scholarly journals Giant Plexiform Neurofibroma

2018 ◽  
Vol 3 (1) ◽  
Author(s):  
Michelangelo Giovanni Vestita ◽  
Rossella Elia ◽  
Giuseppe Giudice
Keyword(s):  
Blood Loss ◽  
Surgical Management ◽  
Rare Case ◽  
Plexiform Neurofibroma ◽  
Type 1 Neurofibromatosis

We report a rare case of giant plexiform neurofibroma in a patient affected by type-1 neurofibromatosis and we describe the correct surgical management of such lesions in order to avoid intra- and post-op blood loss related complications.

PLEXIFORM NEUROFIBROMA OF THE BRACHIAL PLEXUS – A RARE CASE REPORT

2021 ◽  
pp. 13-15
Author(s):  
Surya Rao Rao Venkata Mahipathy ◽  
Alagar Raja Durairaj ◽  
Narayanamurthy Sundaramurthy ◽  
Anand Prasath Jayachandiran ◽  
Suresh Rajendran
Keyword(s):  
Brachial Plexus ◽  
Rare Case ◽  
Autosomal Dominant ◽  
Plexiform Neurofibroma ◽  
Autosomal Dominant Disorder ◽  
Surgical Debulking ◽  
Rare Case Report ◽  
Benign Tumours ◽  
Common Benign Tumour

Neurobroma is a common benign tumour occurring as part of an autosomal dominant disorder, neurobromatosis type 1, leading to the formation of benign tumours or neurobromas of the peripheral nervous system. Large neurobromas of the brachial plexus are rare and present a difcult challenge for surgeon due to the anatomical complexity of the brachial plexus. Dermal neurobromas usually present with swelling and occasional pain, but neurobromas associated with the brachial plexus present with pain and neurological symptoms. These plexiform neurobromas of the brachial plexus are known to undergo malignant transformation. Here, we present a case of a large plexiform neurobroma affecting the left brachial plexus and extending till the elbow, conrmed with MRI and surgical debulking was done.

LARGE PLEXIFORM NEUROFIBROMA OF THE SACRO-GLUTEAL REGION – A RARE CASE REPORT

2021 ◽  
pp. 30-31
Author(s):  
Surya Rao Rao Venkata Mahipathy ◽  
Alagar Raja Durairaj ◽  
Narayanamurthy Sundaramurthy ◽  
Anand Prasath Jayachandiran ◽  
Suresh Rajendran
Keyword(s):  
Rare Case ◽  
Primary Closure ◽  
Plexiform Neurofibroma ◽  
Surgical Excision ◽  
Gluteal Region ◽  
Nerve Sheath Tumor ◽  
Nerve Sheath ◽  
Rare Case Report ◽  
Von Recklinghausen

Plexiform neurobroma is a rare benign nerve sheath tumor that develops in the perineurium and is often considered pathognomonic of neurobromatosis type 1 (NF1 or von Recklinghausen disease). They occur most frequently in the craniomaxillofacial region, rarely on back and extremities. These lesions are highly vascular and there is 15-20% potential for malignant transformation. Here, we present a 26-year-old female with neurobromatosis all over her body, but with a large plexiform neurobroma in the sacral region which was causing difculty in sitting and lying supine as well as disgurement of the gluteal region. Surgical excision with primary closure of the swelling was done. Histopathology ndings were consistent with neurobromatosis.

PLEXIFORM NEUROFIBROMA IN TYPE 1 NEUROFIBROMATOSIS

2006 ◽  
Vol 25 (2) ◽  
pp. 87-93 ◽  
Author(s):  
Connie A. Keehn ◽  
Pearl Myers ◽  
Charles N. Paidas ◽  
Enid Gilbert-Barness
Keyword(s):  
Plexiform Neurofibroma ◽  
Type 1 Neurofibromatosis

scholarly journals Bilateral Plexiform Neurofibroma of the Sciatic Nerve Associated with Neurofibromatosis Type 1: A Rare Case

2020 ◽  
Vol 8 (8) ◽  
pp. 1871-1873
Author(s):  
Fekhaoui Mohammed Reda ◽  
Ghannam Abdelaziz ◽  
Boufettal Moncef ◽  
Bassir Rida-Allah ◽  
Kharmaz Mohammed ◽  
...  
Keyword(s):  
Sciatic Nerve ◽  
Neurofibromatosis Type 1 ◽  
Rare Case ◽  
Plexiform Neurofibroma ◽  
Neurofibromatosis Type

scholarly journals A rare case of internal jugular vein aneurysmal degeneration in a type 1 neurofibromatosis complicated by potentially life-threatening thrombosis

2011 ◽  
Vol 54 (4) ◽  
pp. 1170-1173 ◽  
Author(s):  
Mirko Belcastro ◽  
Andrea Palleschi ◽  
Riccardo A. Trovato ◽  
Ruggero Landini ◽  
Maurizio Di Bisceglie ◽  
...  
Keyword(s):  
Internal Jugular Vein ◽  
Rare Case ◽  
Jugular Vein ◽  
Type 1 Neurofibromatosis ◽  
Life Threatening

A rare case of a spontaneous neck hematoma in a patient with type 1 neurofibromatosis

2016 ◽  
Vol 43 (5) ◽  
pp. 591-594 ◽  
Author(s):  
Stamatia Dova ◽  
Kyriakos Ktenidis ◽  
Petros Karkos ◽  
Sarantis Blioskas ◽  
Georgios Psillas ◽  
...  
Keyword(s):  
Rare Case ◽  
Type 1 Neurofibromatosis

Plexiform neurofibromatosis of penis: a rare presentation of type 1 neurofibromatosis

2020 ◽  
Vol 13 (11) ◽  
pp. e236542
Author(s):  
Ravi Banthia ◽  
Priyank Yadav ◽  
Rajiv Agarwal ◽  
Hira Lal
Keyword(s):  
Unusual Case ◽  
English Literature ◽  
Plexiform Neurofibroma ◽  
External Genitalia ◽  
Rare Presentation ◽  
Solitary Neurofibroma ◽  
Type 1 Neurofibromatosis ◽  
Plexiform Neurofibromatosis

Although more than 100 cases of genitourinary neurofibromas have been reported, only 16 cases of solitary neurofibroma arising in the penis have been reported in English literature. There can be diffuse or localised pelvic involvement in cases of neurofibromatosis and sometimes these masses can extend into and disfigure the external genitalia. We report an unusual case of plexiform neurofibroma arising from penis and review the literature on penile neurofibromas.

scholarly journals A rare case of thoracic myelocystocele associated with type 1 split cord malformation with low lying tethered cord, dorsal syrinx and sacral agenesis: Pentad finding

2015 ◽  
Vol 6 (01) ◽  
pp. 087-090 ◽  
Author(s):  
Dipanker Singh Mankotia ◽  
Guru Dutta Satyarthee ◽  
Bhawani Shankar Sharma
Keyword(s):  
Spina Bifida ◽  
Surgical Management ◽  
Rare Case ◽  
Clinical Presentation ◽  
Spinal Dysraphism ◽  
Tethered Cord ◽  
Split Cord Malformation ◽  
Rare Form ◽  
Sacral Agenesis

ABSTRACTMyelocystocele is a rare form of spinal dysraphism. Thoracic myelocystocele is still rarer. The occurrence of thoracic myelocystocele associated with type-1 split cord malformation, low lying tethered cord, dorsal syrinx and spina bifida is extremely rare. Clinical presentation of such a rare case and an early surgical management is discussed briefly.

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