasis with Malignant Peripheral Nerve Sheath Tumor in a Patient with von Recklinghausen Disease

Haigan ◽  
2018 ◽  
Vol 58 (3) ◽  
pp. 211-215
Author(s):  
Naoki Suzuki ◽  
Toshiaki Masaoka ◽  
Ko Sato ◽  
Hidenori Kawakami ◽  
Shinya Uchigasaki ◽  
...  
Keyword(s):  
Peripheral Nerve ◽  
Lung Metastasis ◽  
Nerve Sheath Tumor ◽  
High Grade ◽  
Peripheral Nerve Sheath Tumor ◽  
Von Recklinghausen Disease ◽  
Nerve Sheath ◽  
Recklinghausen Disease ◽  
Von Recklinghausen

scholarly journals Intramural Duodenal Hematoma In 2-year Old Child

2018 ◽  
Vol 9 (3) ◽  
pp. 18
Author(s):  
Dayanand Hota ◽  
Kamal Nain Rattan ◽  
Ahmad Khursheed ◽  
Manish Swami ◽  
Harish Bhardwaj
Keyword(s):  
Duodenal Obstruction ◽  
Intramural Hematoma ◽  
Abdominal Distension ◽  
Rare Entity ◽  
Diagnostic Dilemma ◽  
X Ray ◽  
Duodenal Hematoma ◽  
High Degree ◽  
High Intestinal Obstruction ◽  
Head Of Pancreas

Background: Intramural hematoma of the duodenum is a rare cause of acquired duodenal obstruction. It is often a diagnostic dilemma and a high degree of suspicion is required to make an early and accurate diagnosis in children. Case Report: A 2-year-old child presented with bilious vomiting and abdominal distension. X-ray abdomen showed high intestinal obstruction. Ultrasound and CT scan abdomen gave suspicion of pancreatic pseudo-cyst near head of pancreas. At surgery, an intramural hematoma of the duodenum was found and drained. Conclusion: Intramural duodenal hematoma is a rare entity especially in children and should be considered in differential diagnosis of acquired duodenal obstruction.

LARGE PLEXIFORM NEUROFIBROMA OF THE SACRO-GLUTEAL REGION – A RARE CASE REPORT

2021 ◽  
pp. 30-31
Author(s):  
Surya Rao Rao Venkata Mahipathy ◽  
Alagar Raja Durairaj ◽  
Narayanamurthy Sundaramurthy ◽  
Anand Prasath Jayachandiran ◽  
Suresh Rajendran
Keyword(s):  
Rare Case ◽  
Primary Closure ◽  
Plexiform Neurofibroma ◽  
Surgical Excision ◽  
Gluteal Region ◽  
Nerve Sheath Tumor ◽  
Nerve Sheath ◽  
Rare Case Report ◽  
Von Recklinghausen

Plexiform neurobroma is a rare benign nerve sheath tumor that develops in the perineurium and is often considered pathognomonic of neurobromatosis type 1 (NF1 or von Recklinghausen disease). They occur most frequently in the craniomaxillofacial region, rarely on back and extremities. These lesions are highly vascular and there is 15-20% potential for malignant transformation. Here, we present a 26-year-old female with neurobromatosis all over her body, but with a large plexiform neurobroma in the sacral region which was causing difculty in sitting and lying supine as well as disgurement of the gluteal region. Surgical excision with primary closure of the swelling was done. Histopathology ndings were consistent with neurobromatosis.

Spinal malignant nerve-sheath tumor or cellular schwannoma? A striking difference in prognosis

1993 ◽  
Vol 79 (4) ◽  
pp. 528-532 ◽  
Author(s):  
Matti T. Seppälä ◽  
Matti J. J. Haltia
Keyword(s):  
Malignant Tumors ◽  
Spinal Tumors ◽  
Striking Difference ◽  
Malignant Neoplasms ◽  
Nerve Sheath Tumor ◽  
Content Type ◽  
Nerve Sheath Tumors ◽  
Nerve Sheath ◽  
Cellular Schwannoma ◽  
S 100

✓ Cellular schwannoma, a recently delineated entity, has a histological appearance mimicking that of malignant neoplasms. The aim of this study was to determine the outcome for patients treated for a spinal cellular schwannoma or malignant nerve-sheath tumor. A histological re-examination was conducted of 283 spinal tumors, considered to originate from a nerve root, that were treated in the Department of Neurosurgery between 1953 and 1985. After re-examination, 50 of these were determined to be other tumors or nonneoplastic lesions. The review yielded eight cellular schwannomas and six malignant nerve-sheath tumors out of 233 of nerve-sheath origin. Immunohistochemical staining with a commercially available polyclonal antibody against S-100 protein was positive in all cases of cellular schwannoma, but negative for the malignant tumors. Clinical outcome was favorable for patients with cellular schwannomas, but uniformly poor for those with the malignant tumors.

scholarly journals Intrathoracic Malignant Peripheral Nerve Sheath Tumor in von Recklinghausen`s Disease

2001 ◽  
Vol 16 (3) ◽  
pp. 201-204 ◽  
Author(s):  
Ju Hyung Park ◽  
Koang Ho Choi ◽  
Heung Bum Lee ◽  
Yang Keun Rhee ◽  
Yong Chul Lee ◽  
...  
Keyword(s):  
Peripheral Nerve ◽  
Nerve Sheath Tumor ◽  
Peripheral Nerve Sheath Tumor ◽  
Nerve Sheath ◽  
Von Recklinghausen

Nerve Sheath Tumors: Malignant peripheral nerve sheath tumors, Schwannomas, and Neurofibromas

2019 ◽  
Author(s):  
Keila E Torres ◽  
Wei-Lien Wang ◽  
Alexander Lazar ◽  
Ian E McCutcheon
Keyword(s):  
Molecular Biology ◽  
Peripheral Nerve ◽  
Malignant Tumors ◽  
Therapeutic Strategies ◽  
Benign Tumors ◽  
Nerve Sheath Tumor ◽  
High Grade ◽  
Nerve Sheath Tumors ◽  
Peripheral Nerve Sheath Tumors ◽  
Nerve Sheath

Peripheral nerve sheath tumors represent a spectrum of entities ranging from benign tumors, such as schwannoma, to high-grade malignant tumors termed malignant peripheral nerve sheath tumors. In this chapter, we discuss current concepts and problematic areas in the diagnosis, treatment, and management of peripheral nerve sheath tumors. We discuss the major categories of nerve sheath tumors including schwannomas, neurofibromas, and malignant peripheral nerve sheath tumors. The different benign variants and their propensity for malignant transformation are highlighted. We suggest useful guidelines for the surgical management of these challenging cases. Finally, we discuss some of the advances in molecular biology that have provided new insights into the nature of the various peripheral nerve sheath tumors and suggest potential novel targeted therapeutic strategies for these tumors. This review contains 11 figures, 5 tables and 66 references. Key Words: malignant peripheral nerve sheath tumors, nerve sheath tumor, neurofibroma, neurofibromatosis, schwannoma, schwannomatosis, NF1, NF2

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