scholarly journals Spinal Anesthesia for Urologic Surgery in an Infant with Hemi-Fontan Physiology: A Case Report

2019 ◽  
Vol 4 (4) ◽  
Keyword(s):  
Case Report ◽  
Right Ventricle ◽  
Spinal Anesthesia ◽  
Congenital Heart Defect ◽  
Congenital Heart ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Fontan Physiology ◽  
Surgical Conditions ◽  
Left Heart Syndrome

Hypoplastic left heart syndrome is a congenital heart defect characterized by hypoplasia of left-sided heart structures and a single functional right ventricle. The resultant physiology poses significant challenges for the anesthesiologist when general anesthesia is necessary for these children. This case report describes an infant with hemi-Fontan physiology undergoing circumcision in which awake spinal anesthesia was used with favorable hemodynamic, respiratory, and surgical conditions. Written consent for publication was obtained from the patient’s parents.

scholarly journals CASE REPORT – COVID-19 Infection in Infant with Severe Congenital Heart Disease

2021 ◽  
pp. 1-5
Author(s):  
Natalie Pexton ◽  
Amy Svenson ◽  
Deepti Bhat
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Case Report ◽  
Congenital Heart ◽  
Supplemental Oxygen ◽  
The Novel ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome ◽  
Severe Congenital Heart Disease

Abstract We describe the case of a 2 month old born with hypoplastic left heart syndrome who presented with fever and vomiting and was found to be infected with the novel corona virus (COVID-19). He underwent treatment with supplemental oxygen, heparin, and dexamethasone. After a 6 day hospitalization he recovered remarkably well without major adverse effects.

Hypoplastic Left Heart Syndrome: Natural History in a Geographically Defined Population

PEDIATRICS ◽  
1990 ◽  
Vol 85 (6) ◽  
pp. 977-983
Author(s):  
Cynthia D. Morris ◽  
Jacquelyn Outcalt ◽  
Victor D. Menashe
Keyword(s):  
Natural History ◽  
Hypoplastic Left Heart Syndrome ◽  
Congenital Heart ◽  
Heart Defects ◽  
Norwood Procedure ◽  
Secular Change ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
History Of ◽  
Left Heart Syndrome

Advances in surgical treatment of hypoplastic left heart syndrome with the Norwood procedure and cardiac transplantation have made essential the understanding of the natural history of hypoplastic left heart syndrome. In a geographically defined population, we ascertained the prevalence of hypoplastic left heart syndrome in children born in Oregon from 1971 through 1986. Clinical and anatomic data were extracted from the charts of the 98 affected children and the survival rate was calculated. Hypoplastic left heart syndrome occurred in 0.162 per 1000 live births in Oregon during this period. No syndrome complex was prevalent and 84% were free of other congenital malformations. However, there was an increased occurrence of congenital heart defects in first-degree relatives of probands with hypoplastic left heart syndrome. Of the affected children 15 ± 4% died on the first day of life, 70 ± 5% died within the first week, and 91 ± 3% died within 30 days. No secular change in survival occurred during the study. Palliation with the Norwood procedure was performed in 20 children. Although survival was significantly improved with this surgery (P = .01), the effect was observed principally through 30 days of life and only one of these children remains alive. Hypoplastic left heart syndrome is a lethal congenital heart defect in children and poses management and ethical dilemmas.

Use of a saphenous venous homograft for constructing a conduit from the right ventricle to the pulmonary arteries in the Norwood procedure

2004 ◽  
Vol 14 (3) ◽  
pp. 325-327 ◽  
Author(s):  
Luca A. Vricella ◽  
Jane E. Crosson ◽  
Duke E. Cameron
Keyword(s):  
Birth Weight ◽  
Right Ventricle ◽  
Pulmonary Arteries ◽  
Operative Management ◽  
Norwood Procedure ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Pulmonary Arterial ◽  
The Right ◽  
Left Heart Syndrome

The use of a conduit of polytetrafluoroethylene placed between the right ventricle and the pulmonary arteries as source of pulmonary arterial supply during the first stage of palliation for the hypoplastic left heart syndrome has facilitated post-operative management and resulted in decreased mortality. We describe here the use of a cryopreserved saphenous vein inserted in reversed direction to create the connection between the right ventricle and the pulmonary arteries in a neonate with low birth weight undergoing the modified Norwood procedure.

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